Aggressive angiomyxoma of the ischioanal fossa in a post-menopausal woman

2021 ◽  
Vol 103 (2) ◽  
pp. e59-e64
Author(s):  
E Peterknecht ◽  
E Agerbak ◽  
AYY Mohamedahmed ◽  
S Stonelake ◽  
K Kulkarni ◽  
...  
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Perianal Abscess ◽  
Surgical Excision ◽  
Reproductive Age ◽  
Ischiorectal Fossa ◽  
Menopausal Woman ◽  
Aggressive Angiomyxoma ◽  
Buttock Pain ◽  
Post Menopausal

Aggressive angiomyxoma is a rare mesenchymal tumour, primarily arising in the soft tissue of the pelvis and perineum in women of reproductive age. There is a paucity of evidence on optimal management because of the rarity of these tumours, but the consensus has been for surgical excision. We present the case of a 65-year-old woman who was admitted with left-sided buttock pain and initially diagnosed with a perianal abscess. She underwent examination under anaesthesia rectum with surgical excision of the lesion, subsequent histopathological and immunochemical analysis was suggestive of aggressive angiomyxoma. To complement our case report, we also present a literature review focusing on aggressive angiomyxoma in the ischioanal fossa (also known as the ischiorectal fossa) with only eight cases of primary aggressive angiomyxoma involving the ischioanal fossa documented to date. The primary aims of this case report and literature review are to familiarise clinicians with the clinical, histopathological and immunochemical features of these tumours, and to increase appreciation that despite the rarity of aggressive angiomyxoma, it might be considered in the differential diagnosis of ischioanal lesions.

scholarly journals Sertoli-Leydig cell tumor with unique nail findings in a post-menopausal woman: a case report and literature review

2014 ◽  
Vol 7 (1) ◽  
Author(s):  
Dalia Moghazy ◽  
Chakradhari Sharan ◽  
Malika Nair ◽  
Cassandra Rackauskas ◽  
Robert Burnette ◽  
...  
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Leydig Cell ◽  
Leydig Cell Tumor ◽  
Cell Tumor ◽  
Menopausal Woman ◽  
Post Menopausal Woman ◽  
Post Menopausal

scholarly journals Radical excision of a massive vulvo: Vaginal mass

2016 ◽  
Author(s):  
J. Meena ◽  
A. Parthasarathy ◽  
R. Vatsa ◽  
N. Singh ◽  
S. Kumar ◽  
...  
Keyword(s):  
Condylomata Acuminata ◽  
Surgical Excision ◽  
Posterior Wall ◽  
Reproductive Age ◽  
Ischiorectal Fossa ◽  
Radical Excision ◽  
Aggressive Angiomyxoma ◽  
Diagnostic Features ◽  
Vaginal Mass

Background: Vulvo-vaginal masses has a varied presentation and causes. The most common differential diagnosis are Condylomata acuminata, Vulvular abscess, Vulvular/vaginal cysts, Vulval carcinoma, Vulval lipoma, Angiomyofibroblastoma and Aggressive Angiomyxoma. Surgical excision of the mass is the main method of treatment and the outcome differs with the histological diagnosis. We present a video of excision of a massive Vulvo vaginal mass in toto. Case: A 45 year old P3 L3 female, presented with complaint of mass in perineal area & discharge per vaginum for 2 years. The mass was growing progressively and reached the present size. On examination there was a 9 X 8 cm irregular firm to cystic mass, arising from posterior wall of vagina and protruding out of introitus with bossellated surface. The mass also extended into right ischiorectal fossa, 10 X 10 cm mass with cystic, smooth surface that was irreducible with no cough impulse. CECT abdomen and pelvis revealed a well-defined 12 X 10 X 8 cm mass in right perineum arising from right lower lateral vaginal wall with ischiorectal fossa extension. There was no extension into cervix, bladder or rectum. Biopsy taken from the mass was inconclusive. A wide local excision was done under general anesthesia wherein an ischiorectal and vaginal mass of size 30 X 10 cm with irregular margin was excised in toto. Histopathology was suggestive of Aggressive Angiomyxoma. The patient is under follow up. Discussion: Aggressive Angiomyxoma is a rare slow growing locally invasive mesenchymal tumor and has a substantial potential for recurrence. It is often misdiagnosed. Pre-operative diagnosis is difficult due to rarity of this entity and absence of diagnostic features, but it should be considered in case of masses in genital, perianal and pelvic region in a woman of reproductive age. Radical surgical excision is the first line of management. A long term follow up of the case is necessary and MRI is preferred method for detecting recurrences.

scholarly journals Radical excision of a massive vulvo-vaginal mass

2016 ◽  
Author(s):  
J. Meena ◽  
A. Parthasarathy ◽  
R. Vatsa ◽  
N. Singh ◽  
S. Kumar ◽  
...  
Keyword(s):  
Condylomata Acuminata ◽  
Surgical Excision ◽  
Posterior Wall ◽  
Reproductive Age ◽  
Ischiorectal Fossa ◽  
Radical Excision ◽  
Aggressive Angiomyxoma ◽  
Diagnostic Features ◽  
Vaginal Mass

