scholarly journals Oral rehabilitation with removable dental prosthesis in a six-year-old patient with hypohidrotic ectodermal dysplasia

RSBO ◽  
2017 ◽  
Vol 1 (1) ◽  
pp. 44
Author(s):  
Mariana Dalledone ◽  
Fernanda Mara De Paiva Bertoli ◽  
Ana Paula Sponchiado ◽  
Estela Maris Losso ◽  
João Armando Brancher ◽  
...  
Keyword(s):  
Case Report ◽  
Ectodermal Dysplasia ◽  
Self Esteem ◽  
Vertical Dimension ◽  
Hypohidrotic Ectodermal Dysplasia ◽  
Oral Rehabilitation ◽  
Palatal Expansion ◽  
Expansion Procedure ◽  
Removable Dental Prosthesis

Introduction: Ectodermal dysplasia is an abnormality of the ectoderm and its derivatives, phenotypically expressed in males and genetically inherited from mothers. Objective: To report the efficacy of the prosthetics treatment of severe ectodermal dysplasia in a 6-year-old boy with hypohidrotic ectodermal dysplasia (HED). Case report: The boy had difficulty in speaking and eating and the condition also affected his self-esteem. Prosthetic treatments included the construction of acrylic custom trays, determination of the vertical dimension of occlusion (VDO), construction of upper and lower dentures, and palatal expansion procedure. Conclusion: Significant improvements in the patient’s stomatognathic functionand self-esteem were evident.

scholarly journals Oral rehabilitation with removable dental prosthesis in a six-year-old patient with hypohidrotic ectodermal dysplasia

RSBO ◽  
2017 ◽  
Vol 14 (1) ◽  
pp. 44-09
Author(s):  
Mariana Dalledone ◽  
Fernanda Mara de Paiva Bertoli ◽  
Ana Paula Sponchiado ◽  
Estela Maris Losso ◽  
João Armando Brancher ◽  
...  
Keyword(s):  
Case Report ◽  
Ectodermal Dysplasia ◽  
Self Esteem ◽  
Vertical Dimension ◽  
Hypohidrotic Ectodermal Dysplasia ◽  
Oral Rehabilitation ◽  
Palatal Expansion ◽  
Expansion Procedure ◽  
Removable Dental Prosthesis

Ectodermal dysplasia is an abnormality of the ectoderm and its derivatives, phenotypically expressed in males and genetically inherited from mothers. Objective: To report the efficacy of the prosthetics treatment of severe ectodermal dysplasia in a 6-year-old boy with hypohidrotic ectodermal dysplasia (HED). Case report: The boy had difficulty in speaking and eating and the condition also affected his self-esteem. Prosthetic treatments included the construction of acrylic custom trays, determination of the vertical dimension of occlusion (VDO), construction of upper and lower dentures, and palatal expansion procedure. Conclusion: Significant improvements in the patient’s stomatognathic function and self-esteem were evident.

scholarly journals Ectodermal dysplasia - Maxillary and mandibular alveolar reconstruction with dental rehabilitation: A case report and review of the literature

2010 ◽  
Vol 43 (01) ◽  
pp. 092-096
Author(s):  
Sanjeev N. Deshpande ◽  
Vikas Kumar
Keyword(s):  
Case Report ◽  
Ectodermal Dysplasia ◽  
Review Of The Literature ◽  
Hypohidrotic Ectodermal Dysplasia ◽  
Inherited Disorders ◽  
Oral Rehabilitation ◽  
Osseointegrated Implants ◽  
Dental Rehabilitation ◽  
Free Fibula ◽  
Rare Group

ABSTRACTEctodermal dysplasia is a rare group of inherited disorders characterized by aplasia or dysplasia of tissues of ectodermal origin, such as hair, nails, teeth and skin. Dental manifestations include hypodontia, complete anodontia or malformed teeth. Oral rehabilitation is the major surgical challenge in such patients. It frequently requires alveolar reconstruction followed by dental implants. We report a case of hypohidrotic ectodermal dysplasia, which was managed with reconstruction of both the upper and the lower alveolus using free fibula flaps with dental rehabilitation using osseointegrated implants.

Treatment Considerations for a Patient with Hypohidrotic Ectodermal Dysplasia: A Case Report

2008 ◽  
Vol 9 (3) ◽  
pp. 128-134 ◽  
Author(s):  
Dilek Tüfekcioğlu ◽  
Chenkhan Bal ◽  
Bilge Turhan Bal
Keyword(s):  
Case Report ◽  
Behavioral Problems ◽  
Ectodermal Dysplasia ◽  
Young Patients ◽  
Hair Follicles ◽  
Sweat Glands ◽  
Clinical Report ◽  
Hypohidrotic Ectodermal Dysplasia ◽  
Oral Rehabilitation ◽  
Treatment Considerations

Abstract Aim This clinical report describes the oral rehabilitation of a 6-year-old male ectodermal dysplasia (ED) patient diagnosed with hypodontia. Background ED is a hereditary disease characterized by a congenital dysplasia of one or more ectodermal structures and their accessory appendages. Common manifestations include defective hair follicles and eyebrows, frontal bossing with prominent supraorbital ridges, nasal bridge depression, and protuberant lips. Intraorally, most common findings are anadontia or hypodontia, conical teeth, and generalize spaces. The patient may suffer from dry skin, hyperthermia, and unexplained high fever as a result of deficiency of sweat glands. Report A six-year-old boy who exhibited many of the manifestations of ED as well as behavioral problems and a severe gag reflex. The treatment was designed to improve his appearance and oral functions and included the fabrication of several removable prostheses and acid-etched composite resin restorations during his growth and development. Summary Young patients with ED need to be evaluated early by a dental professional to determine the oral ramifications of the condition. When indicated, appropriate care needs to be rendered throughout the child's growth cycle to maintain oral functions as well as to address the esthetic needs of the patient. This clinical report demonstrates that removable partial dentures associated with direct composite restorations can be a reversible and inexpensive method of treatment for young ED patients. Citation Bal C, Bal BT, Casela L, Tüfekçioğlu D. Treatment Considerations for a Patient with Hypohidrotic Ectodermal Dysplasia: A Case Report. J Contemp Dent Pract 2008 March; (9)3:128-134.

