Fibroid Arising in a Müllerian Duct Remnant Presenting as a Pelvic Mass

Persistent Mullerian duct syndrome has been described as a disease of internal male pseudohermaphroditism, a rare autosomal recessive disease, characterised by persistent Mullerian derivatives in patients with male pattern 46, XY karyotype and normal pattern virilisation. We present a case of an elderly man, who on evaluation for bilateral undescended testes was found to have a pelvic mass suggestive of malignant transformation of an undescended testis on imaging. On surgical exploration, uterus with multiple fibroids, bilateral fallopian tubes, cervix and bilateral atrophic testes were identified. Interestingly, in this case, imaging (contrastCT and MRI) had missed Mullerian structures due to varied presentation, but exploration and excision of the structures followed by their histopathology revealed uterine leiomyomas and confirmed other Mullerian structures (bilateral fallopian tubes, cervix) with bilateral testes.

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Xanthogranulomatous abscess of a Mullerian duct remnant

Diseases of the Colon & Rectum ◽

10.1007/bf02555328 ◽

1986 ◽

Vol 29 (11) ◽

pp. 755-759 ◽

Cited By ~ 8

Author(s):

Michael Davis ◽

Mark E. Whitley ◽

Abida K. Haque ◽

Cecilia Fenoglio-Preiser ◽

Robert Waterman

Keyword(s):

Mullerian Duct ◽

Müllerian Duct ◽

Mullerian Duct Remnant

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V07-11 ROBOTIC TRANSVESICAL EXCISION OF A MULLERIAN DUCT REMNANT

The Journal of Urology ◽

10.1097/01.ju.0000556591.01284.a9 ◽

2019 ◽

Vol 201 (Supplement 4) ◽

Author(s):

Ziho Lee* ◽

Matthew Lee ◽

Anand V. Badri ◽

Zarine Balsara ◽

Jonatha A. Roth ◽

...

Keyword(s):

Mullerian Duct ◽

Müllerian Duct ◽

Mullerian Duct Remnant

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An unusual appearance of the post-pubertal Herlyn-Werner-Wunderlich syndrome with acute abdominal pain: A case report

International Journal of Reproductive BioMedicine ◽

10.18502/ijrm.v17i10.5498 ◽

2019 ◽

Cited By ~ 1

Author(s):

Marzieh Ghasemi ◽

Arezoo Esmailzadeh

Keyword(s):

Abdominal Pain ◽

Acute Abdominal Pain ◽

Pelvic Mass ◽

Mullerian Duct ◽

Early Puberty ◽

Vaginal Septum ◽

Müllerian Duct ◽

Uterus Didelphys ◽

Obstructed Hemivagina ◽

One Year

Background: Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital urogenital defect. It is detected by unilateral low vaginal obstruction, uterus didelphys, and ipsilateral kidney agenesis. It usually becomes apparent with pain, dysmenorrhea, and presence of a vaginal or pelvic mass. Purulent vaginal discharge may also happen rarely because of infective complications of the obstructed hemivagina. In this report, we describe a post-pubertal case with acute abdominal pain. Case: The patient was a 13-yr-old girl who was referred to us with acute abdominal pain one year after the onset of her menarche. In the pelvic examination, we detected hematocolpos. Abdominopelvic-computed tomography scan confirmed the presence of mullerian duct anomalies with uterus didelphys. This case of HWW syndrome along with pyocolpus was managed by vaginal septum resection, drainage of pus, and salpingectomy. Conclusion: The symptoms of HWW syndrome should be monitored in early puberty to prevent more complications. Key words: Herlyn-Werner-Wunderlich syndrome, Uterus didelphys, Kidney agenesis, Mullerian duct anomaly.

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A Huge Mullerian Duct Remnants in An Adult: A Case Report and Literature Review

10.21203/rs.3.rs-111300/v1 ◽

2020 ◽

Author(s):

Yonghui Wang ◽

Peng Xiang ◽

Wei Wang ◽

Shuang Li ◽

Hao Ping ◽

...

Keyword(s):

Cystic Lesion ◽

Pelvic Cavity ◽

Mullerian Duct ◽

Resonance Imaging ◽

Computed Tomography Scan ◽

Case Presentation ◽

Müllerian Duct ◽

Laparoscopic Excision ◽

Tomography Scan ◽

Mullerian Duct Remnant

Abstract Background: müllerian duct remnant is a disease which was reported infrequently. The cyst’s size in this case is even rarer. We performed surgery on this patient and introduced the procedure in detail. Case presentation: We present a case that a 58-year-old patient with a huge müllerian duct remnant between the prostate and rectum. Magnetic resonance imaging and computed tomography scan of abdominal and pelvic showed that a cystic lesion with a size of 14×10×10 cm in the pelvic cavity. There were no surgical contraindications were found after some related preoperative examinations, so the laparoscopic surgery was performed. The features of the mass of postoperative pathologic examination presented that the characteristics are consistent with the Müllerian duct. Conclusions: Laparoscopic excision is a perfect way to manage müllerian duct remnant. This way can get good outcome and minimize the damage to the patient.

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