scholarly journals Osteopathic correction in case of coarctation of the aorta and stenosis of the pulmonary artery in a patient with Williams syndrome

2021 ◽  
Vol 83 (3) ◽  
pp. 73-84
Author(s):  
Dmitriy Efimov ◽  
Svyatoslav Novoseltsev
Keyword(s):  
Pulmonary Artery ◽  
Williams Syndrome ◽  
Coarctation Of The Aorta ◽  
Vascular Pathology ◽  
Central Hemodynamics

The research was done for studying capabilities of osteopathic correction of vascular pathology in a patient (a child) with Williams syndrome. The change of the central hemodynamics parameters during the 5-year period was demonstrated. The change data was registered by echocardiography. The obtained result makes it possible to recommend the osteopathic correction methods as safe and eff ective ones for the treatment of patients with similar pathology.

Absence of the fetal right pulmonary artery complicated with coarctation of the aorta: Prenatal and postnatal diagnosis

2019 ◽  
Vol 36 (9) ◽  
pp. 1787-1789
Author(s):  
Yu Wang ◽  
Jiaqi Zhang ◽  
Wei Feng ◽  
You Wu ◽  
Li Yang ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Coarctation Of The Aorta ◽  
Postnatal Diagnosis ◽  
Right Pulmonary Artery

MRI detection of occult venous anomalies in a patient with Williams syndrome: a case report

2020 ◽  
Vol 30 (4) ◽  
pp. 568-570 ◽  
Author(s):  
Thomas S. Davis ◽  
Monica S. Epelman ◽  
Peace C. Madueme ◽  
Karen S. Bender ◽  
Gul H. Dadlani
Keyword(s):  
Case Report ◽  
Aortic Stenosis ◽  
Pulmonary Artery ◽  
Williams Syndrome ◽  
Artery Stenosis ◽  
Congenital Disorder ◽  
Pulmonary Artery Stenosis ◽  
Supravalvar Aortic Stenosis ◽  
Venous Ectasia ◽  
Arterial Stenoses

AbstractWilliams syndrome is a multisystem, congenital disorder which is commonly associated with arterial stenoses: supravalvar aortic stenosis and peripheral pulmonary artery stenosis. Venous abnormalities have not been previously reported in children with Williams syndrome. We present a case of a 3-year-old girl with Williams syndrome and diffuse venous ectasia as detected by MRI.

Spontaneous pulmonary artery aneurysm in a case of Williams syndrome

2020 ◽  
Vol 14 (6) ◽  
pp. e170-e171
Author(s):  
Vineeta Ojha ◽  
Niraj Nirmal Pandey ◽  
Mansi Verma ◽  
Avichala Taxak ◽  
Sanjeev Kumar ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Williams Syndrome ◽  
Artery Aneurysm ◽  
Pulmonary Artery Aneurysm

Anomalous origin of left coronary artery from right pulmonary artery in an infant with coarctation of the aorta

2004 ◽  
Vol 78 (1) ◽  
pp. 324-326 ◽  
Author(s):  
Anil Sivadasan Radha ◽  
Baiju Sasi Dharan ◽  
Raman Krishna Kumar ◽  
Suresh Gururaja Rao
Keyword(s):  
Coronary Artery ◽  
Pulmonary Artery ◽  
Left Coronary Artery ◽  
Coarctation Of The Aorta ◽  
Anomalous Origin ◽  
Right Pulmonary Artery

Chronic effects of pulmonary artery stenosis on hemodynamic and structural development of the lungs

2013 ◽  
Vol 304 (1) ◽  
pp. L17-L28 ◽  
Author(s):  
Hedi Razavi ◽  
Sarah E. Stewart ◽  
Chengpei Xu ◽  
Hirofumi Sawada ◽  
Shahrzad Y. Zarafshar ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Lung Volume ◽  
Left Lung ◽  
Vascular Pathology ◽  
Pulmonary Artery Stenosis ◽  
Sham Operation ◽  
Structural Development ◽  
Sprague Dawley ◽  
Bronchial Arteries ◽  
Chronic Effects

Pulmonary artery (PA) stenosis is a difficult obstructive defect to manage since clinicians cannot know a priori which obstructions to treat and when. Prognosis of PA stenosis and its chronic effects on lung development are poorly understood. This study aimed to characterize the hemodynamic and structural effects of PA stenosis during development. Fourteen male Sprague-Dawley rats underwent left PA (LPA) banding at age 21 days, and 13 underwent sham operation. Hemodynamic and structural impacts were studied longitudinally at 20, 36, 52, 100, and 160 days. Chronic LPA banding resulted in a significant reduction in LPA flow ( P < 0.0001) and size of both proximal LPA ( P < 0.0001) and distal LPA ( P < 0.01), as well as a significant increase in flow and size of the right PA ( P < 0.05) throughout development. Flows and sizes adapted such that normal levels of wall shear were restored after banding. At 160 days, LPA banding resulted in a significant decrease in left lung volume and an increase in right lung volume but no significant differences in total lung volume. There was an elevation of proximal LPA pressure as well as right ventricular hypertrophy in the banded animals. The banded lung exhibited arterial disorganization, loss of vessels, and enlargement of its bronchial arteries, whereas the contralateral lung showed signs of vascular pathology. There are consequences on development of both lungs in the presence of an LPA stenosis at young age. These results suggest that early intervention may be necessary to optimize left lung growth and minimize right lung vascular pathology.

Recurrent coarctation in Williams syndrome: novel approach of drug-eluting stent implantation

2020 ◽  
Vol 30 (2) ◽  
pp. 294-297
Author(s):  
Aphrodite Tzifa ◽  
Konstantinos S. Mylonas ◽  
Antonios Halapas
Keyword(s):  
Pulmonary Artery ◽  
Williams Syndrome ◽  
Stent Implantation ◽  
Aortic Coarctation ◽  
Vascular Wall ◽  
Drug Eluting Stent ◽  
Novel Approach ◽  
Drug Eluting ◽  
Multiple Recurrences

AbstractPatients with Williams syndrome often present with abnormalities of the vascular wall of the aorta and/or the pulmonary artery. Surgery may result in restenosis of the affected vessel. Herein, we report a case of an infant with multiple recurrences of aortic coarctation successfully treated with Zotarolimus drug-eluting stent.

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