Background: Vulvo-vaginal masses has a varied presentation and causes. The most common differential diagnosis are condylomata acuminata, vulvular abscess, vulvular/vaginal cysts, vulval carcinoma, vulval lipoma, angiomyofibroblastoma and aggressive angiomyxoma. Surgical excision of the mass is the main method of treatment and the outcome differs with the histological diagnosis. We present a video of excision of a massive Vulvo vaginal mass in toto. Case: A 45 year old P3 L3 female, presented with complaint of mass in perineal area and discharge per vaginum for 2 years. The mass was growing progressively and reached the present size. On examination there was a 9 × 8 cm irregular firm to cystic mass, arising from posterior wall of vagina and protruding out of introitus with bossellated surface. The mass also extended into right ischiorectal fossa, 10 × 10 cm mass with cystic, smooth surface that was irreducible with no cough impulse. CECT abdomen and pelvis revealed a well-defined 12 × 10 × 8 cm mass in right perineum arising from right lower lateral vaginal wall with ischiorectal fossa extension. There was no extension into cervix, bladder or rectum. Biopsy taken from the mass was inconclusive. A wide local excision was done under general anesthesia wherein an ischiorectal and vaginal mass of size 30 × 10 cm with irregular margin was excised in toto. Histopathology was suggestive of aggressive angiomyxoma. The patient is under follow up. Discussion: Aggressive Angiomyxoma is a rare slow growing locally invasive mesenchymal tumor and has a substantial potential for recurrence. It is often misdiagnosed. Pre-operative diagnosis is difficult due to rarity of this entity and absence of diagnostic features, but it should be considered in case of masses in genital, perianal and pelvic region in a woman of reproductive age. Radical surgical excision is the first line of management. A long term follow up of the case is necessary and MRI is preferred method for detecting recurrences.

scholarly journals Radical excision of a massive vulvo-vaginal mass

2016 ◽  
Author(s):  
J. Meena ◽  
A. Parthasarathy ◽  
R. Vatsa ◽  
N. Singh ◽  
S. Kumar ◽  
...  
Keyword(s):  
Condylomata Acuminata ◽  
Surgical Excision ◽  
Posterior Wall ◽  
Reproductive Age ◽  
Ischiorectal Fossa ◽  
Radical Excision ◽  
Aggressive Angiomyxoma ◽  
Diagnostic Features ◽  
Vaginal Mass

Background: Vulvo-vaginal masses has a varied presentation and causes. The most common differential diagnosis are Condylomata acuminata, Vulvular abscess, Vulvular/vaginal cysts, Vulval carcinoma, Vulval lipoma, Angiomyofibroblastoma and Aggressive Angiomyxoma. Surgical excision of the mass is the main method of treatment and the outcome differs with the histological diagnosis. We present a video of excision of a massiveVulvo vaginal mass in toto. Case: A 45 year old P3 L3female, presented with complaint of mass in perineal area & discharge per vaginum for 2 years. The mass was growing progressively and reached the present size. On examination there was a 9 X 8 cm irregular firm to cystic mass, arising from posterior wall of vagina and protruding out of introitus with bossellated surface. The mass also extended into right ischiorectal fossa, 10 X 10 cm mass with cystic, smooth surface that was irreducible with no cough impulse. CECT abdomen and pelvis revealed a well-defined 12 X 10 X 8 cm mass in right perineum arising from right lower lateral vaginal wall with ischiorectal fossa extension. There was no extension into cervix, bladder or rectum. Biopsy taken from the mass was inconclusive. A wide local excision was done under general anesthesia wherein an ischiorectal and vaginal mass of size 30 X 10 cm with irregular margin was excised in toto. Histopathology was suggestive of Aggressive Angiomyxoma. The patient is under follow up. Discussion: Aggressive Angiomyxoma is a rare slow growing locally invasive mesenchymal tumor and has a substantial potential for recurrence. It is often misdiagnosed. Pre-operative diagnosis is difficult due to rarity of this entity and absence of diagnostic features, but it should be considered in case of masses in genital, perianal and pelvic region in a woman of reproductive age. Radical surgical excision is the first line of management. A long term follow up of the case is necessary and MRI is preferred method for detecting recurrences.

scholarly journals Aggressive Angiomyxoma of the Vulva: A Précis for Primary Care Providers

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
R. Elkattah ◽  
O. Sarkodie ◽  
H. Otteno ◽  
A. Fletcher
Keyword(s):  
Primary Care ◽  
Case Report ◽  
Literature Review ◽  
Surgical Excision ◽  
Primary Care Providers ◽  
Aggressive Angiomyxoma ◽  
Care Providers ◽  
Complete Surgical Excision ◽  
Pathologic Features ◽  
Slow Growing

Vulvar aggressive angiomyxoma (AA) is a rare mesenchymal tumor of the vulva. Due to its slow-growing nature, it is often overlooked and misdiagnosed by primary care providers (PCPs). We describe a case report of vulvar AA in a 38-year-old woman who underwent complete surgical excision of the neoplasm with no evidence of recurrence on a 5-year followup. A literature review follows to provide PCPs with the clinical, radiologic, and pathologic features that this tumor displays.

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