scholarly journals Hypoplastic Left Heart Syndrome: Diagnostic Difficulties in Prenatal Period

2021 ◽  
Vol 18 (5) ◽  
pp. 416-422
Author(s):  
Nodira M. Normuradova ◽  
Аkram A. Fazilov ◽  
Munisa M. Rasulova
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Color Doppler ◽  
Ductus Arteriosus ◽  
Interventricular Septum ◽  
Diagnostic Errors ◽  
Prenatal Period ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Atrioventricular Canal ◽  
Left Heart Syndrome

The article discusses the possible diagnostic errors in the hypoplastic left heart syndrome (HLHS) with mitral atresia and intact interventricular septum. “Atrioventricular canal defects” can be commonly and mistakenly diagnosed the prenatal period in such cases. The aspects and possibilities of differential diagnosis of these defects in the prenatal period are discussed. Ultrasound sign is presented in the article, we have named it “hockey stick with puck” that characterizes the retrograde blood flow in the aortic arch. This sign is diagnosed by color Doppler mapping of the sagittal section of the ductus arteriosus and can serve as a marker of mitral/aortic atresia.

Predictors of Ductus Arteriosus In-Stent Stenosis in the Hybrid Approach to Hypoplastic Left Heart Syndrome

2012 ◽  
Vol 34 (3) ◽  
pp. 656-660 ◽  
Author(s):  
Holly A. Nadorlik ◽  
Matthew J. Egan ◽  
Sharon L. Hill ◽  
John P. Cheatham ◽  
Mark Galantowicz ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Ductus Arteriosus ◽  
Hybrid Approach ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome ◽  
Stent Stenosis

scholarly journals Proximal ductus arteriosus stenosis after the hybrid stage I procedure in a newborn with hypoplastic left heart syndrome

2013 ◽  
Vol 2 ◽  
pp. 187-189
Author(s):  
Maciej Chojnicki ◽  
Ireneusz Haponiuk ◽  
Mariusz Steffens ◽  
Radoslaw Jaworski ◽  
Aneta Szofer-Sendrowska ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Ductus Arteriosus ◽  
Stage I ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

scholarly journals Analysis of the patients diagnosed as hypoplastic left heart syndrome at prenatal period

2014 ◽  
Vol 22 (2) ◽  
pp. 88-92
Author(s):  
Hakan Kalaycı ◽  
Halis Özdemir ◽  
Çağrı Gülümser ◽  
Ayşe Parlakgümüş ◽  
Tayfun Çok ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Prenatal Period ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Computational Modeling of Hypoplastic Left Heart Syndrome (HLHS) in Newborn Babies

2011 ◽  
Author(s):  
Ali Jalali ◽  
C. Nataraj ◽  
Gerard F. Jones ◽  
Daniel J. Licht
Keyword(s):  
Cardiac Output ◽  
Pulmonary Artery ◽  
Hypoplastic Left Heart Syndrome ◽  
Ductus Arteriosus ◽  
Compartmental Analysis ◽  
Electrical Circuit ◽  
Lumped Parameter Model ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome

Hypoplastic left heart syndrome (HLHS) is a congenital heart defect (CHD) in which left side of the heart is severely underdeveloped. To better understand this unique physiology, a computational model of the hypoplastic heart was constructed on the basis of compartmental analysis. Lumped parameter model of HLHS is developed based on the electrical circuit analogy. Model is made up of three parts: hypoplastic heart, pulmonary circulation and systemic circulation. Plots of blood pressure and flow for various parts of body show great match between predicted values and what we expected for the case of HLHS babies. Influence of patent ductus arteriosus (PDA) and ASD resistances on cardiac output and pulmonary to systemic flow was also studied. Results show that by increasing the PDA resistance causes more flow to pulmonary compartments and so the ratio increases. Blood flow increases by decreasing of pulmonary artery resistant. Increasing the PDA resistance causes decrease the cardiac output because of more resistance against blood occurs. Saturation increases by decreasing of pulmonary artery resistant.

Comparison of self-expandable and balloon-expanding stents for hybrid ductal stenting in hypoplastic left heart complex

2016 ◽  
Vol 27 (5) ◽  
pp. 837-845 ◽  
Author(s):  
Sebastian Goreczny ◽  
Shakeel A. Qureshi ◽  
Eric Rosenthal ◽  
Thomas Krasemann ◽  
Mohamed S. Nassar ◽  
...  
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Ductus Arteriosus ◽  
Left Heart ◽  
Stent Group ◽  
Hypoplastic Left Heart ◽  
Group 4 ◽  
Left Heart Syndrome ◽  
Term Performance ◽  
Hypoplastic Left Heart Complex

AbstractObjectivesWe aimed to compare the procedural and mid-term performance of a specifically designed self-expanding stent with balloon-expandable stents in patients undergoing hybrid palliation for hypoplastic left heart syndrome and its variants.BackgroundThe lack of specifically designed stents has led to off-label use of coronary, biliary, or peripheral stents in the neonatal ductus arteriosus. Recently, a self-expanding stent, specifically designed for use in hypoplastic left heart syndrome, has become available.MethodsWe carried out a retrospective cohort comparison of 69 neonates who underwent hybrid ductal stenting with balloon-expandable and self-expanding stents from December, 2005 to July, 2014.ResultsIn total, 43 balloon-expandable stents were implanted in 41 neonates and more recently 47 self-expanding stents in 28 neonates. In the balloon-expandable stents group, stent-related complications occurred in nine patients (22%), compared with one patient in the self-expanding stent group (4%). During follow-up, percutaneous re-intervention related to the ductal stent was performed in five patients (17%) in the balloon-expandable stent group and seven patients (28%) in self-expanding stents group.ConclusionsHybrid ductal stenting with self-expanding stents produced favourable results when compared with the results obtained with balloon-expandable stents. Immediate additional interventions and follow-up re-interventions were similar in both groups with complications more common in those with balloon-expandable stents.

Outcomes following prenatal diagnosis of hypoplastic left heart syndrome

2002 ◽  
Vol 13 (3) ◽  
pp. 169-180 ◽  
Author(s):  
David A Somerset ◽  
Katherine J Barber ◽  
Mark D Kilby
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Cardiac Disease ◽  
Neonatal Death ◽  
Ductus Arteriosus ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Systemic Blood ◽  
Systemic Blood Flow ◽  
Congenital Cardiac Disease ◽  
Left Heart Syndrome

Hypoplastic Left Heart Syndrome (HLHS) was first described fifty years ago. It is characterised by underdevelopment of the left ventricle with associated aortic and mitral valve hypoplasia or atresia, and varying degrees of hypoplasia of the aortic arch (Figure 1). In utero a physiological right to left shunt of oxygenated blood through the ductus arteriosus bypasses the obstruction and allows normal fetal growth. Closure of the ductus arteriosus in the post-natal period interrupts systemic blood flow, resulting in rapid deterioration and death. Untreated it is a universally fatal condition, leading to neonatal death within the first few days or weeks of life. Although HLHS affects only one baby in 10,000 and accounts for less than 10% of all congenital heart disease, HLHS is responsible for 25% of all deaths due to congenital cardiac disease occurring within the first week of life.

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