scholarly journals Malignant peripheral nerve sheath tumor of anterior abdominal wall- A rare presentation

2021 ◽  
Vol 3 (3) ◽  
pp. 81-83
Author(s):  
Benny P B ◽  
T A Vasu ◽  
Illakia Selvan ◽  
Anjali Rajan
Keyword(s):  
Early Diagnosis ◽  
Peripheral Nerve ◽  
Head And Neck ◽  
Abdominal Wall ◽  
Malignant Tumors ◽  
Anterior Abdominal Wall ◽  
Nerve Sheath Tumor ◽  
Rare Presentation ◽  
Peripheral Nerve Sheath Tumor ◽  
Nerve Sheath

Malignant peripheral nerve sheath tumor is highly malignant tumors that occur most commonly in head and neck as well as extremities. Very rarely it seen in the retroperitoneum. When associated with neurofibromatosis, they are having a poor outcome. We present a case malignant peripheral nerve sheath tumor of anterior abdominal wall. The location and rapid increase in size of the swelling permitted early diagnosis and treatment.

Anterior abdominal wall malignant peripheral nerve sheath tumor in an infant

2001 ◽  
Vol 36 (12) ◽  
pp. 1866-1868 ◽  
Author(s):  
Pelin Oğuzkurt ◽  
Fazilet Kayaşelcuk ◽  
I.Serdar Arda ◽  
Özlem Barutçu ◽  
Ilhan Tuncer ◽  
...  
Keyword(s):  
Peripheral Nerve ◽  
Abdominal Wall ◽  
Anterior Abdominal Wall ◽  
Nerve Sheath Tumor ◽  
Peripheral Nerve Sheath Tumor ◽  
Nerve Sheath

scholarly journals A CASE OF ABDOMINAL WALL MALIGNANT PERIPHERAL NERVE SHEATH TUMOR WHICH IS DIFFICULT TO DISTINGUISH FROM A URACHAL DISEASE

2013 ◽  
Vol 104 (5) ◽  
pp. 663-666
Author(s):  
Tomoyuki Tatenuma ◽  
Ryoko Sakata ◽  
Shinpei Sugiura ◽  
Takehiro Tajiri ◽  
Toshikazu Gondo ◽  
...  
Keyword(s):  
Peripheral Nerve ◽  
Abdominal Wall ◽  
Nerve Sheath Tumor ◽  
Peripheral Nerve Sheath Tumor ◽  
Nerve Sheath

scholarly journals Giant Malignant Peripheral Nerve Sheath Tumor of the Head and Neck: A Case Report and Literature Review

2020 ◽  
pp. 014556131989764 ◽  
Author(s):  
Anju Chen ◽  
Tiantian Wang ◽  
Xianfa Xu
Keyword(s):  
Peripheral Nerve ◽  
Head And Neck ◽  
Tumor Resection ◽  
Muscle Flap ◽  
Petrous Bone ◽  
Surgical Reconstruction ◽  
Temporal Region ◽  
Nerve Sheath Tumor ◽  
Peripheral Nerve Sheath Tumor ◽  
Nerve Sheath

Malignant peripheral nerve sheath tumor (MPNST) is a malignant soft tissue sarcoma with high mortality, low morbidity, and poor prognosis. The MPNST occurs mostly in the limbs and torso, and rarely in the head and neck. However, MPNST is insensitive to radiotherapy and chemotherapy, and complete surgical resection with negative margin is the most important and effective strategy. We present a case of MPNST in the head and neck. The tumor invades the left temporal bone, petrous bone, and mastoid bone, and compression changes in the focal cerebellum and sigmoid sinus. The patient underwent the left temporal region tumor resection + surgical reconstruction with temporalis muscle flap and pectoralis major myocutaneous flap. Adjuvant radiotherapy (55 Gy) was given after surgery, and there were no local recurrence and distant metastasis after 31-month follow-up.

scholarly journals Malignant Peripheral Nerve Sheath Tumor of the Anterior Mediastinum: A Rare Presentation

Rare Tumors ◽  
2014 ◽  
Vol 6 (4) ◽  
pp. 140-142 ◽  
Author(s):  
Babusha Kalra ◽  
Pamela Alice Kingsley ◽  
Harinder Singh Bedi ◽  
Kanwardeep Singh Kwatra ◽  
Preeti Negi
Keyword(s):  
Peripheral Nerve ◽  
Anterior Mediastinum ◽  
Nerve Sheath Tumor ◽  
Rare Presentation ◽  
Peripheral Nerve Sheath Tumor ◽  
Nerve Sheath

scholarly journals Malignant Peripheral Nerve Sheath Tumor of the Inguinum and Angiosarcoma of the Scalp in a Child with Neurofibromatosis Type 1

2017 ◽  
Vol 2017 ◽  
pp. 1-4
Author(s):  
Marija Milković Periša ◽  
Tihana Džombeta ◽  
Jasminka Stepan Giljević ◽  
Božo Krušlin
Keyword(s):  
Peripheral Nerve ◽  
Neurofibromatosis Type 1 ◽  
Malignant Tumors ◽  
Young Patients ◽  
Neurofibromatosis Type ◽  
Nerve Sheath Tumor ◽  
Peripheral Nerve Sheath Tumor ◽  
Nerve Sheath ◽  
The Right

Benign and malignant tumors are common in the setting of neurofibromatosis type 1 (NF1). Malignant peripheral nerve sheath tumor (MPNST) and angiosarcoma are rare tumors in children and adolescents and mostly occur in young patients in relation to NF1. Both histological types can be present in the same tumor mass in patients with NF1. We present a case of 12.5-year-old girl with NF1 who first presented with MPNST of the right inguinal region and 1.5 years later with unrelated angiosarcoma of the scalp.

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