Importance of the arc of Riolan in children with severe middle aortic syndrome

Middle aortic syndrome (MAS) is a rare disease characterized by distal thoracic aorta or abdominal aorta coarctation, and thoraco-abdominal aortic bypass grafting is an effective treatment for this condition. However, significant trauma is associated with the conventional surgical approach. We report a 26-year-old woman with MAS who presented with hypertension and needed thoraco-abdominal bypass grafting. In this operation, we adopted the endoscopic technique to improve the conventional surgical approach (reduce the incision). This case report shows that it is safe and feasible to use an endoscopic technique to reduce the trauma during this kind of operation, and provides a reference for similar treatments.

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Surgical Management of Middle Aortic Syndrome in the Elderly

Annals of Vascular Surgery ◽

10.1016/j.avsg.2009.12.012 ◽

2010 ◽

Vol 24 (5) ◽

pp. 694.e5-694.e8 ◽

Cited By ~ 4

Author(s):

Chika Cho ◽

Raphael Coscas ◽

Fabien Koskas

Keyword(s):

Surgical Management ◽

The Elderly ◽

Middle Aortic Syndrome

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A Unique Case of Middle Aorta Syndrome With a “Corkscrew” Descending Aorta

World Journal for Pediatric and Congenital Heart Surgery ◽

10.1177/2150135119873854 ◽

2019 ◽

Vol 10 (6) ◽

pp. 799-800

Author(s):

Mubeena Abdulkarim ◽

Yaa Karikari ◽

Rohit S. Loomba ◽

Robert H. Anderson ◽

Luca Vricella ◽

...

Keyword(s):

Surgical Management ◽

Advanced Imaging ◽

Unique Case ◽

Descending Aorta ◽

Middle Aortic Syndrome

Middle aortic syndrome is a rare anatomic defect of the descending aorta and presents with hypertension. We present a unique case with “corkscrew” configuration. This case highlights the need for evaluation with advanced imaging for diagnosis to facilitate surgical management and avoid hypertensive complications.

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Emergent thoracic aortic angioplasty and stenting for middle aortic syndrome in non-specific aortitis

Cardiovascular Intervention and Therapeutics ◽

10.1007/s12928-010-0012-5 ◽

2010 ◽

Vol 25 (2) ◽

pp. 117-121

Author(s):

Susumu Fujino ◽

Tomohito Mabuchi ◽

Shohei Yoshida ◽

Masatomo Suzuki ◽

Yoshihiro Noji ◽

...

Keyword(s):

Middle Aortic Syndrome ◽

Angioplasty And Stenting

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Endovascular Management of Middle Aortic Syndrome Presenting with Uncontrolled Hypertension

Case Reports in Vascular Medicine ◽

10.1155/2018/9586025 ◽

2018 ◽

Vol 2018 ◽

pp. 1-4

Author(s):

Owen S. Glotzer ◽

Kathryn Bowser ◽

F. Todd Harad ◽

Sandra Weiss

Keyword(s):

Open Surgery ◽

Unusual Case ◽

Case Series ◽

Uncontrolled Hypertension ◽

Endovascular Management ◽

Vascular Disorder ◽

Middle Aortic Syndrome ◽

Surgical Bypass ◽

Endovascular Approach

Middle Aortic Syndrome is a rare vascular disorder consisting of narrowing or stenosis of the distal thoracic or abdominal aorta. It is described in the literature in the form of case studies and case series. The authors present an unusual case of Middle Aortic Syndrome attributed to Takayasu’s arteritis in a 60-year-old female who presented to the emergency department with uncontrolled hypertension. Traditional intervention involves open surgical bypass. This case study reviews the published literature on this rare syndrome and illustrates a successful alternative to open surgery through an endovascular approach.

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