scholarly journals Fabry's disease with complete atrioventricular block: histological evidence of involvement of the conduction system

Heart ◽  
1992 ◽  
Vol 68 (9) ◽  
pp. 323-325 ◽  
Author(s):  
Y. Ikari ◽  
K. Kuwako ◽  
T. Yamaguchi

2001 ◽  
Vol 119 (5) ◽  
pp. 184-186 ◽  
Author(s):  
Fábio Ferrari ◽  
Paulo do Nascimento Junior ◽  
Pedro Thadeu Galvão Vianna

CONTEXT: Patients with Alport's syndrome (causing 5% of end-stage renal disease) have a higher risk of heart conduction abnormalities. OBJECTIVE: To report a case of Alport's syndrome developing complete atrioventricular block during renal transplantation. CASE REPORT: A 21-year-old man with chronic renal failure due to Alport's syndrome was submitted to a renal transplantation under epidural anesthesia and, during the intraoperative period, a complete atrioventricular block was diagnosed and promptly treated with a transcutaneous pacemaker. This extensive sympathetic block can contribute towards disturbances in the heart conduction system, particularly in patients with chronic renal disease in hemodialysis. Even in patients with a normal preoperative electrocardiogram or no conduction system disturbances, some degree of atrioventricular block, including complete atrioventricular block, can occur. In this situation, a transcutaneous pacemaker provides rapid and effective treatment in the operating room, thereby permitting the planning of a definitive treatment.



1981 ◽  
Vol 22 (2) ◽  
pp. 275-280 ◽  
Author(s):  
Takako FUJIWARA ◽  
Yuichi AKIYAMA ◽  
Hiroyasu NARITA ◽  
Tadashi UEDA ◽  
Tadashi HAYASHIDERA ◽  
...  




1975 ◽  
Vol 90 (1) ◽  
pp. 78-83 ◽  
Author(s):  
Maurice Lev ◽  
Saroja Bharati ◽  
Franklin G. Hoffman ◽  
Leonard Leight


2009 ◽  
Vol 12 (1) ◽  
pp. E30-E34 ◽  
Author(s):  
Cüneyt Narin ◽  
Ahmet Ozkara ◽  
Ahmet Soylu ◽  
Erdal Ege ◽  
Akif Düzenli ◽  
...  


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