Follicular atrophoderma with multiple basal cell carcinomas. An abortive form of bazex syndrome.

1989 ◽  
Vol 51 (2) ◽  
pp. 250-255
Author(s):  
Seiji ARASE ◽  
Hideki NAKANISHI ◽  
Shin HARADA ◽  
Fumio SHIGEMI ◽  
Katsuyuki TAKEDA
Rare Tumors ◽  
2021 ◽  
Vol 13 ◽  
pp. 203636132110264
Author(s):  
Andrea Dekanić ◽  
Marko Velepič ◽  
Margita Belušić Gobić ◽  
Ita Hadžisejdić ◽  
Nives Jonjić

Malignant mesenchymal tumors of oropharyngeal mucosa are rare. Those with fibroblastic and histiocytic differentiation in the skin are called atypical fibroxanthoma (AFX) and in the soft tissue undifferentiated pleomorphic sarcoma (UPS). Here we present a case of an older patient with a history of multiple basal cell carcinomas and recently with a rapidly growing polypoid lesion in the mucosa of posterior oropharyngeal wall with AFX/UPS morphology. The differential diagnosis, histological pitfalls of this poorly characterized mesenchymal lesions, and the challenges associated with treatment are discussed.


Author(s):  
Vincent Hoffmann ◽  
Ralf Husak ◽  
Fritz Maiwirth ◽  
Bianca Sasama ◽  
Axel Zahn ◽  
...  

2009 ◽  
Vol 12 (1) ◽  
pp. 61-64
Author(s):  
R Rosti ◽  
A Irem ◽  
H Kayserili ◽  
S Yalcin

Gorlin's Syndrome: Case Report and Management ProtocolGorlin's syndrome (GS) is a rare autosomal, dominant syndrome, characterized by multiple basal cell carcinomas, odontogenic keratocysts, a characteristic facial appearance, skeletal anomalies and malignancies of various organs throughout the body. We describe a 14-year-old girl with GS and propose a management protocol.


2018 ◽  
Vol 45 (10) ◽  
pp. 1187-1190
Author(s):  
Koji Adachi ◽  
Yuichi Yoshida ◽  
Hisashi Noma ◽  
Hiroyuki Goto ◽  
Osamu Yamamoto

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