scholarly journals Case Report: Pericardial Effusion Treated With Pericardiectomy Plus Right Atrial Mass Resection: A 2-Year Follow-Up of Cardiac Rosai-Dorfman Disease

2021 ◽  
Vol 8 ◽  
Author(s):  
Edoardo Conte ◽  
Antonio Brucato ◽  
Francesco Petrella ◽  
Emanuela Passoni ◽  
Gianfranco Lauri ◽  
...  

Background: Rosai-Dorfman disease (RDD) is rare a sinus histiocytosis typically causing lymphadenopathy. Heart involvement is anecdotal, and <30 cases of cardiac RDD (cRDD) have been reported so far.Case Presentation: A 46-year old woman with positive clinical history for RDD was admitted to our cardiology department with transthoracic echocardiography diagnosis of severe pericardial effusion and right atrial masses. Pericardiocentesis with catheter insertion was performed 3 days after the admission due to clinical evidence of cardiac tamponade. After 10 weeks of maximal medical therapy for inflammatory pericarditis, including non-steroidal anti-inflammatory drugs (NSAIDs), colchicine, steroids, and anakinra, at least 100 ml of pericardial citric liquid has been daily drained suggesting no clinical improvement. Pericardial liquid analysis demonstrated no malignant cells, but immunohistochemical analysis resulted positive for AE1–AE3, D2–40, S100, and CD68 consistent with an RDD diagnosis. Surgical management was judged clinically indicated, and 2 months after admission, the patient underwent pericardiectomy and debulking of atrial mass with freezing of remaining atrial neoformation. Regular clinical and echocardiography evaluation was performed without pericardial effusion recurrence after 2 years of follow-up.Conclusions: This is the first case ever reported of cRDD who survived after 2 years of follow-up. Pericardiectomy could be feasible and effective for recurrent pericardial effusion in cRDD. Close follow-up and a multidisciplinary environment is needed to take care of cRDD patients.

2003 ◽  
Vol 58 (2) ◽  
pp. 155-158 ◽  
Author(s):  
Cevdet ERDÖL ◽  
Ercüment OVALI ◽  
Merih BAYKAN

2013 ◽  
Vol 4 (1) ◽  
pp. 68-70 ◽  
Author(s):  
Smita Sarma ◽  
Navin Kumar ◽  
Sunil Sharma ◽  
Manish Bansal ◽  
Ravi R. Kasliwal ◽  
...  

2011 ◽  
Vol 27 (3) ◽  
pp. 362-362 ◽  
Author(s):  
Justin Chan ◽  
Jitendra Kumar ◽  
Andrew Cheng ◽  
Cheng-Hon Yap ◽  
Xiao Bo Zhang

2015 ◽  
Vol 67 (5) ◽  
pp. 485-488 ◽  
Author(s):  
Mohamad Lazkani ◽  
Tomas Rivera-Bonilla ◽  
Moneer Eddin ◽  
Sudhakar Girotra ◽  
Ashish Pershad

2018 ◽  
Vol 2018 ◽  
pp. 1-3 ◽  
Author(s):  
Fahad Syed Naseerullah ◽  
Hemangkumar Javaiya ◽  
Avinash Murthy

Primary tumours of the heart are often encountered in clinical practice. Different autopsy series estimate the incidence to be anywhere from 0.001% to 0.19%. Cardiac lipoma is a rare type of tumour of the heart and pericardium. It comprises approximately 10–19% of all cardiac tumours. We present a case of a large cardiac lipoma in a fifty-year-old female. She presented with sharp chest pains, palpitations, and dizziness. Acute coronary syndrome was ruled out. A transthoracic echocardiogram showed an abnormal, large, fixed right atrial mass. The mass was noted to be occupying most of the right atrium. It was excised due to its large size and persistent symptoms. On pathophysiology, the mass was definitively diagnosed to be an 80 mm × 70 mm cardiac lipoma. Postoperatively, the patient did well with resolution of her symptoms. This case provides evidence that even large, invasive, symptomatic cardiac lipomas can be successfully resected with good outcomes.


2012 ◽  
Vol 43 (6) ◽  
pp. 958-960 ◽  
Author(s):  
Lauren Xu ◽  
Jean Jeudy ◽  
Allen P. Burke

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