A very unusual combination of straddling and overriding of the tricuspid valve associated with clefting of the mitral valve

2005 ◽  
Vol 15 (4) ◽  
pp. 422-424 ◽  
Author(s):  
Liane Eberhardt ◽  
Philippe Chetaille ◽  
Bernard Kreitmann
Keyword(s):  
Mitral Valve ◽  
Tricuspid Valve ◽  
Septal Defect ◽  
Surgical Repair ◽  
Atrioventricular Septal Defect ◽  
Left Ventricular ◽  
Atrioventricular Junction ◽  
Unusual Association ◽  
The Right ◽  
Double Orifice

We describe a patient in whom we found dual orifices in a straddling and overriding tricuspid valve, with two normally sized ventricles and a cleft in the mitral valve. The patient underwent successful surgical repair. We discuss the concept of “double-orifice right atrium”, as well as the need to differentiate the isolated cleft of the morphologically mitral valve from the zone of apposition between the left ventricular components of the bridging leaflets seen in the setting of atrioventricular septal defect with common atrioventricular junction. We emphasise the unusual association of these abnormalities of the right and left atrioventricular valves in patients with separate atrioventricular junctions.

Solitary trunk from the right ventricle with a cleft mitral valve simulating the trifoliate left valve of an atrioventricular septal defect with common atrioventricular junction

2004 ◽  
Vol 14 (4) ◽  
pp. 444-446
Author(s):  
Geoffrey P. Sharratt ◽  
Robert H. Anderson
Keyword(s):  
Mitral Valve ◽  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Left Ventricular ◽  
Papillary Muscles ◽  
Left Valve ◽  
Anterior Leaflet ◽  
Atrioventricular Junction ◽  
Arterial Trunk ◽  
The Right

We report a case of a true cleft in the anterior leaflet of the mitral valve. The cleft, however, is directed toward the ventricular septum, and the left ventricular papillary muscles have the same arrangement as seen in the setting of a common atrioventricular orifice. The atrioventricular septum is intact. This appearance reflects the presence, in this patient, of right ventricular origin of a solitary arterial trunk, so that there was no outflow tract within the left ventricle to interpose between the mitral valve and the septum.

scholarly journals Results of surgical repair of atrioventricular septal defect with double-orifice left atrioventricular valve

2009 ◽  
Vol 138 (5) ◽  
pp. 1167-1171 ◽  
Author(s):  
Gerard J.F. Hoohenkerk ◽  
Arnold C.G. Wenink ◽  
Paul H. Schoof ◽  
Dave R. Koolbergen ◽  
Eline F. Bruggemans ◽  
...  
Keyword(s):  
Septal Defect ◽  
Surgical Repair ◽  
Atrioventricular Septal Defect ◽  
Atrioventricular Valve ◽  
Double Orifice

The current surgical perspective to repair of atrioventricular septal defect with common atrioventricular junction

2010 ◽  
Vol 20 (S3) ◽  
pp. 120-127 ◽  
Author(s):  
Tom R. Karl ◽  
Sylvio C. J. Provenzano ◽  
Graham R. Nunn ◽  
Robert H. Anderson
Keyword(s):  
Tetralogy Of Fallot ◽  
Septal Defect ◽  
Surgical Repair ◽  
Atrioventricular Septal Defect ◽  
Indications For Surgery ◽  
Cardiac Malformation ◽  
Technical Aspects ◽  
Atrioventricular Junction ◽  
Congenital Cardiac Malformation ◽  
Surgery Timing

AbstractAtrioventricular septal defect with common atrioventricular junction is a relatively common congenital cardiac malformation. It sometimes presents challenging surgical problems, especially when seen in combination with tetralogy of Fallot. We describe herein our current concepts regarding surgical repair of atrioventricular septal defect with and without tetralogy, discussing indications for surgery, timing, technical aspects, and outcomes.

Management of the left atrioventricular valve in 95 patients with atrioventricular septal defects and a common atrioventricular orifice—a ten year review

1991 ◽  
Vol 1 (4) ◽  
pp. 367-373 ◽  
Author(s):  
François Lacour-Gayet ◽  
Juan Comas ◽  
Jacqueline Bruniaux ◽  
Alain Serraf ◽  
Jean Losay ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Septal Defect ◽  
Primary Repair ◽  
Ventricular Outflow Tract ◽  
Atrioventricular Septal Defect ◽  
Left Ventricular ◽  
Atrioventricular Valve ◽  
Septal Defects ◽  
Left Ventricular Outflow ◽  
The Right

SummaryDuring a 10 year interval, between January 1, 1981 and January 1, 1991, primary repair of atrioventricular septal defect with a common atrioventricular orifice was performed in 95 patients younger than 1 year. Patients with atrioventricular septal defect having two atrioventricular orifices and a small ventricular septal defect, and those with severe hypoplasia of the left ventricle, were not included in the present study. According to the presence of associated anomalies, patients were divided into those with simple forms (72%) and those with complex forms (28%). These included parachute deformity of the left atrioventricular valve (10 cases), multiple muscular ventricular septal defects (5 cases), low-lying infundibular stenosis of the right ventricle (4 cases), obstruction of the left ventricular outflow tract (3 cases), tetralogy ofFallot (2 cases) and hypoplasia of the left ventricle (2 cases).

