Ureteropelvic junction obstruction and calyceal diverticulum in a child with Turner syndrome and horseshoe kidney

2010 ◽  
Vol 6 (5) ◽  
pp. 463.e1-463.e4 ◽  
Author(s):  
Florian Obermayr ◽  
Philipp Szavay ◽  
Jürgen Schäfer ◽  
Jörg Fuchs
Keyword(s):  
Turner Syndrome ◽  
Ureteropelvic Junction Obstruction ◽  
Horseshoe Kidney ◽  
Ureteropelvic Junction ◽  
Calyceal Diverticulum

Percutaneous Endopyelotomy for Ureteropelvic Junction Obstruction in a Horseshoe Kidney

1996 ◽  
Vol 30 (2) ◽  
pp. 145-147 ◽  
Author(s):  
Yasuhiro Koikawa ◽  
Seiji Naito ◽  
Jiro Uozumi ◽  
Tetsuji Uemura ◽  
Ken Goto ◽  
...  
Keyword(s):  
Ureteropelvic Junction Obstruction ◽  
Horseshoe Kidney ◽  
Ureteropelvic Junction

Renal Malformations in Patients With Turner Syndrome: Imaging in 141 Patients

PEDIATRICS ◽  
1988 ◽  
Vol 82 (6) ◽  
pp. 852-856
Author(s):  
Barbara Lippe ◽  
Mitchell E. Geffner ◽  
Rosalind B. Dietrich ◽  
M. Ines Boechat ◽  
Hooshang Kangarloo
Keyword(s):  
Turner Syndrome ◽  
Ureteropelvic Junction Obstruction ◽  
Imaging Technique ◽  
Imaging Study ◽  
Horseshoe Kidney ◽  
Initial Screening ◽  
Renal Malformations ◽  
Initial Imaging ◽  
Routine Imaging ◽  
Crossed Ectopia

Turner syndrome occurs in 1/2,000 to 1/5,000 live female births. The presence of renal malformations was evaluated in 141 patients with Turner syndrome and abnormalities were found in 47 (33%). Prior to 1980, IVP was the radiologic method used for initial screening, and subsequently, ultrasonography has been used as the initial imaging technique. With both methods, major malformations can be detected. Ten patients had a horseshoe kidney, 11 had double collecting systems, four had complete absence of one kidney, three had crossed ectopia, and one had a pelvic kidney. Three patients had ureteropelvic junction obstruction; two of these were asymptomatic and the obstructions were detected only because of the routine imaging. Two patients had ureterovesicular junction obstruction, with one studied as part of a routine evaluation for short stature. Four of these five patients required surgery. Ultrasonography should be used as the initial renal imaging study for all patients at the time the diagnosis of Turner syndrome is made.

scholarly journals Evaluation of the Patients with Antenatal Hydronephrosis Diagnosed Ureteropelvic Junction Obstruction with the Hydronephrosis Severity Score

2021 ◽  
Author(s):  
Gökçen Erfidan ◽  
Eren Soyaltın ◽  
Tunç Özdemir ◽  
Secil Arslansoyu Çamlar ◽  
Demet Alaygut ◽  
...  
Keyword(s):  
Clinical Outcomes ◽  
Severity Score ◽  
Ureteropelvic Junction Obstruction ◽  
Surgical Intervention ◽  
Outlet Obstruction ◽  
Case Series ◽  
Horseshoe Kidney ◽  
Ureteropelvic Junction ◽  
Ureterovesical Junction ◽  
Antenatal Hydronephrosis

Objective: Ureteropelvic junction obstruction is the main cause of obstructive antenatal hydronephrosis. Although surgery is the traditional treatment modality, there is still no consensus on surgical indications. We aimed to analyse the patients referred as antenatal hydronephrosis and diagnosed with ureteropelvic junction obstruction with Hydronehprosis Severity Score that has been developed by Babu at al. Method: The patients who were admitted with antenatal hydronephrosis in 2013-2018 and diagnosed as ureteropelvic junction obstruction and followed up in our clinic for at least one year were evaluated. The cases with unilateral hydronephrosis were included. Those with vesicoureteral reflux, horseshoe kidney, hydroureter, ureterovesical junction obstruction were excluded. Renal ultrasonography and nuclear scintigraphy results were re-evaluated. They were grouped as mild (0-4), moderate (5-8) and severe (9-12) based on scoring of three parameters; differantial renal function, drainage curve pattern and US grade. Clinical outcomes were also classified in three groups; resolution (grade 1-no hydronephrosis), persistance (grade 2-3 hydronephrosis) and surgical intervention. The relation between the scores and clinical outcomes were analysed. Results: A total of 57 patients were evaluated. 2 with horseshoe kidney, 4 with vesicoureteralreflux, 7 with bilateral hydronephrosis, 4 with ureteric outlet obstruction, 12 with incomplete records were excluded. Finally, 28 patients were included. Hydronephrosis was resolved in 4 (14.2%), persisted in 5 (17.8%) and surgical intervention was required in 19 (67.8%) patients. 1/5 patients with mild, 15/20 patients with moderate and 3/3 patients with severe HSS underwent surgery. 77.2% of the patients with a total score of ≥6 initially required surgical intervention at their follow-up. Conclusion: HSS may provide a significant predictive value for surgical intervention for the patients classified as “mild” or “severe” at the initial evaluation. In the “moderate” group, the risk increases in the patients with HSS≥6. Existing data should be evaluated with larger case series.

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