Rare conditions presenting in adulthood

2017 ◽  
Author(s):  
Sara Thorne ◽  
Sarah Bowater
Keyword(s):  
Coronary Artery ◽  
Pulmonary Artery ◽  
Left Coronary Artery ◽  
Sinus Of Valsalva ◽  
Coronary Anomalies ◽  
Arteriovenous Fistulae ◽  
Sinus Of Valsalva Aneurysm

This chapter discusses rare conditions presenting in adulthood, including coronary anomalies (left coronary artery from pulmonary artery [LCAPA], congenital coronary arteriovenous fistulae) and sinus of Valsalva aneurysm.

Incidence and clinical relevance of primary congenital anomalies of the coronary arteries in children and adults

2012 ◽  
Vol 23 (3) ◽  
pp. 381-386 ◽  
Author(s):  
Giulia Tuo ◽  
Maurizio Marasini ◽  
Claudio Brunelli ◽  
Lucio Zannini ◽  
Manrico Balbi
Keyword(s):  
Coronary Artery ◽  
Coronary Angiography ◽  
Pulmonary Artery ◽  
Left Coronary Artery ◽  
Paediatric Population ◽  
Coronary Anomalies ◽  
Coronary Artery Anomalies ◽  
Anomalous Left Coronary Artery ◽  
Left Circumflex Artery ◽  
Anomalous Left Coronary

AbstractObjectivesTo describe our experience in the management of coronary artery anomalies both in an adult and in a paediatric population and to compare the two groups for finding out differences in terms of angiographic incidence and treatment.Patients and methodsDatabases at the Department of Cardiology of San Martino Adult's Hospital and of Gaslini Children's Hospital were searched for all patients with a diagnosis of coronary artery anomaly who underwent coronary angiography between 1994 and 2006.ResultsCoronary anomalies were diagnosed in 76 (1%) adult patients. Anomalous left circumflex artery was the commonest coronary anomaly (25%). Anomalous left coronary artery from pulmonary artery and myocardial bridges were the only anomalies responsible for angina-like symptoms. No patients except the one with anomalous left coronary artery from pulmonary artery needed surgical intervention. In the paediatric population, we found 28 (0.9%) patients with coronary anomalies. Anomalous left coronary artery from pulmonary artery was the most common anomaly (48%) and always required emergency surgical treatment; in addition there were two patients with stenosis of the left main coronary artery.ConclusionCoronary artery anomalies may be associated with very acute, even life-threatening symptoms in children, whereas they are usually clinically silent and detected by accident on coronary angiography in adults. Recognition of coronary artery anomalies enables early treatment or close follow-up in children, whereas it could be useful in case of cardiac surgery in adults.

Acquired and congenital coronary artery abnormalities

2017 ◽  
Vol 27 (S1) ◽  
pp. S31-S35 ◽  
Author(s):  
Ming-Lon Young ◽  
Michael McLeary ◽  
Kak-Chen Chan
Keyword(s):  
Coronary Artery ◽  
Pulmonary Artery ◽  
Cardiac Death ◽  
Left Coronary Artery ◽  
Sinus Of Valsalva ◽  
Anomalous Left Coronary Artery ◽  
Coronary Artery Abnormalities ◽  
Asymptomatic Patients ◽  
The Right ◽  
Anomalous Left Coronary

AbstractSudden unexpected cardiac deaths in approximately 20% of young athletes are due to acquired or congenital coronary artery abnormalities. Kawasaki disease is the leading cause for acquired coronary artery abnormalities, which can cause late coronary artery sequelae including aneurysms, stenosis, and thrombosis, leading to myocardial ischaemia and ventricular fibrillation. Patients with anomalous left coronary artery from the pulmonary artery can develop adequate collateral circulation from the right coronary artery in the newborn period, which remains asymptomatic only to manifest in adulthood with myocardial ischaemia, ventricular arrhythmias, and sudden death. Anomalous origin of coronary artery from the opposite sinus occurs in 0.7% of the young general population aged between 11 and 15 years. If the anomalous coronary artery courses between the pulmonary artery and the aorta, sudden cardiac death may occur during or shortly after vigorous exercise, especially in patients where the anomalous left coronary artery originates from the right sinus of Valsalva. Symptomatic patients with evidence of ischaemia should have surgical correction. No treatment is needed for asymptomatic patients with an anomalous right coronary artery from the left sinus of Valsalva. At present, there is no consensus regarding how to manage asymptomatic patients with anomalous left coronary artery from the right sinus of Valsalva and interarterial course. Myocardial bridging is commonly observed in cardiac catheterisation and it rarely causes exercise-induced coronary syndrome or cardiac death. In symptomatic patients, refractory or β-blocker treatment and surgical un-bridging may be considered.

scholarly journals Anomalous Origin of Left Coronary Artery from Pulmonary Trunk in an Adult Patient –A Rare Occurrence

1970 ◽  
Vol 1 (1) ◽  
pp. 117-121
Author(s):  
AW Chowdhury ◽  
MA Muttalib ◽  
MA Baqui ◽  
S Dutta ◽  
MM Alam ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Pulmonary Artery ◽  
Left Coronary Artery ◽  
Left Main Coronary Artery ◽  
Pulmonary Trunk ◽  
Anomalous Origin ◽  
First Year ◽  
Coronary Anomalies ◽  
First Year Of Life ◽  
Sixth Decade

Anomalous origin of coronary arteries is a rare cause of cardiac disease. One of the very rare coronary anomalies is origin of left main coronary artery from pulmonary trunk. Most of these patients die in the first year of life and only 10-15% survive in adulthood. We are reporting a rare case of anomalous origin of left coronary artery from pulmonary artery who survives into sixth decade of life. Key words: Anomalous origin of coronary artery, Pulmonary artery, Left coronary artery DOI: http://dx.doi.org/10.3329/cardio.v1i1.8209 Cardiovasc. j. 2008; 1(1) : 117-121

scholarly journals Anomalous Right Coronary Artery Arising from the Pulmonary Artery with Associated Enlargement of the Left Coronary Artery: A Case Report

2021 ◽  
Vol 24 (2) ◽  
pp. E293-E295
Author(s):  
Yueqiu Su ◽  
Zhongze Cao ◽  
Yunfei Ling ◽  
Yong jun Qian
Keyword(s):  
Coronary Artery ◽  
Pulmonary Artery ◽  
Right Coronary Artery ◽  
Left Coronary Artery ◽  
Female Child ◽  
Ascending Aorta ◽  
Coronary Anomalies ◽  
The Right ◽  
Congenital Coronary Anomalies

An anomalous right coronary artery arising from the pulmonary artery (ARCAPA) is among the least common form of congenital coronary anomalies, accounted for the incidence of only 0.002% in the general population. Most ARCAPA patients have no symptoms but may develop myocardial ischemia. Surgical correction of the anomaly is recommended to prevent subsequent fatal outcomes. Here, we reported a case of a 2-year-old female child initially hospitalized for diarrhea, but later diagnosed with an ARCAPA through echocardiogram and computed tomography. Surgical reimplantation of the right coronary artery from the pulmonary artery to the ascending aorta was performed. The patient recovered well from the surgery with no postoperative complications. In the follow-up assessments, normal coronary function and myocardial effusion were demonstrated.

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