scholarly journals Esophageal Atresia and Tracheoesophageal Fistula with Unilateral Pulmonary Agenesis - Hypoplasia

2013 ◽  
Vol 2 (2) ◽  
pp. 21
Author(s):  
Shraddha Verma ◽  
Jai Kumar Mahajan ◽  
Katragadda Laxmi Narsimha Rao
Keyword(s):  
Esophageal Atresia ◽  
Tracheoesophageal Fistula ◽  
Pulmonary Hypoplasia ◽  
Full Term ◽  
Lung Hypoplasia ◽  
Pulmonary Agenesis ◽  
Male Baby ◽  
Unilateral Pulmonary Agenesis

Association of unilateral severe pulmonary hypoplasia or agenesis and esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) is an exceedingly rare and highly lethal combination. We report a case of full term male baby who had EA with TEF and right lung hypoplasia, managed at our centre. He is alive and doing well at 10 years of age.

Unilateral pulmonary agenesis, esophageal atresia, and distal tracheoesophageal fistula

1995 ◽  
Vol 59 (2) ◽  
pp. 511-513 ◽  
Author(s):  
Kevin M. Steadland ◽  
Max R. Langham ◽  
Michael A. Greene ◽  
Charles E. Bagwell ◽  
David W. Kays ◽  
...  
Keyword(s):  
Esophageal Atresia ◽  
Tracheoesophageal Fistula ◽  
Pulmonary Agenesis ◽  
Unilateral Pulmonary Agenesis

Pulmonary agenesis with esophageal atresia and tracheoesophageal fistula

1987 ◽  
Vol 22 (2) ◽  
pp. 125-126 ◽  
Author(s):  
Kazue Takayanagi ◽  
Elizabieta Grochowska ◽  
Samier Abu-El Nas
Keyword(s):  
Esophageal Atresia ◽  
Tracheoesophageal Fistula ◽  
Pulmonary Agenesis

Tracheoesophageal Fistula, Esophageal Atresia, and Left Pulmonary Agenesis

1991 ◽  
Vol 11 (2) ◽  
pp. 228-229
Author(s):  
Jayanth K. Iyengar ◽  
Subramaniam Sivasankaran ◽  
Matthew F. Omojola
Keyword(s):  
Esophageal Atresia ◽  
Tracheoesophageal Fistula ◽  
Pulmonary Agenesis

Esophageal Atresia and Tracheoesophageal Fistula: Supportive Measures That Affect Survival

PEDIATRICS ◽  
1974 ◽  
Vol 54 (5) ◽  
pp. 558-564
Author(s):  
C. Everett Koop ◽  
Louise Schnaufer ◽  
A. Michael Broennle
Keyword(s):  
Survival Rate ◽  
Esophageal Atresia ◽  
Tracheoesophageal Fistula ◽  
Surgical Care ◽  
Full Term ◽  
Recent Experience ◽  
Term Infants ◽  
Technical Problems ◽  
Surgical Technical ◽  
Esophageal Pouch

The survival of infants with esophageal atresia with or without tracheoesophageal fistula has been analyzed over a 24-year period divided into three eras of five years each depending upon the quality of intensive care available and the most recent nine years' experience. Early diagnosis and skillful transportation to definitive surgical care are essential. Diagnosis by x-ray with a coiled catheter in the upper esophageal pouch without the use of radiopaque material is beneficially reflected in a decreased incidence of pneumonia and a reduced mortality. The skills of anesthesia carried over into close supervision of respiratory care postoperatively have further increased the salvage rate of these infants. As surgical technical problems have been overcome, the percentage of deaths due to associated major anomalies and pneumonia and/or sepsis has increased. Invasive techniques for diagnosis, for monitoring, and for treatment do not seem to be responsible for the sepsis. In the most recent experience with 134 patients over nine years the overall survival was 66%; full-term infants had a 70% survival while the survival rate for prematures was 52%. In full-term infants without pneumonia and without a major associated congenital anomaly, the survival rate was 100% (44 patients). Clearly the target for improvement in survival is the prevention of and the improvement in treatment of pneumonia and sepsis.

scholarly journals Dextrocardia with pulmonary hypoplasia: an unusual cause of unilateral lung white-out

2019 ◽  
Vol 12 (5) ◽  
pp. e229413
Author(s):  
Sagnik Biswas ◽  
Animesh Ray
Keyword(s):  
Situs Inversus ◽  
Developmental Disorder ◽  
Pulmonary Hypoplasia ◽  
Respiratory Infections ◽  
Bronchial Tree ◽  
Lung Hypoplasia ◽  
Pulmonary Agenesis ◽  
Type Iii ◽  
Pulmonary Parenchyma ◽  
Lung Agenesis

Pulmonary agenesis is a rare developmental disorder with many syndromic associations. Type III agenesis presents with variable amounts of bronchial tree, pulmonary parenchyma and supporting vasculature. It is also reported to be associated with dextrocardia due to shifting of the heart to occupy the space left by the underdeveloped lung, which occurs as early as the fourth week of gestation. Right lung agenesis is considered rarer than its left-sided counterpart and also has a poorer prognosis due to increased chances of respiratory infections. We report a case of isolated right-sided lung hypoplasia with dextrocardia without situs inversus or heterotaxy.

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