scholarly journals Jaw cyst-Basal cell nevus-Bifid rib syndrome: A case report

Author(s):  
S Rai ◽  
K Gauba
Keyword(s):  
Jaw Cyst ◽  
2011 ◽  
Vol 4 (1) ◽  
pp. 33-37
Author(s):  
Ruchi M. Anand ◽  
Sunil S. Mishra ◽  
Shirish S. Degwekar ◽  
Rahul R. Bhowate ◽  
Mukta B. Motwani ◽  
...  

2014 ◽  
Vol 5 (1) ◽  
pp. 39-41
Author(s):  
Shahanavaj Imam Husen Khaji ◽  
Gayathri H Kulkarni ◽  
Harish S Kulkarni ◽  
Suryakant B Metkari ◽  
Reshma Kulkarni

ABSTRACT Nevoid basal cell carcinoma syndrome is a syndrome with wide variety of manifestations ranging from oral lesions to skeletal deformities. It calls for due responsibility of maxillofacial surgeon to diagnose the syndrome because very often they are the first health professionals to see the patient for the treatment of keratocystic odontogenic tumor. Keratocystic odontogenic tumor (KCOT) has been the topic of numerous investigators and is known for its potentially aggressive behavior and significant rate of recurrences. Keratocystic odontogenic tumor often occurs as a solitary lesion, and in some instances multiple keratocysts may occur in association with a syndrome called Gorlin-Goltz syndrome (nevoid basal cell carcinoma, jaw cyst bifid rib basal cell nevus syndrome). Here, we present a case of multiple keratocysts in the mandible in association with skeletal, ocular and cutaneous anomalies in the given clinical scenario which has profound relevance in the clinical dental practice. How to cite this article Kulkarni GH, Khaji SI, Kulkarni HS, Metkari SB, Kulkarni R. Multiple Keratocysts of the Mandible in Association with Multiple Basal Epithelioma, Jaw Cysts and Bifid Rib Syndrome: A Rare Case Report. Int J Head Neck Surg 2014;5(1):39-41.


2019 ◽  
Vol 55 (04) ◽  
pp. 213-218
Author(s):  
Jayachandran Sadaksharam ◽  
Amutha Velappan Annapoorni

AbstractGorlin–Goltz syndrome, is an uncommon genetic condition characterized by the presence of multiple odontogenic keratocysts of jaws along with several other abnormal, cutaneous, ophthalmic, and osseous displays. This syndrome is also acknowledged by various names, such as nevoid basal cell carcinoma syndrome, jaw cyst, and bifid rib syndrome. This article illustrates about the clinical, radiological, and histological diagnostic findings and the multidisciplinary approach of treatment given to one such rare case of Gorlin–Goltz syndrome.


Hand Surgery ◽  
2002 ◽  
Vol 07 (02) ◽  
pp. 295-298 ◽  
Author(s):  
M. Galeano ◽  
M. Colonna ◽  
M. Lentini ◽  
F. Stagno D'Alcontres

Basal cell carcinoma (BCC) is the most common skin malignancy arising from cells of the basal layer of the epithelium or from the external root sheath of the hair follicle. BCC of the digit is a rare entity. The article presents one such case of bowenoid BCC of the thumb which required amputation at the MP joint.


2014 ◽  
Vol 117 (2) ◽  
pp. e141-e142
Author(s):  
BARBAHRA CAROLYNIE AMORIM REIS ◽  
DANIEL DO CARMO CARVALHO ◽  
DIMITRE RAMOS GRANDEZ ARAÚJO ◽  
IGOR BRASIL VILLAR ◽  
LUCIANO HENRIQUE DE JESUS ◽  
...  

2021 ◽  
Vol 86 ◽  
pp. 106318
Author(s):  
Nadeen Al Mushcab ◽  
Raja Husain ◽  
Mohammad Al Subaiei ◽  
Ayedh Al Qarni ◽  
Ahmed Abbas ◽  
...  

2018 ◽  
Vol 6 (11) ◽  
pp. 2213-2216
Author(s):  
Lerinza Van der Worm ◽  
Riyaadh Roberts ◽  
Thuraya Isaacs ◽  
Reginald M. Ngwanya

2018 ◽  
Vol 2018 ◽  
pp. 1-8
Author(s):  
P. Santander ◽  
E. M. C. Schwaibold ◽  
F. Bremmer ◽  
S. Batschkus ◽  
P. Kauffmann

Background. We report a case of multiple keratocysts first diagnosed in an 8-year-old boy. Case report. The incidental radiographic finding of a cystic lesion in an 8-year-old boy led to the surgical enucleation and further diagnosis of a keratocyst associated with a tooth crown. In the course of dental maturation from deciduous to permanent teeth, the boy presented new lesions, always associated with the crowns of teeth. Gorlin-Goltz (nevoid basal-cell carcinoma) syndrome was suspected, and the genetic analysis detected a previously undescribed germline variant in the PTCH1 gene. Treatment. This included a surgical removal of the cystic lesions, as well as the affected teeth. Follow-up. Due to the high recurrence rate of the keratocysts, frequent radiological checks were performed over a 5-year period.


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