Langerhans' Cell Histiocytosis Showing Low-Attenuation Mediastinal Mass and Cystic Lung Disease

2000 ◽  
Vol 174 (3) ◽  
pp. 877-878 ◽  
Author(s):  
Lane F. Donnelly ◽  
Donald P. Frush
Keyword(s):  
Lung Disease ◽  
Langerhans Cell Histiocytosis ◽  
Mediastinal Mass ◽  
Langerhans Cell ◽  
Cystic Lung ◽  
Cystic Lung Disease

scholarly journals Paediatric pulmonary Langerhans cell histiocytosis

Breathe ◽  
2020 ◽  
Vol 16 (2) ◽  
pp. 200003
Author(s):  
Mhairi Barclay ◽  
Rebecca Devaney ◽  
Jayesh. M. Bhatt
Keyword(s):  
Respiratory Failure ◽  
Lung Disease ◽  
Langerhans Cell Histiocytosis ◽  
Multidisciplinary Treatment ◽  
Langerhans Cell ◽  
List Type ◽  
Cystic Lung ◽  
Pulmonary Langerhans Cell Histiocytosis ◽  
Cystic Lung Disease ◽  
Management Of Complications

Paediatric pulmonary Langerhans cell histiocytosis (pPLCH) is a rare diffuse cystic lung disease. Unlike pulmonary Langerhans cell histiocytosis (LCH) in adults, which is often seen as an isolated condition with smoking being a major risk factor, isolated pPLCH is vanishingly rare in children and it is most often a component of multisystem LCH. Diagnosis should be based on histological and immunophenotypic examination of affected tissue in addition to clinical and radiological features. It should be considered an important differential for diffuse cystic lung disease in paediatric patients. Recent progress in the biological understanding of the disease supports the classification of LCH as an inflammatory myeloid neoplasia. Chemotherapy and specific management of respiratory complications are the mainstays of treatment. The lungs are no longer considered a “risk organ” in LCH as pulmonary involvement is not associated with a worse prognosis than the involvement of other organs. Multidisciplinary treatment approaches are needed.Prognosis can be good but is adversely influenced by multisystem involvement, and complications such as pneumothoraces and respiratory failure can be life threatening. This review aims to give an overview of this condition, with a focus on the diagnosis, monitoring and management of complications such as pneumothoraces and respiratory failure, which can be challenging for the paediatric respiratory specialist.Educational aimsTo give an overview of paediatric pulmonary LCH.To discuss the differential diagnosis of paediatric cystic lung disease.

Cystic Lung Disease

Chest Imaging ◽  
2019 ◽  
pp. 429-433
Author(s):  
Juliana Bueno
Keyword(s):  
Lung Disease ◽  
Langerhans Cell Histiocytosis ◽  
Normal Lung ◽  
Lung Cysts ◽  
Cystic Lung ◽  
Pulmonary Langerhans Cell Histiocytosis ◽  
Cystic Lung Disease ◽  
Lymphocytic Interstitial Pneumonia ◽  
Cavitary Disease ◽  
Diffuse Lung

A lung cyst is a round parenchymal lucency or low-attenuating area with a well-defined interface with adjacent normal lung and surrounded by an epithelial or fibrous wall that is often less than 2 mm in thickness. Diseases that manifest with lung cysts comprise a limited but well known group of entities. Classic diseases manifesting with diffuse lung cysts include pulmonary Langerhans cell histiocytosis (PLCH), lymphangioleiomyomatosis (LAM), lymphocytic interstitial pneumonia (LIP) and Birt-Hogg-Dubé syndrome. However, it is important to recognize other conditions that may mimic cystic lung disease, such as pneumatoceles, tracheobronchial papillomatosis, cavitary disease (e.g. tuberculosis, fungal infection), bronchiectasis, and emphysema. Differentiation between true cysts and cyst mimics may be difficult, and may rely on identification of ancillary findings.

scholarly journals COVID-19 pneumonitis and cystic lung disease, pneumothorax and pneumomediastinum

Thorax ◽  
2021 ◽  
pp. thoraxjnl-2021-217390
Author(s):  
Serenydd Everden ◽  
Irfan Zaki ◽  
Gareth Trevelyan ◽  
James Briggs
Keyword(s):  
Lung Disease ◽  
Cystic Lung ◽  
Cystic Lung Disease

Congenital Pulmonary Airway Malformation Presenting as Unilateral Cystic Lung Disease

2013 ◽  
Vol 188 (8) ◽  
pp. 1030-1031 ◽  
Author(s):  
Eric D. McLoney ◽  
Philip T. Diaz ◽  
Jerry Tran ◽  
Konstantin Shilo ◽  
Subha Ghosh
Keyword(s):  
Lung Disease ◽  
Congenital Pulmonary Airway Malformation ◽  
Cystic Lung ◽  
Cystic Lung Disease ◽  
Pulmonary Airway

Congenital mydriasis, patent ductus arteriosus, and congenital cystic lung disease: New syndromic spectrum?

2004 ◽  
Vol 131A (3) ◽  
pp. 318-319 ◽  
Author(s):  
Benjamin D. Lemire ◽  
J.R. Buncic ◽  
Shelley J. Kennedy ◽  
Sarah J. Dyack ◽  
Ahmad S. Teebi
Keyword(s):  
Patent Ductus Arteriosus ◽  
Lung Disease ◽  
Ductus Arteriosus ◽  
Cystic Lung ◽  
Cystic Lung Disease ◽  
Congenital Cystic Lung Disease ◽  
Patent Ductus

scholarly journals Diffuse Cystic Lung Disease. Part II

2015 ◽  
Vol 192 (1) ◽  
pp. 17-29 ◽  
Author(s):  
Nishant Gupta ◽  
Robert Vassallo ◽  
Kathryn A. Wikenheiser-Brokamp ◽  
Francis X. McCormack
Keyword(s):  
Lung Disease ◽  
Cystic Lung ◽  
Cystic Lung Disease
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