Pulmonary Hypertension in the CREST Syndrome Variant of Progressive Systemic Sclerosis (Scleroderma)

1977 ◽  
Vol 86 (4) ◽  
pp. 394 ◽  
Author(s):  
ROSEMARIE SALERNI
Keyword(s):  
Pulmonary Hypertension ◽  
Systemic Sclerosis ◽  
Progressive Systemic Sclerosis ◽  
Crest Syndrome

Myocardial function and perfusion in the CREST syndrome variant of progressive systemic sclerosis

1984 ◽  
Vol 77 (3) ◽  
pp. 489-496 ◽  
Author(s):  
William P. Follansbee ◽  
Edward I. Curtiss ◽  
Thomas A. Medsger ◽  
Gregory R. Owens ◽  
Virginia D. Steen ◽  
...  
Keyword(s):  
Systemic Sclerosis ◽  
Myocardial Function ◽  
Progressive Systemic Sclerosis ◽  
Crest Syndrome

scholarly journals Juvenile Onset Systemic Sclerosis

1984 ◽  
Vol 77 (9) ◽  
pp. 793-794 ◽  
Author(s):  
S M Burge ◽  
T J Ryan ◽  
R P R Dawber
Keyword(s):  
Systemic Sclerosis ◽  
Progressive Systemic Sclerosis ◽  
Crest Syndrome ◽  
Juvenile Onset ◽  
Anticentromere Antibody

A case of progressive systemic sclerosis (CREST syndrome), which began in childhood, is described. Juvenile onset CREST syndrome is extremely rare; there are few well documented cases and no published series of children with this form of progressive systemic sclerosis. An anticentromere antibody was recently detected in this case and its significance is discussed.

The role of vasodilators in patients with progressive systemic sclerosis. Interstitial lung disease and pulmonary hypertension

CHEST Journal ◽  
1985 ◽  
Vol 88 (4) ◽  
pp. 263S-265 ◽  
Author(s):  
J. Ohar ◽  
C. Polatty ◽  
A. Robichaud ◽  
A. Fowler ◽  
G. Vetrovec ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Systemic Sclerosis ◽  
Interstitial Lung Disease ◽  
Lung Disease ◽  
Progressive Systemic Sclerosis

scholarly journals Uncommon skeletal findings in systemic sclerosis (scleroderma)

2002 ◽  
Vol 6 (1) ◽  
pp. 28-32
Author(s):  
Betsie Van der Walt ◽  
Irma Van de Werke ◽  
Zarina Lockhat
Keyword(s):  
Systemic Sclerosis ◽  
Pulmonary Fibrosis ◽  
Progressive Systemic Sclerosis ◽  
Small Vessel ◽  
Crest Syndrome ◽  
Radiological Features ◽  
Interstitial Pulmonary Fibrosis ◽  
Diffuse Disease ◽  
Diffuse Scleroderma ◽  
Skeletal Findings

Scleroderma or progressive systemic sclerosis is a diffuse disease characterised by excessive deposition of collagen and small-vessel arteritis. Systemic sclerosis is divided into two groups.1. Diffuse scleroderma, where interstitial pulmonary fibrosis is common,  and2. The CREST syndrome, which is characterised more commonly by vasculitis with pulmonary hypertension.The CREST syndrome consists of calcinosis of the skin, Raynaud's phenomenon, sclerodactyly, telangiectasis and oesophageal dysmotility.This case describes a 48-year-old woman with known scleroderma demonstrating some of the less common radiological features.

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