A rare cause of AA amyloidosis and end-stage kidney failure: Questions

2018 ◽  
Vol 34 (9) ◽  
pp. 1533-1535
Author(s):  
Mehmet Taşdemir ◽  
Sezen Yılmaz ◽  
Zeliha Füsun Baba ◽  
Ilmay Bilge
Keyword(s):  
Kidney Failure ◽  
Aa Amyloidosis ◽  
End Stage

scholarly journals Comments on Tașdemir et al.: A rare cause of AA amyloidosis and end-stage kidney failure

2019 ◽  
Vol 34 (9) ◽  
pp. 1635-1635
Author(s):  
Joris Galland ◽  
Léa Savey
Keyword(s):  
Kidney Failure ◽  
Aa Amyloidosis ◽  
End Stage

Comments on the letter of Galland et al. on “A rare cause of AA amyloidosis and end-stage kidney failure”

2019 ◽  
Vol 34 (9) ◽  
pp. 1633-1634
Author(s):  
Mehmet Taşdemir ◽  
Sezen Yılmaz ◽  
Zeliha Füsun Baba ◽  
Ilmay Bilge
Keyword(s):  
Kidney Failure ◽  
Aa Amyloidosis ◽  
End Stage

A rare cause of AA amyloidosis and end-stage kidney failure: Answers

2018 ◽  
Vol 34 (9) ◽  
pp. 1537-1539
Author(s):  
Mehmet Taşdemir ◽  
Sezen Yılmaz ◽  
Zeliha Füsun Baba ◽  
Ilmay Bilge
Keyword(s):  
Kidney Failure ◽  
Aa Amyloidosis ◽  
End Stage

scholarly journals MO961KIDNEY TRANSPLANTATION AS A TREATMENT OF CHOICE FOR AA AMYLOIDOSIS DUE TO PERIODIC FEVER SYNDROME

2021 ◽  
Vol 36 (Supplement_1) ◽  
Author(s):  
Ivana Dedinska ◽  
Karol Graňák ◽  
Matej Vnučák
Keyword(s):  
Early Childhood ◽  
Kidney Transplantation ◽  
Clinical Course ◽  
Periodic Fever ◽  
Periodic Fever Syndrome ◽  
Aa Amyloidosis ◽  
Periodic Fever Syndromes ◽  
Post Transplant ◽  
Fever Syndromes ◽  
End Stage

Abstract Background and Aims Renal AA amyloidosis is the most serious complication of periodic fever syndrome, which, inadequate suppression, due to persistent inflammation, leads to nephrotic syndrome and renal failure over several years. In most cases, periodic fever syndromes begin to manifest clinically in early childhood. Occurrence in adulthood is considered rare and is associated with a poorer clinical course. Kidney transplantation is an effective and safe treatment for end-stage chronic kidney disease (CKD) based on AA amyloidosis. Method We present cases of two patients after deceased donor kidney transplantation, who have been diagnosed with adult periodic fever syndrome. Conclusion Periodic fever syndromes are diseases beginning to manifest clinically in early childhood in 60–90% of cases, most often in the case of familial Mediterranean fever around 4 years of age, in the case of CAPS usually only a few months after birth. Occurrence in adulthood is considered rare and is associated with a poorer clinical course. Kidney transplantation is an effective and safe treatment of end-stage CKD based on AA amyloidosis associated with periodic fever syndrome. Adequate targeted treatment against IL-1 or TNF is important and appears to be safe during the post-transplant period, with regular monitoring of renal function, acute phase inflammatory reactants, and histological findings by protocol graft biopsies. It will be important and necessary to assess the development of diseases in the post-transplant period in the long term.

scholarly journals POJOK BACA (BALANCE CAIRAN) UNTUK SURVIVOR HEMODIALISIS

2018 ◽  
Vol 2 (2) ◽  
pp. 138
Author(s):  
Eska Dwi Prajayanti
Keyword(s):  
Kidney Failure ◽  
Fluid Intake ◽  
Fluid Overload ◽  
Hemodialysis Patients ◽  
Fluid Restriction ◽  
End Stage Renal Failure ◽  
Severity Of The Disease ◽  
The Right ◽  
End Stage

