'Budd Chiari Syndrome' - A Case Report

'Budd Chiari syndrome (BCS)' is an uncommon condition induced by thrombotic or nonthrombotic obstruction to hepatic venous outflow. This disease can be potentially life-threatening but prognosis is more favorable in patient with IVC webs but is extremely poor in malignant and haematological cases. A cooperative collaboration of hepatologist and cardiologist can make the situation easy for diagnosis, even in treatment of some cases. (University Heart Journal 2007; 3 : 80-82)

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Case Report: Budd Chiari Syndrome

Journal of Pharmaceutical Research International ◽

10.9734/jpri/2021/v33i58a34082 ◽

2021 ◽

pp. 8-12

Author(s):

Seema Singh ◽

Sonali Wawre ◽

Savita Poheka r ◽

Aarti Raut ◽

Samruddhi Gujar ◽

...

Keyword(s):

Case Report ◽

Rare Condition ◽

Acute Onset ◽

Budd Chiari Syndrome ◽

Venous Outflow ◽

Ultrasound Technique ◽

Chiari Syndrome ◽

History Of ◽

Hepatic Venous Outflow ◽

Comprehensive History

Budd-syndrome Chiari's is a rare condition is causes by obstruction to hepatic venous outflow. The female patient 25-year old who was admitted to Acharya Vinoba Bahave Rural Hospital on date 19/06/2019. 4 months ago, she noticed that her abdomen had become prominent. Her appetite became poor and she had vomiting bouts whenever she took food. A detailed clinical evaluation of the The syndrome of Budd-Chiari is based on a comprehensive history of of the patient, angiography is often used to assist in the diagnosis. The treatment also uses (MRI) and ultrasound technique. If the condition is detected early, treatment of Budd-Chiari syndrome is more effective. Large doses of corticosteroid, prednisone can also be recommended as heparin like anticoagulants can be efficient in the treatment of Budd-Chiari syndrome individuals. However, the condition typically has an acute onset and can become chronic later in life. The present case with right anticoagulant therapy, early diagnosis and successful treatment is reported.

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Budd-Chiari Syndrome in Childhood Secondary to Inferior Vena Caval Obstruction

PEDIATRICS ◽

10.1542/peds.63.5.808 ◽

1979 ◽

Vol 63 (5) ◽

pp. 808-812

Author(s):

Arvind Taneja ◽

S. K. Mitra ◽

P. D. Moghe ◽

P. N. Rao ◽

N. Samanta ◽

...

Keyword(s):

Inferior Vena ◽

Vena Cava ◽

Hepatic Veins ◽

Budd Chiari Syndrome ◽

Venous Outflow ◽

Massive Ascites ◽

Inferior Vena Caval ◽

Uncommon Disease ◽

Chiari Syndrome ◽

Hepatic Venous Outflow

Budd-Chiari syndrome is an uncommon disease caused by an obstruction to hepatic venous outflow either at the level of the hepatic veins or in the hepatic part of the inferior vena cava. Clinically, it presents with ascites, abdominal pain, hepatomegaly, edema, and occasionally jaundice. The syndrome was first recognised by Lamboran1 in 1842 and later described by Budd2 in 1846 and Chiari3 in 1899. The syndrome is caused by obstruction to the hepatic veins. In the Fig 1. Photograph showing massive ascites and dilated superficial abdominal veins. majority of cases, the obstruction is ascribed to obliterative thrombophlebitis of unknown cause.4

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A young man with progressive jaundice and abdominal distension

Thai Journal of Hepatology ◽

10.30856/th.jhep2019vol2iss1_02 ◽

2019 ◽

Vol 2 (1) ◽

pp. 6-8

Author(s):

Sith Siramolpiwat ◽

Tanabute Limprukkasem

Keyword(s):

Abdominal Distension ◽

Caudate Lobe ◽

Hepatic Veins ◽

Budd Chiari Syndrome ◽

Complete Obliteration ◽

Chiari Syndrome ◽

Life Threatening ◽

Hepatic Venous Outflow ◽

Complete Thrombosis ◽

Upper Abdomen

Budd-Chiari syndrome (BCS) is a rare, life-threatening disease caused by obstruction of hepatic venous outflow. Common presentations are right upper quadrant pain, ascites, and hepatomegaly. A diagnosis of Budd-Chiari syndrome should be suspected when liver disease occurs in a patient with known risk factors for hypercoagulable state. We report a 22-years old transgender man presented with jaundice, marked ascites and hepatomegaly. Imaging studies showed complete thrombosis of all hepatic veins. Finally, he was diagnosed with Budd-Chiari syndrome with antiphospholipid syndrome. Figure 1 ภาพ CT upper abdomen แสดงให้เห็น marked ascites with heterogeneous liver enhancement, complete obliteration of all hepatic, caudate lobe hypertrophy, small intrahepatic venous collateral และ small arterial enhancing nodules

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Budd-Chiari Syndrome - Hepatic Venous Outflow Tract Obstruction

Portal Hypertension V ◽

10.1002/9781444393989.ch13 ◽

2010 ◽

pp. 141-150

Author(s):

Dominique-Charles Valla

Keyword(s):

Outflow Tract ◽

Budd Chiari Syndrome ◽

Venous Outflow ◽

Chiari Syndrome ◽

Hepatic Venous Outflow

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The Spectrum of Histologic Findings in Hepatic Outflow Obstruction

Archives of Pathology & Laboratory Medicine ◽

10.5858/arpa.2015-0388-oa ◽

2016 ◽

Vol 141 (1) ◽

pp. 98-103 ◽

Cited By ~ 7

Author(s):

Raul S. Gonzalez ◽

Michael A. Gilger ◽

Won Jae Huh ◽

Mary Kay Washington

Keyword(s):

Portal Tract ◽

Central Vein ◽

Budd Chiari Syndrome ◽

Outflow Obstruction ◽

Venous Outflow ◽

Ductular Reaction ◽

Chiari Syndrome ◽

Hepatic Venous Outflow ◽

Venous Outflow Obstruction ◽

Hematoxylin And Eosin

Context.—Cardiac hepatopathy and Budd-Chiari syndrome are 2 forms of hepatic venous outflow obstruction with different pathophysiology but overlapping histologic findings, including sinusoidal dilation and centrilobular necrosis. Objective.—To determine whether a constellation of morphologic findings could help distinguish between the 2 and could suggest the diagnoses in previously undiagnosed patients. Design.—We identified 26 specimens with a diagnosis of cardiac hepatopathy and 23 with a diagnosis of Budd-Chiari syndrome. Slides stained with hematoxylin and eosin and with trichrome were evaluated for several distinctive histologic findings. Results.—Features common to both forms of hepatic outflow obstruction included sinusoidal dilation and portal tract changes of fibrosis, chronic inflammation, and bile ductular reaction. Histologic findings significantly more common in cardiac hepatopathy included pericellular/sinusoidal fibrosis and fibrosis around the central vein. Only centrilobular hepatocyte dropout/necrosis was significantly more common in Budd-Chiari, regardless of duration. Conclusions.—The finding of pericellular/sinusoidal fibrosis in cardiac hepatopathy compared with Budd-Chiari is not unexpected, given the chronic nature of most cardiac hepatopathy. Portal tract changes are common in both forms of hepatic outflow obstruction and should not deter one from making the diagnosis of hepatic outflow obstruction. Fibrosis along sinusoids and around the central vein may be suggestive of cardiac hepatopathy in biopsies from patients without a prior diagnosis.

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