Liver tumours

Mapping Intimacies ◽

10.1093/med/9780198569862.003.0060 ◽

2011 ◽

Author(s):

R. Mark Beattie ◽

Anil Dhawan ◽

John W.L. Puntis

Keyword(s):

Hepatocellular Carcinoma ◽

Liver Disease ◽

Focal Nodular Hyperplasia ◽

Mesenchymal Hamartoma ◽

Nodular Regenerative Hyperplasia ◽

Age Group ◽

Inflammatory Pseudotumour ◽

Liver Tumours ◽

Nodular Hyperplasia ◽

Paediatric Age

Infantile haemangiomata 440Mesenchymal hamartoma 441Focal nodular hyperplasia (FNH) 441Nodular regenerative hyperplasia (NRH) 441Hepatoblastoma 442Hepatocellular carcinoma (HCC) 442Inflammatory pseudotumour 443Fibropolycystic liver disease 443Liver tumours in children are rare, accounting for 0.5–2% of all neoplasms in the paediatric age group....

Download Full-text

Liver tumours

10.1093/med/9780198759928.003.0066 ◽

2018 ◽

Author(s):

Marianne Samyn

Keyword(s):

Hepatocellular Carcinoma ◽

Focal Nodular Hyperplasia ◽

Mesenchymal Hamartoma ◽

Nodular Regenerative Hyperplasia ◽

Liver Tumours ◽

Nodular Hyperplasia ◽

Infantile Haemangiomas

The chapter on liver tumours covers the features and management of infantile haemangiomas, mesenchymal hamartoma, focal nodular hyperplasia, nodular regenerative hyperplasia, hepatoblastoma, and hepatocellular carcinoma.

Download Full-text

Abernethy malformation and hepatocellular carcinoma: a serious consequence of a rare disease

BMJ Case Reports ◽

10.1136/bcr-2019-231843 ◽

2020 ◽

Vol 13 (1) ◽

pp. e231843 ◽

Cited By ~ 1

Author(s):

Manuel Jaklitsch ◽

Mafalda Sobral ◽

Ana Maria Carvalho ◽

Hugo Pinto Marques

Keyword(s):

Hepatocellular Carcinoma ◽

Treatment Strategies ◽

Nodular Regenerative Hyperplasia ◽

Portal Flow ◽

Abernethy Malformation ◽

Liver Tumours ◽

Portosystemic Shunts ◽

Nodular Hyperplasia ◽

Patient Series ◽

Malignant Liver

Congenital portosystemic shunts (CPSS) are a rare vascular consequence of embryogenetic vascular alterations or the persistence of the fetal circulation elements, first described by John Abernethy in 1793 and classified by Morgan and Superina, into complete and partial portosystemic shunts. Its prevalence to this day has not been defined. We present a patient series of a 44-year-old and 47-year-old man and woman, with this rare congenital malformation and underlining hepatocellular carcinoma (HCC) treatment strategies. Over half of the individuals with CPSS have benign or malignant liver tumours, ranging from nodular regenerative hyperplasia, focal nodular hyperplasia, adenomas, HCC and hepatoblastomas. Additionally, it is known that half of individuals with Abernethy malformation type Ib will develop one or multiple types of tumours. There seems to be a direct association with tumorigenesis and CPSS, which is the primary consequence of absent portal flow. Surgery is the treatment of choice, either as a curative resection or orthotopic liver transplantation if recommended as per the criteria, in which replacing the hepatic parenchyma in the setting of an Abernathy malformation will correct the underlining hyper-arterialisation.

Download Full-text