Double orifice mitral valve associated with subaortic stenosis—echocardiographic and anatomic findings

1994 ◽  
Vol 4 (2) ◽  
pp. 168-171
Author(s):  
Thomas B. Johnson ◽  
Derek A. Fyfe ◽  
Stephen J. Swanger
Keyword(s):  
Mitral Valve ◽  
Congenital Heart ◽  
Surgical Repair ◽  
Subaortic Stenosis ◽  
Complex Congenital Heart Disease ◽  
Surgical Results ◽  
Intraoperative Transesophageal Echocardiography ◽  
Hemodynamic Function ◽  
Subaortic Obstruction ◽  
Double Orifice

SummaryWe describe an infant with complex congenital heart disease, including double orifice of the mitral valve associated with complex subaortic stenosis. Transthoracic and intraoperative transesophageal echocardiography were used to define three distinct anatomic abnormalities, all potentially contributing to the subaortic obstruction. Stepwise surgical repair with transesophageal echocardiographic monitoring of hemodynamic function ensured optimal initial surgical results. Overwhelming postoperative complications ensued, however, and the patient died. Postmortem findings are also presented.

scholarly journals Surgical repair for isolated congenital double-orifice mitral valve

2011 ◽  
Vol 39 (2) ◽  
pp. 268-270
Author(s):  
Dan Zhu ◽  
Anqing Chen ◽  
Qiang Zhao
Keyword(s):  
Mitral Valve ◽  
Surgical Repair ◽  
Double Orifice

scholarly journals The Appearance of an Underrecognized Congenital Heart Disease in a Patient With COVID-19 Pneumonia

2021 ◽  
Vol 9 ◽  
pp. 232470962110433
Author(s):  
Sofia Lakhdar ◽  
Chandan Buttar ◽  
Sameen Hassan ◽  
Most Sirajum Munira ◽  
Theo Trandafirescu
Keyword(s):  
Heart Failure ◽  
Emergency Department ◽  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Surgical Repair ◽  
Late Presentation ◽  
Complex Congenital Heart Disease ◽  
Productive Cough ◽  
Shortness Of Breath

A 60-year-old woman presented to the emergency department with worsening shortness of breath and non-productive cough for 1 week, which was preceding a recent COVID-19 infection. At the time the patient thought this was part of the constellation of symptoms of COVID-19, so she stayed home until her symptoms worsened to the point of needing hospitalization. The patient was found to have a rare and complex congenital heart disease that led her to develop acute heart failure precipitated by COVID-19 pneumonia. Medical management and surgical repair were essential in this patient given the late presentation.

scholarly journals Reconstructive surgery of idiopathic hypertrophic cardiomyopathy, systolic anterior motion and severe mitral regurgitation

2004 ◽  
Vol 132 (7-8) ◽  
pp. 254-257
Author(s):  
Ivan Stojanovic ◽  
Milan Vukovic ◽  
Vojislava Neskovic ◽  
Milan Babic ◽  
Miroljub Zlatanovic ◽  
...  
Keyword(s):  
Mitral Valve ◽  
Mitral Annulus ◽  
Subaortic Stenosis ◽  
Mitral Insufficiency ◽  
Systolic Anterior Motion ◽  
Anterior Leaflet ◽  
Septal Myectomy ◽  
Long Time ◽  
Subaortic Obstruction ◽  
Idiopathic Disease

Hypertrophie obstructive cardiomyopathy (HOCM) is an idiopathic disease frequently associated with systolic anterior motion (SAM). The anterior leaflet of mitral valve is sucked by Ventury effect into the left ventricle outflow tract making subaortic stenosis more severe and producing mitral insufficiency at the same time. Septal myectomy along with mitral valve replacement has been the treatment of choice for a long time. An understanding of pathoanatomy and hemodynamics of the disease has opened possibility for total reconstructive treatment of both subaortic stenosis and mitral insufficiency in such patients. This is a case report of 50-year-old male with severe subaortic stenosis (136/70 mmHg) due to HOCM and SAM along with grade IV mitral insufficiency. Septal myectomy was performed. Mitral insufficiency was managed by reducing the height of posterior cusp along with remodeling of mitral annulus by Carpentier-Classic ring. In that way, subaortic obstruction was reduced to 30.9/10 mmHg while mitral insufficiency was lowered to negligible level. The patient was discharged from hospital with sinus rhythm eight days after the surgery.

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