scholarly journals Dental behavior management of a patient with osteogenesis imperfecta type V: case report

2020 ◽  
Vol 28 (87) ◽  
Author(s):  
Danilo Cassiano Ferraz ◽  
Ana Luiza Rodrigues Ribeiro ◽  
Ronan Machado de Alcântra ◽  
Alessandra Maia de Castro ◽  
Fabiana Sodré de Oliveira ◽  
...  
Keyword(s):  
Osteogenesis Imperfecta ◽  
Behavior Management ◽  
Parental Education ◽  
Bone Fractures ◽  
Pediatric Dentistry ◽  
Bone Fragility ◽  
Osteogenesis Imperfecta Type ◽  
Dental Biofilm ◽  
Stabilization Technique ◽  
Type V

Aim: the aim of this study is to report a case of a four-year-old male patient diagnosed with Osteogenesis Imperfecta (OI) type V and the dental care performed.  Material and method: the patient has been monitored by a multidisciplinary team composed by Pediatric Dentistry, Nurse and Nutritionist at a Special Patients Center in Dentistry Hospital on the Federal University of Uberlândia since one month of life. It was reported that a child had already suffered several bone fractures and currently he has been using calcium carbonate, D vitamin and pamidronate. Results: the proposed intervention was dental preventive strategies by parental education, caries risk assessment and controlling the dental biofilm with professional prophylaxis. But, due to the uncooperative behavior, it was used the active protective stabilization technique and mouth opener. Conclusion: it was concluded that due to the bone fragility and the risk of fractures, it is important a careful placement of the patient on the dental chair. Also, the correct use of basic auxiliary devices and advanced techniques of behavior management were relevant.

scholarly journals Osteogenesis Imperfecta (Type IV) with Dental Findings in Siblings

2011 ◽  
Vol 2011 ◽  
pp. 1-4 ◽  
Author(s):  
Shishir Ram Shetty ◽  
Deepa Dsouza ◽  
Subhas Babu ◽  
Preethi Balan
Keyword(s):  
Osteogenesis Imperfecta ◽  
Bone Fractures ◽  
Age Groups ◽  
Bone Fragility ◽  
Osteogenesis Imperfecta Type ◽  
Recessive Factor ◽  
Radiological Features ◽  
Type Iv ◽  
History Of ◽  
Blue Sclera

Osteogenesis imperfecta (OI) is a hereditary disorder characterized by increased tendency for bone fractures due to high fragility. The clinical and radiological features of OI manifest in different age groups, although the disease is congenital in nature. Besides bone fragility, features like laxity of the ligaments, blue sclera, growth retardation, and scoliosis are also observed. In severe cases, respiratory distress and death have been reported. The most important oral finding in OI is the presence of yellowish-brown-coloured brittle teeth characteristic of dentinogenesis imperfecta. Genetic factors play a very important role in the pathogenesis of OI either as a dominant or recessive factor. When a child has OI, there is a 25% chance of the sibling to have the same disorder. We report two cases of OI in siblings born to parents with a history of consanguineous marriage. The clinical and radiological features of the two cases are described in detail.

A new start-codon in IFITM5 causes osteogenesis imperfecta type V

2013 ◽  
Author(s):  
Semler Oliver ◽  
Hoyer-Kuhn Heike ◽  
Garbes Lutz ◽  
Netzer Christian ◽  
Schoenau Eckhard
Keyword(s):  
Osteogenesis Imperfecta ◽  
Start Codon ◽  
Osteogenesis Imperfecta Type ◽  
Type V

Osteogenesis imperfecta type V due to a rare mutation c.119C> T in the IFITM5: A case report

2020 ◽  
Author(s):  
Tatiana Grebennikova ◽  
Alina Gavrilova ◽  
Anatoly Tiulpakov ◽  
Natalia Tarbaeva ◽  
Galina Melnichenko ◽  
...  
Keyword(s):  
Case Report ◽  
Osteogenesis Imperfecta ◽  
Osteogenesis Imperfecta Type ◽  
Rare Mutation ◽  
Type V

scholarly journals Osteogenesis Imperfecta Type V: A Report of Two Filipino Families and Review of Literature

2015 ◽  
Vol 49 (4) ◽  
Author(s):  
Melissa Mae P. Baluyot ◽  
Barbra Charina V. Cavan ◽  
Maria Melanie Liberty B. Alcausin
Keyword(s):  
Osteogenesis Imperfecta ◽  
Osteogenesis Imperfecta Type ◽  
Review Of Literature ◽  
Type V

...

scholarly journals Clinical and Radiological Manifestations of Osteogenesis Imperfecta Type V

2006 ◽  
Vol 21 (4) ◽  
pp. 709 ◽  
Author(s):  
Dong Yeon Lee ◽  
Tae-Joon Cho ◽  
In Ho Choi ◽  
Chin Youb Chung ◽  
Won Joon Yoo ◽  
...  
Keyword(s):  
Osteogenesis Imperfecta ◽  
Osteogenesis Imperfecta Type ◽  
Type V

The effect of cyclical intravenous pamidronate in children and adolescents with osteogenesis imperfecta Type V

Bone ◽  
2006 ◽  
Vol 38 (1) ◽  
pp. 13-20 ◽  
Author(s):  
Leonid Zeitlin ◽  
Frank Rauch ◽  
Rose Travers ◽  
Craig Munns ◽  
Francis H. Glorieux
Keyword(s):  
Osteogenesis Imperfecta ◽  
Children And Adolescents ◽  
Osteogenesis Imperfecta Type ◽  
Intravenous Pamidronate ◽  
Type V

Osteogenesis imperfecta type V: Genetic and clinical findings in eleven Chinese patients

2016 ◽  
Vol 462 ◽  
pp. 201-209 ◽  
Author(s):  
Yi Liu ◽  
Jiawei Wang ◽  
Doudou Ma ◽  
Fang Lv ◽  
Xiaojie Xu ◽  
...  
Keyword(s):  
Osteogenesis Imperfecta ◽  
Clinical Findings ◽  
Chinese Patients ◽  
Osteogenesis Imperfecta Type ◽  
Type V
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