scholarly journals Left pulmonary artery agenesis

2010 ◽  
Vol 93 (3) ◽  
pp. 158
Author(s):  
B J Van Kelckhoven ◽  
A.P.G Van Gils
2013 ◽  
Vol 12 (4) ◽  
pp. 462-466
Author(s):  
A Santra ◽  
R Padhi ◽  
P Dutta ◽  
R Manjhi ◽  
S Pothal ◽  
...  

Proximal interruption of the unilateral pulmonary artery is a rare congenital anomaly, which is often associated with other cardiovascular abnormalities. It is usually diagnosed in children but rarely discovered in adulthood as an isolated phenomenon, occurring more frequently on the right side and is often associated with a contralateral aortic arch. We are presenting a rare case of a sixty year old male who was diagnosed with left lung hypoplasia due to proximal interruption of left pulmonary artery with left sided aortic arch without any associated cardiovascular anomalies. DOI: http://dx.doi.org/10.3329/bjms.v12i4.13689 Bangladesh Journal of Medical Science Vol. 12 No. 04 October ’13 Page 462-466


2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
Cenk Aypak ◽  
Hülya Yıkılkan ◽  
Zekai Uysal ◽  
Süleyman Görpelioğlu

Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. UAPA is usually associated with cardiac anomalies and surgically treated in childhood. We report a rare case of a 50-year-old woman who was diagnosed with left pulmonary artery agenesis without any other cardiac anomalies. Clinicians should be aware of the possibility of undiagnosed cases of UAPA in patients through a chest radiograph that suggests the diagnosis. Confirmation of the diagnosis and anatomic details can be discerned by CT scanning.


2016 ◽  
Vol 1 (1) ◽  
pp. 88-91
Author(s):  
Cristina Blesneac ◽  
Carmen Corina Şuteu ◽  
Marian Pop ◽  
Rodica Togănel

Abstract Unilateral pulmonary artery agenesis is a rare congenital anomaly, that may develop in isolation, or in association with other congenital cardiovascular anomalies, such as tetralogy of Fallot, septal defects, right-sided aortic arch, or pulmonary atresia. Left-sided pulmonary artery agenesis is less frequent than the right-sided one. Diagnosis of unilateral pulmonary artery agenesis can be difficult. We report the case of a 15 year-old boy who presented with reduced exercise tolerance, shortness of breath and cyanosis. He was diagnosed with left pulmonary artery agenesis, associated with subaortic-ventricular septal defect, right-sided aortic arch, and severe pulmonary arterial hypertension (PAH), that precluded the surgical repair. Pulmonary vasodilator therapy was initiated in this case. The mortality rate of this rare anomaly is high due to its complications. It is essential to establish an early and correct diagnosis, in order to provide adequate treatment and prevent complications in this disease.


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