Carnitine palmitoyl transferase I deficiency

2020 ◽  
pp. 285-290
Author(s):  
William L. Nyhan ◽  
Georg F. Hoffmann ◽  
Aida I. Al-Aqeel ◽  
Bruce A. Barshop
Keyword(s):  
Carnitine Palmitoyl Transferase ◽  
Carnitine Palmitoyl Transferase I

Carnitine palmitoyl transferase-I activity in the aging mouse heart

1995 ◽  
Vol 79 (2-3) ◽  
pp. 127-136 ◽  
Author(s):  
Jeff A. Odiet ◽  
Michaël E.T.I. Boerrigter ◽  
Jeanne Y. Wei
Keyword(s):  
Mouse Heart ◽  
Carnitine Palmitoyl Transferase ◽  
Aging Mouse ◽  
Carnitine Palmitoyl Transferase I

Carnitine palmitoyl transferase I and the control of myocardial β-oxidation flux

2001 ◽  
Vol 29 (2) ◽  
pp. 245-249 ◽  
Author(s):  
S. Eaton ◽  
K. Fukumoto ◽  
N. Paladio Duran ◽  
A. Pierro ◽  
L. Spitz ◽  
...  
Keyword(s):  
Carnitine Palmitoyltransferase ◽  
Carnitine Palmitoyl Transferase ◽  
Malonyl Coa ◽  
Carnitine Palmitoyltransferase I ◽  
Rate Limiting ◽  
Carnitine Palmitoyl Transferase I

Carnitine palmitoyltransferase I is assumed to be rate limiting for β-oxidation in all tissues. However, the concentration of malonyl-CoA in heart and muscle is high and is enough to completely inhibit β-oxidation if this assumption is correct. In this review, we consider whether: (i) there is a malonyl-CoA-insensitive carnitine palmitoyltransferase I activity; (ii) the measured malonyl-CoA concentration in the heart is physiologically meaningful; and (iii) carnitine palmitoyltransferase I is rate-limiting for β-oxidation in the heart.

scholarly journals Acyl-CoA binding proteins interact with the acyl-CoA binding domain of mitochondrial carnitine palmitoyl transferase I

2011 ◽  
Vol 355 (1-2) ◽  
pp. 135-148 ◽  
Author(s):  
Heather A. Hostetler ◽  
Dan Lupas ◽  
Yingran Tan ◽  
Jia Dai ◽  
Matthew S. Kelzer ◽  
...  
Keyword(s):  
Binding Proteins ◽  
Binding Domain ◽  
Carnitine Palmitoyl Transferase ◽  
Carnitine Palmitoyl Transferase I

CARNITINE PALMITOYL TRANSFERASE-I INHIBITION IS NOT ASSOCIATED WITH CARDIAC HYPERTROPHY IN RATS FED A HIGH-FAT DIET

2007 ◽  
Vol 34 (1-2) ◽  
pp. 113-119 ◽  
Author(s):  
Isidore C Okere ◽  
Margaret P Chandler ◽  
Tracy A McElfresh ◽  
Julie H Rennison ◽  
Theodore A Kung ◽  
...  
Keyword(s):  
Cardiac Hypertrophy ◽  
High Fat Diet ◽  
High Fat ◽  
Carnitine Palmitoyl Transferase ◽  
Carnitine Palmitoyl Transferase I
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