rosai dorfman disease
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Author(s):  
Sofia Garces ◽  
L. Jeffrey Medeiros ◽  
Mario Luiz Marques-Piubelli ◽  
Sheila Aparecida Coelho Siqueira ◽  
Roberto N. Miranda ◽  
...  

Author(s):  
Satoshi Kurahashi ◽  
Naohiro Toda ◽  
Masaaki Fujita ◽  
Katsuya Tanigaki ◽  
Jun Takeoka ◽  
...  

Author(s):  
Rabiul Karim ◽  
Mohammad Majed Sultan ◽  
Kamal Hossain ◽  
Himel Chowdhury ◽  
Moshiur Rahman

2021 ◽  
Vol 9 (1) ◽  
pp. 40-45
Author(s):  
Amit Gupta ◽  
Aditya Menon ◽  
Ravi Bhadiyadra ◽  
Ramesh Deshpande ◽  
Vikas M Agashe

2021 ◽  
Author(s):  
José Luis Navarro-Olvera ◽  
Armando Armas-Salazar ◽  
José Damián Carrillo-Ruiz ◽  
Jesús Q. Beltrán ◽  
Gustavo Parra-Romero ◽  
...  

This chapter describes the epidemiology, clinical and neuroimaging features, histological characteristics, surgical approach, outcomes, and prognostic factors of different cases of very rare intracranial tumors, associated with complex clinical syndromes. Highlighting the important aspects in the diagnosis and management that were considered relevant through the experience of our center. Here we included an intracranial Rosai-Dorfman disease manifested as an apparent multiple meningiomatosis, a choroid plexus papilloma clinically manifested as a hemifacial spasm originated by a compression of the facial colliculus, and a neuroenteric cyst associated with Klippel-Feil syndrome. This type of tumor presents a challenge to the neurosurgeon, originating various questions about its management. In this chapter, we present the experience we had with these pathologies to establish the most appropriate management decisions.


2021 ◽  
Vol 146 (1) ◽  
pp. 40-46
Author(s):  
Roberto A. Garcia ◽  
Edward F. DiCarlo

Context.— Rosai-Dorfman disease is a rare histiocytic proliferative disorder of unknown pathogenesis that may be diagnostically difficult in extranodal sites. It is commonly an unsuspected diagnosis when arising in bone and soft tissue, especially when it presents without associated lymphadenopathy. Its variable clinical presentation and nonspecific imaging findings make the diagnosis quite challenging, particularly in small biopsies. The problem is compounded by its less-characteristic histomorphologic features in comparison with nodal disease. Awareness of the potential diagnostic pitfalls in Rosai-Dorfman disease of bone and soft tissue should raise the degree of diagnostic accuracy. Objective.— To review the clinical manifestations, imaging characteristics, and histomorphologic features of Rosai-Dorfman disease of bone and soft tissue along with a brief discussion of its differential diagnosis, pathogenesis, and current management. Data Sources.— Thorough review of the literature with focus on clinical manifestations, imaging findings, key histomorphologic features, pathogenesis, and treatment. Conclusions.— The diagnosis of Rosai-Dorfman disease of bone and soft tissue may be quite challenging because of its variable clinical presentation and nonspecific imaging findings. It may be asymptomatic without systemic manifestations or associated lymphadenopathy. The definitive diagnosis relies on histopathologic identification of the characteristic S-100–positive histiocytes demonstrating emperipolesis. Bone and soft tissue lesions tend to have lower numbers of characteristic histiocytes and less conspicuous emperipolesis and often demonstrate areas of fibrosis or storiform spindle cell areas resembling fibrohistiocytic lesions. Awareness of these unusual features is necessary in order to consider Rosai-Dorfman disease in the differential diagnosis when confronting these rare and often misleading lesions.


2021 ◽  
Author(s):  
Anne Thieme ◽  
Katja Maurus ◽  
Karen Ernestus ◽  
Steffen Hirsch ◽  
Kathrin Schramm ◽  
...  

2021 ◽  
Vol 104 (12) ◽  
pp. 1988-1991

Rosai-Dorfman disease (RDD) manifesting as a solitary osseous lesion especially of talus bone is rare. The authors reported a 31-year-old Thai man who had chronic left ankle pain and the biopsy of his talar lesion demonstrated emperipolesis, the typical histological feature of RDD. He was treated with curettage and adjuvant bisphosphonate and appeared to show improvement in clinical symptoms and radiological evidence. To the authors’ knowledge, this is the first report of an intraosseous RDD lesion treated with bisphosphonate with imaging follow-up. Keywords: Rosai-Dorfman disease; Talus; Solitary; Radiology; Bisphosphonate


2021 ◽  
pp. 31-32
Author(s):  
Gridhati Srinivas ◽  
Tarun Kumar Dutta

Rosai-Dorfman disease (RDD) is a rare, benign, and predominantly nodal disease that most commonly presents as bilateral, painless cervical lymphadenopathy; although inguinal, axillary, mediastinal, and hilar lymphadenopathy has also been reported. Apart from nodal involvement, RDD has extra nodal manifestations involving bone, soft tissue, and liver as well as constitutional symptoms of fever, night sweats, and weight loss, which make it reasonable to rule out the infectious, autoimmune, and malignant conditions as the differential diagnosis.


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