Background: Management of end-stage renal failure patients one of the treatments is hemodialysis. Complications that arise with respect to fluid overload in patients with kidney failure can be prevented through effective and efficient fluid intake restrictions. Efforts to create restrictions on fluid intake in patients with kidney failure can be done through monitoring fluid intake per day. Fluid restriction program in patients in order to prevent complications and maintain quality of life, it is necessary to analyze practices related to intervention in controlling the amount of fluid intake through recording the amount of fluid taken and urine released every day. Pojok Balance Cairan (BACA) is one way to help hemodialysis patients learn how to calculate fluid needs in their body and help determine dietary settings for hemodialysis patients where in the reading corner will be explained related to how to calculate fluid balance and how the right diet in patients hemodialysis according to the severity of the disease. Method of implementation: lectures and demonstrations. Conclusion: POJOK BACA can prolong the life of patients undergoing hemodialysis because it can reduce the risk of complications that arise such as shortness of breath.Keywords: Hemodialysis, Liquid, Pojok Baca

scholarly journals Use of the Kidney Failure Risk Equation to Determine the Risk of Progression to End-stage Renal Disease in Children With Chronic Kidney Disease

2018 ◽  
Vol 172 (2) ◽  
pp. 174 ◽  
Author(s):  
Erica Winnicki ◽  
Charles E. McCulloch ◽  
Mark M. Mitsnefes ◽  
Susan L. Furth ◽  
Bradley A. Warady ◽  
...  
Keyword(s):  
Chronic Kidney Disease ◽  
Kidney Disease ◽  
Renal Disease ◽  
Kidney Failure ◽  
End Stage Renal Disease ◽  
Risk Equation ◽  
Failure Risk ◽  
Risk Of Progression ◽  
Stage Renal Disease ◽  
End Stage

scholarly journals Bioimpedance-defined overhydration predicts survival in end stage kidney failure (ESKF): systematic review and subgroup meta-analysis

2018 ◽  
Vol 8 (1) ◽  
Author(s):  
Matthew Tabinor ◽  
Emma Elphick ◽  
Michael Dudson ◽  
Chun Shing Kwok ◽  
Mark Lambie ◽  
...  
Keyword(s):  
Systematic Review ◽  
Kidney Failure ◽  
Meta Analysis ◽  
End Stage

scholarly journals Adult Nesidioblastosis in Chronic Kidney Disease

2019 ◽  
Vol 2019 ◽  
pp. 1-6
Author(s):  
Eduardo Lozano-Melendez ◽  
Mercedes Aguilar-Soto ◽  
Luis Eugenio Graniel-Palafox ◽  
Laura Elena Ceceña-Martínez ◽  
Rafael Valdez-Ortiz ◽  
...  
Keyword(s):  
Chronic Kidney Disease ◽  
Renal Function ◽  
Case Report ◽  
Kidney Disease ◽  
Kidney Failure ◽  
Hyperinsulinemic Hypoglycemia ◽  
Histopathological Diagnosis ◽  
Insulin Levels ◽  
First Case ◽  
End Stage

Context. Nesidioblastosis is a rare cause of hyperinsulinemic hypoglycemia in adults. The diagnosis is further complicated in patients with kidney failure, since impaired renal function can cause hypoglycemia by itself and diagnostic criteria for this clinical scenario have not been developed yet. Case Description. We present the case report of a 36-year-old patient with end stage chronic kidney disease who presented to the emergency department because of hypoglycemia. However, the patient’s hypoglycemia did not respond well to medical treatment; the diagnosis of hyperinsulinemic hypoglycemia was made due to the presence of inappropriately high levels of insulin, proinsulin, and C-peptide during an episode of hypoglycemia. Imaging studies were performed without any conclusive findings; so selective intra-arterial pancreatic stimulation with hepatic venous sampling (SACTS) was done. Based on the results of this study the patient was referred for subtotal pancreatectomy. Classic criteria for the diagnosis of insulinoma with SACTS required a 2-fold increase in insulin levels but newer criteria suggest thresholds that are useful in the differential diagnosis of insulinoma and nesidioblastosis. In our patient, the former criteria were positive; however, the new criteria were not compatible with insulinoma but with nesidioblastosis, which was the final histopathological diagnosis. Conclusion. This seems to be the first case report of a patient with end stage chronic kidney disease and nesidioblastosis, as well as the first case of hyperinsulinemic hypoglycemia in the context of kidney failure diagnosed by SACTS. We consider this method to be very useful in patients with renal impairment because peripancreatic insulin levels do not depend on the renal function.

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