Surgical Correction of a Partial Atrioventricular Septal Defect With a Ventricular Septal Defect in a Dog

2005 ◽  
Vol 41 (2) ◽  
pp. 137-143 ◽  
Author(s):  
Midori Akiyama ◽  
Ryou Tanaka ◽  
Kohji Maruo ◽  
Yoshihisa Yamane
Keyword(s):  
Mitral Valve ◽  
Ventricular Septal Defect ◽  
Septal Defect ◽  
Left Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Atrioventricular Septal Defect ◽  
Left Ventricular ◽  
Surgical Correction ◽  
Cardiac Murmur ◽  
Left Ventricular Outflow

Echocardiography of a dog with a cardiac murmur revealed an ostium primum septal defect, a ventricular septal defect, and mitral valve malformation with regurgitation. The mitral valve and tricuspid valve were separated and displaced at the same level as the ventricular septum. The mitral valve had a cleft in the septal cusp. Cardiac catheterization and angiocardiography showed a left-to-right shunt and a "goose-neck sign," which indicated an elongated left ventricular outflow tract. The diagnosis of a partial atrioventricular septal defect with ventricular septal defect was made. Surgical correction was successfully performed under extracorpo-real circulation using a cardiopulmonary bypass system.

Echo-morphological correlates in patients with atrioventricular septal defect and common atrioventricular junction

2006 ◽  
Vol 16 (S3) ◽  
pp. 43-51 ◽  
Author(s):  
William T. Mahle ◽  
Girish S. Shirali ◽  
Robert H. Anderson
Keyword(s):  
Septal Defect ◽  
Clinical Presentation ◽  
Three Dimensional ◽  
Atrioventricular Septal Defect ◽  
Atrioventricular Canal ◽  
Atrioventricular Junction ◽  
Atrioventricular Septal Defects ◽  
Septal Defects ◽  
The Common ◽  
The Right

It is now well recognized that patients fulfilling the diagnostic criterions for the group of hearts usually described as atrioventricular canal malformations, or atrioventricular septal defects, can present with shunting at atrial level, at both atrial and ventricular levels, and on occasion, with shunting only at ventricular level.1,2It is also well recognized that, in most instances, the patients with shunting exclusively at atrial level have separate atrioventricular valvar orifices for the right and left ventricles, this arrangement often described as the “ostium primum” variant of atrial septal defect.3Morphological and echocardiographic studies, however, have shown that, in this variant presumed to represent deficient atrial septation, it is the atrioventricular septal structures, rather than the atrial septum, which are deficient, the phenotypic feature being the presence of a common atrioventricular junction.4,5In this review, we will show how, using modern day echocardiographic techniques, particularly the newly developed potential for three-dimensional display, it is an easy matter to identify the presence or absence of the common atrioventricular junction, and then to demonstrate the various relationships between the valvar leaflets, the septal structures, and the common junction itself which determine the options for clinical presentation within the group.

scholarly journals Atrioventricular Septal Defect: What Is in a Name?

2021 ◽  
Vol 8 (2) ◽  
pp. 19
Author(s):  
Michael Rigby
Keyword(s):  
Mitral Valve ◽  
Septal Defect ◽  
Adult Congenital Heart Disease ◽  
Atrioventricular Septal Defect ◽  
Atrioventricular Canal ◽  
Aortic Leaflet ◽  
Adult Congenital ◽  
The Right ◽  
Cardiac Surgeons ◽  
Almost All

Robert Anderson has made a huge contribution to almost all aspects of morphology and understanding of congenital cardiac malformations, none more so than the group of anomalies that many of those in the practice of paediatric cardiology and adult congenital heart disease now call ‘Atrioventricular Septal Defect’ (AVSD). In 1982, with Anton Becker working in Amsterdam, their hallmark ‘What’s in a name?’ editorial was published in the Journal of Thoracic and Cardiovascular Surgery. At that time most described the group of lesions as ‘atrioventricular canal malformation’ or ‘endocardial cushion defect’. Perhaps more significantly, the so-called ostium primum defect was thought to represent a partial variant. It was also universally thought, at that time, that the left atrioventricular valve was no more than a mitral valve with a cleft in the aortic leaflet. In addition to this, lesions such as isolated cleft of the mitral valve, large ventricular septal defects opening to the inlet of the right and hearts with straddling or overriding tricuspid valve were variations of the atrioventricular canal malformation. Anderson and Becker emphasised the differences between the atrioventricular junction in the normal heart and those with a common junction for which they recommended the generic name, ‘atrioventricular septal defect’. As I will discuss, over many years, they continued to work with clinical cardiologists and cardiac surgeons to refine diagnostic criteria and transform the classification and understanding of this complex group of anomalies. Their emphasis was always on accurate diagnosis and communication, which is conveyed in this review.

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