scholarly journals A Hybrid Oral Rehabilitation of Hypohidrotic Ectodermal Dysplasia: A Conservative Approach with Three-Year Follow-Up

2021 ◽  
Vol 2021 ◽  
pp. 1-6
Author(s):  
Aryen Kaushik ◽  
HarshVardhan Sinha ◽  
M. N. Hombesh ◽  
Pooja Rani ◽  
Taranjeet Kaur
Keyword(s):  
Ectodermal Dysplasia ◽  
Vertical Dimension ◽  
Hypohidrotic Ectodermal Dysplasia ◽  
Oral Rehabilitation ◽  
Removable Partial Denture ◽  
Partial Denture ◽  
Long Span ◽  
Clinical Scenarios ◽  
Atraumatic Extraction ◽  
And Coping

This case report presents a 19-year-old male patient with hypohidrotic ectodermal dysplasia, having a chief complaint of multiple missing teeth. Atraumatic extraction of the teeth with hopeless prognosis was done, and teeth with grade 2 mobility were submerged using cast dowel and coping. Following this, incremental increase in the vertical dimension was made using removable flexible splint of two-millimeter thickness. After facebow transfer and making appropriate eccentric bite records to program the semiadjustable articulator, wax-up was done at the desired vertical dimension (VD). The upper arch was finally restored using a long-span fixed partial denture and lower arch using bilateral attachment (Rhein 83) retained cast removable partial denture as a definitive prosthesis. Therefore, in conditions like hypodontia or oligodontia caused due to ectodermal dysplasia, attachment retained removable partial denture may prove beneficial by effectively distributing the occlusal forces. In clinical scenarios where implant is not feasible or not opted by the patient, this combination treatment may be a viable option.

scholarly journals EDA mutation as a cause of hypohidrotic ectodermal dysplasia: a case report and review of the literature

2015 ◽  
Vol 14 (3) ◽  
pp. 10344-10351 ◽  
Author(s):  
S.X. Huang ◽  
J.L. Liang ◽  
W.G. Sui ◽  
H. Lin ◽  
W. Xue ◽  
...  
Keyword(s):  
Case Report ◽  
Ectodermal Dysplasia ◽  
Review Of The Literature ◽  
Hypohidrotic Ectodermal Dysplasia

Clinical management of hypohidrotic ectodermal dysplasia with anodontia: case report

2003 ◽  
Vol 27 (1) ◽  
pp. 5-8 ◽  
Author(s):  
Ekaterini Paschos ◽  
Karin Christine Huth ◽  
Reinhard Hickel
Keyword(s):  
Case Report ◽  
Young Child ◽  
Clinical Management ◽  
Ectodermal Dysplasia ◽  
Psychological Development ◽  
Early Age ◽  
Complete Dentures ◽  
Hypohidrotic Ectodermal Dysplasia ◽  
Need For Treatment ◽  
Stomatognathic System

Ectodermal dysplasia is a rare hereditary disorder with a characteristic physiognomy. The case of a 5-year-old child with hypohidrotic ectodermal dysplasia and complete anodontia is presented. Because of the anodontia and the need for treatment at an early age, the prosthetic management of such a young child can be difficult. Complete dentures were provided to encourage a normal psychological development and to improve the function of the stomatognathic system.

Case report: Higher-than-expected prevalence of hypohidrotic ectodermal dysplasia in a rural Mexican setting: report of 20 cases

2010 ◽  
Vol 49 (9) ◽  
pp. 1050-1055 ◽  
Author(s):  
Nayellin Reyes-Chicuellar ◽  
Roberto De Haro ◽  
Rafael Jiménez-Flores ◽  
Jovita Monje-Martínez ◽  
Norma Motta-Castañeda ◽  
...  
Keyword(s):  
Case Report ◽  
Ectodermal Dysplasia ◽  
Hypohidrotic Ectodermal Dysplasia

scholarly journals A novel EDA variant causing X-linked hypohidrotic ectodermal dysplasia: Case report

2021 ◽  
Vol 29 ◽  
pp. 100796
Author(s):  
Baiba Alksere ◽  
Liene Kornejeva ◽  
Ieva Grinfelde ◽  
Aigars Dzalbs ◽  
Dace Enkure ◽  
...  
Keyword(s):  
Case Report ◽  
Ectodermal Dysplasia ◽  
Hypohidrotic Ectodermal Dysplasia

scholarly journals Use of Occlusal Splints in Patients with Deep Bite and Bruxism

2018 ◽  
Vol 2 (1) ◽  
pp. 427-431
Author(s):  
Paulina Lozano
Keyword(s):  
Case Report ◽  
Male Patient ◽  
Temporomandibular Disorders ◽  
Vertical Dimension ◽  
Oral Rehabilitation ◽  
Deep Bite ◽  
Full Coverage ◽  
Occlusal Splints ◽  
Intraoral Devices

The occlusal splints are most commonly used devices for the treatment of temporomandibular disorders and bruxism. A case report of a male patient with deep bite and bruxism, indicating two flat occlusal splints presents full coverage made up of rigid acrylic and permanent use for five months is described. Using both intraoral devices allowed restoring lost vertical dimension and protect teeth attrition, deprogram the musculature and establish a new mandibular positioning prior to treatment of oral rehabilitation.

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