scholarly journals Successful Surgery for Scoliosis Supported by Pulmonary Rehabilitation in a Duchenne Muscular Dystrophy Patient With Forced Vital Capacity Below 10%

2013 ◽  
Vol 37 (6) ◽  
pp. 875 ◽  
Author(s):  
Jang Woo Lee ◽  
Yu Hui Won ◽  
Won Ah Choi ◽  
Soon Kyu Lee ◽  
Seong Woong Kang
Keyword(s):  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Forced Vital Capacity ◽  
Pulmonary Rehabilitation ◽  
Vital Capacity ◽  
Duchenne Muscular Dystrophy Patient

Performance of the Upper Limb Module—A Reliable and Valid Evaluation for Chinese Patients with Duchenne Muscular Dystrophy

2020 ◽  
Author(s):  
Yuen Yee Alice Chiu ◽  
Chun Wai Lo ◽  
Chi Kuk Connie Hui ◽  
Wai Chong Susanna Choi ◽  
So Lun Lee ◽  
...  
Keyword(s):  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Upper Limb ◽  
Forced Vital Capacity ◽  
Motor Performance ◽  
Vital Capacity ◽  
High Reliability ◽  
Reliability And Validity ◽  
Chinese Patients ◽  
Rater Reliability

Abstract Background Duchenne muscular dystrophy is a genetic disease leading to progressive muscle weakness and degeneration. Effective assessment tool is needed to allow monitoring of progress to guide the management. This study assessed the reliability and validity of the Performance of Upper Limb (PUL) Module when used in patients with Duchenne Muscular Dystrophy (DMD). MethodsTotal thirty-three Chinese DMD patients were included. Twenty-five video-recorded PUL Module version 1.3 assessments were performed for the recruited patients with three raters evaluated the same recorded video for inter-rater reliability and evaluated the same performance one month later for intra-rater reliability. Construct validity was assessed correlating the PUL Module scores with the patients’ age, their forced vital capacity (N=25) and their Hammersmith motor scale scores (N=25) performed on the same day. ResultsThe intra-rater and inter-rater reliability (ICC 0.92 - 0.99), internal consistency (Cronbach’s alpha 0.97 - 0.99) and known groups validity (AUC 0.97) of PUL module were excellent. PUL was negatively correlated with age (r = -0.912), and positively correlated with the forced vital capacity (r = 0.87) and the Hammersmith motor scale (r = 0.84). The findings confirm the high reliability and validity of PUL module, and its high clinical relevancy in monitoring the deteriorating upper limb motor performance that strongly correlated with the lung function and generalized motor performance as age increased in DMD. ConclusionThis first study of PUL module in Chinese patients with DMD confirmed that it is a reliable valid tool to monitor clinical progress and outcome for DMD.

A longitudinal study of forced vital capacity in Duchenne muscular dystrophy

1997 ◽  
Vol 7 (6-7) ◽  
pp. 435
Author(s):  
M.F. Phillips ◽  
R. Quinlivan ◽  
R.H.T. Edwards ◽  
P.M.A. Calverley
Keyword(s):  
Longitudinal Study ◽  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Forced Vital Capacity ◽  
Vital Capacity

Tracheoinnominate fistula in a Duchenne muscular dystrophy patient: Successful management with an endovascular stent

2005 ◽  
Vol 15 (8) ◽  
pp. 569-571 ◽  
Author(s):  
Andrea Vianello ◽  
Roberto Ragazzi ◽  
Loris Mirri ◽  
Giovanna Arcaro ◽  
Cesare Cutrone ◽  
...  
Keyword(s):  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Duchenne Muscular Dystrophy Patient ◽  
Endovascular Stent ◽  
Successful Management

scholarly journals Successful surgery for a neuromuscular scoliosis patient by pulmonary rehabilitation with forced vital capacity below 30%

2018 ◽  
Vol 27 (9) ◽  
pp. 2072-2075 ◽  
Author(s):  
Kai Han ◽  
Yongqian Wang ◽  
Shangbin Cui ◽  
Caixia Xu ◽  
Peiqiang Su
Keyword(s):  
Forced Vital Capacity ◽  
Pulmonary Rehabilitation ◽  
Vital Capacity ◽  
Neuromuscular Scoliosis ◽  
Scoliosis Patient

Postural vital capacity difference with aging in duchenne muscular dystrophy

2015 ◽  
Vol 52 (5) ◽  
pp. 722-727 ◽  
Author(s):  
Yu Hui Won ◽  
Won Ah Choi ◽  
Dong Hyun Kim ◽  
Seong-Woong Kang
Keyword(s):  
Duchenne Muscular Dystrophy ◽  
Muscular Dystrophy ◽  
Vital Capacity
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