Haemoglobinopathies
Keyword(s):
♦ Haemoglobinopathies are commonly inherited disorders of haemoglobin synthesis♦ Thalassaemia is commonest around the Mediterranean countries and has skeletal manifestations due to massive marrow expansion with thinning of the cortex♦ Sickle cell crises occur in homozygotes and are a result of venous occlusion causing avascular necrosis. Infection and exposure to cold can sometimes precipitate these painful events♦ If surgery is needed blood cross-match must be carefully performed in advance, the theatre should be kept warm, and the hydration and acid/base balance of the patient monitored carefully.
2014 ◽
Vol 84
(3-4)
◽
pp. 0206-0217
◽
Keyword(s):
1954 ◽
Vol 15
(2)
◽
pp. 207-219
◽
Keyword(s):
2016 ◽
Vol 24
(3)
◽
pp. 116-121
1932 ◽
Vol 98
(1)
◽
pp. 253-260
◽
1958 ◽
Vol 1
(10)
◽
pp. 327-328
◽
1965 ◽
Vol 12
(5)
◽
pp. 479-496
◽