scholarly journals A case of neuromyelitis optica spectrum disorder associated with a limited cutaneous systemic sclerosis and Sjögren syndrome

2013 ◽  
Vol 53 (9) ◽  
pp. 695-700 ◽  
Author(s):  
Yasutaka Iwanaga ◽  
Shintaro Hayashi ◽  
Nobutoshi Kawamura ◽  
Yasumasa Ohyagi ◽  
Jun-ichi Kira
Keyword(s):  
Systemic Sclerosis ◽  
Neuromyelitis Optica ◽  
Sjögren Syndrome ◽  
Spectrum Disorder ◽  
Sjogren Syndrome ◽  
Neuromyelitis Optica Spectrum Disorder

scholarly journals Recurrent optic neuritis in a patient with Sjogren syndrome and neuromyelitis optica spectrum disorder

Medicine ◽  
2020 ◽  
Vol 99 (45) ◽  
pp. e23029
Author(s):  
Wei Zheng ◽  
Xiaoping Liu ◽  
Xiujuan Hou ◽  
Yuelan Zhu ◽  
Taotao Zhang ◽  
...  
Keyword(s):  
Optic Neuritis ◽  
Neuromyelitis Optica ◽  
Sjögren Syndrome ◽  
Spectrum Disorder ◽  
Sjogren Syndrome ◽  
Neuromyelitis Optica Spectrum Disorder

Neuromyelitis optica spectrum disorder complicated with Sjogren syndrome successfully treated with tocilizumab: A case report

2013 ◽  
Vol 26 (2) ◽  
pp. 294-296 ◽  
Author(s):  
Toshihiko Komai ◽  
Hirofumi Shoda ◽  
Kenichi Yamaguchi ◽  
Keiichi Sakurai ◽  
Mihoko Shibuya ◽  
...  
Keyword(s):  
Case Report ◽  
Neuromyelitis Optica ◽  
Sjögren Syndrome ◽  
Spectrum Disorder ◽  
Sjogren Syndrome ◽  
Neuromyelitis Optica Spectrum Disorder

scholarly journals A case of pathology-proven neuromyelitis optica spectrum disorder with Sjögren syndrome manifesting aphasia and apraxia due to a localized cerebral white matter lesion

2014 ◽  
Vol 20 (10) ◽  
pp. 1413-1416 ◽  
Author(s):  
Jun Sawada ◽  
Ryosuke Orimoto ◽  
Tatsuro Misu ◽  
Takayuki Katayama ◽  
Hitoshi Aizawa ◽  
...  
Keyword(s):  
White Matter ◽  
Neuromyelitis Optica ◽  
White Matter Lesion ◽  
Sjögren Syndrome ◽  
Spectrum Disorder ◽  
Cerebral White Matter ◽  
Sjogren Syndrome ◽  
Neuromyelitis Optica Spectrum Disorder ◽  
Aqp4 Antibody ◽  
Cerebral White Matter Lesion

A woman with Sjögren syndrome manifesting as aphasia with a left deep cerebral white matter lesion tested positive for anti-aquaporin 4 (AQP4) antibody. Open biopsy of the lesion revealed active demyelination with edematous changes and the preservation of most axons, indicating a non-necrotic demyelinating lesion. Immunostaining for AQP4 was diffusely lost, whereas the loss of glial fibrillary acidic protein immunostaining was limited but with highly degenerated astrocytic foot processes in perivascular areas. These results suggested neuromyelitis optica spectrum disorder (NMOSD) pathology rather than Sjögren-related vasculitis. Only cerebral cortical symptoms with a cerebral white matter lesion could be observed in NMOSDs.

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