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Faculty Opinions recommendation of Effects of ivacaftor in patients with cystic fibrosis who carry the G551D mutation and have severe lung disease.
Faculty Opinions – Post-Publication Peer Review of the Biomedical Literature
◽
10.3410/f.718276081.793491279
◽
2014
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Author(s):
James Chmiel
◽
Danielle Goetz
Keyword(s):
Cystic Fibrosis
◽
Lung Disease
◽
Severe Lung Disease
◽
Severe Lung
Download Full-text
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10.1016/s1569-1993(21)01066-3
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The use of ivacaftor in an adult with severe lung disease due to cystic fibrosis (ΔF508/G551D)
Journal of Cystic Fibrosis
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10.1016/j.jcf.2012.12.004
◽
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◽
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◽
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P209 Use of lumacaftor/ivacaftor as rescue therapy and stabilisation treatment for severe lung disease in children with cystic fibrosis
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◽
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◽
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◽
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◽
pp. S116
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◽
G. Connett
◽
A. Dewar
◽
W. Verling
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Cystic Fibrosis
◽
Lung Disease
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Rescue Therapy
◽
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◽
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P255 Clinical stabilisation following ivacaftor in patients with cystic fibrosis, severe lung disease and rare CFTR mutation: a report of two cases
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◽
10.1016/s1569-1993(19)30548-x
◽
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◽
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◽
pp. S129
Author(s):
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◽
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◽
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...
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Association of chronicCandida albicansrespiratory infection with a more severe lung disease in patients with cystic fibrosis
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10.1002/ppul.23302
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A multicentre, observational cohort study to determine the efficacy and safety of lumacaftor/ivacaftor in patients with severe lung disease and cystic fibrosis
10.1183/13993003.congress-2019.oa2126
◽
2019
◽
Author(s):
Koliarne Tong
◽
Douglas Dorahy
◽
Megan France
◽
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◽
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◽
...
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Efficacy And Safety
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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Effect of low altitude at the Dead Sea on exercise capacity and cardiopulmonary response to exercise in cystic fibrosis patients with moderate to severe lung disease
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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◽
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Management dilemma; a woman with cystic fibrosis and severe lung disease presenting with colonic carcinoma: a case report
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◽
10.1186/1752-1947-2-384
◽
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◽
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◽
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42 Effects of ivacaftor in an adult patient with cystic fibrosis who carries the 3272-26A → G mutation, resulting in residual functioning protein, and has severe lung disease
Journal of Cystic Fibrosis
◽
10.1016/s1569-1993(17)30407-1
◽
2017
◽
Vol 16
◽
pp. S74
Author(s):
D. Salvatore
◽
C. Colangelo
◽
M. D'Andria
◽
G. Marsicovetere
◽
D. Passarella
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Cystic Fibrosis
◽
Lung Disease
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Adult Patient
◽
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Severe Lung
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