The current surgical perspective to repair of atrioventricular septal defect with common atrioventricular junction

2010 ◽  
Vol 20 (S3) ◽  
pp. 120-127 ◽  
Author(s):  
Tom R. Karl ◽  
Sylvio C. J. Provenzano ◽  
Graham R. Nunn ◽  
Robert H. Anderson
Keyword(s):  
Tetralogy Of Fallot ◽  
Septal Defect ◽  
Surgical Repair ◽  
Atrioventricular Septal Defect ◽  
Indications For Surgery ◽  
Cardiac Malformation ◽  
Technical Aspects ◽  
Atrioventricular Junction ◽  
Congenital Cardiac Malformation ◽  
Surgery Timing

AbstractAtrioventricular septal defect with common atrioventricular junction is a relatively common congenital cardiac malformation. It sometimes presents challenging surgical problems, especially when seen in combination with tetralogy of Fallot. We describe herein our current concepts regarding surgical repair of atrioventricular septal defect with and without tetralogy, discussing indications for surgery, timing, technical aspects, and outcomes.

scholarly journals Tetralogy of Fallot with Scimitar syndrome in VACTERL: a very rare association

2017 ◽  
Vol 5 (1) ◽  
pp. 269
Author(s):  
Puneet Anand
Keyword(s):  
Congenital Anomaly ◽  
Tetralogy Of Fallot ◽  
Management Strategy ◽  
Septal Defect ◽  
Early Embryogenesis ◽  
Scimitar Syndrome ◽  
Cardiac Malformation ◽  
Rare Congenital Anomaly ◽  
Rare Association ◽  
Congenital Cardiac Malformation

The most common congenital cardiac malformation that occurs in VACTERL association is ventricular septal defect. Scimitar syndrome is a very rare congenital anomaly of the heart occurring due to maldevelopment of the lung bud or the pulmonary vascularization during early embryogenesis. The occurrence of Scimitar syndrome in VACTERL and its association with another cardiac congenital anomaly such as Tetralogy of Fallot (TOF) is extremely rare. The association of Tetralogy of Fallot with Scimitar syndrome alters the management strategy. Hereby, a very rare combination of Scimitar syndrome and tetralogy of Fallot in a four-year-old boy with VACTERL is presented, who underwent a successful single-stage surgical correction.

scholarly journals Late Presentation of Aortopulmonary Window with Tetralogy of Fallot: Report of a Very Rare Case

2021 ◽  
pp. 1-3
Author(s):  
Muhammad Ishtiaque Sayeed Al-Manzo ◽  
Prodip Kumar Biswas ◽  
M.A.K. Azad ◽  
Eliyas Patwary ◽  
Jesmin Hossain ◽  
...  
Keyword(s):  
Tetralogy Of Fallot ◽  
Rare Case ◽  
Surgical Repair ◽  
Preoperative Evaluation ◽  
Late Presentation ◽  
Aortopulmonary Window ◽  
Cardiac Malformation ◽  
Congenital Cardiac Malformation

Aortopulmonary window (APW) itself is a rare congenital cardiac malformation and its association with Tetralogy of Fallot (TOF) makes it more uncommon. We report a case of APW with TOF who presented at 4-year 10 months of age. As the boy was still in operable state, after thorough preoperative evaluation successful surgical repair was done.

Surgical repair of atrioventricular septal defect with common atrioventricular junction when associated with tetralogy of Fallot or double outlet right ventricle

2006 ◽  
Vol 16 (S3) ◽  
pp. 59-64 ◽  
Author(s):  
Christo I. Tchervenkov ◽  
Samantha Hill ◽  
Danny Del Duca ◽  
Stephen Korkola
Keyword(s):  
Right Ventricle ◽  
Tetralogy Of Fallot ◽  
Septal Defect ◽  
Surgical Techniques ◽  
Atrioventricular Septal Defect ◽  
Double Outlet Right Ventricle ◽  
Biventricular Repair ◽  
Atrioventricular Junction ◽  
Common Arterial Trunk ◽  
Arterial Trunk

The association of atrioventricular septal defect with common atrioventricular junction and malformations of the ventricular outflow tracts presents a significant challenge for the surgeon. In the most common of these, the association with tetralogy of Fallot, several surgical techniques have been described, and shown to deliver excellent results.1–10On the other hand, in the setting of more extreme malformations, such as double-outlet right ventricle, discordant ventriculo-arterial connections, or common arterial trunk, albeit rare lesions, the combination presents a more formidable surgical challenge, as evidenced by the few reports of successful repair of these lesions. This challenge is both physiological, when dealing with a very sick neonate or infant, as well as anatomical in terms of the complexity of the malformation and the ability to achieve a successful biventricular repair. Our goal in this review is to discuss the surgical treatment in the setting of tetralogy of Fallot and double outlet right ventricle, with emphasis on biventricular repair.

A very unusual combination of straddling and overriding of the tricuspid valve associated with clefting of the mitral valve

2005 ◽  
Vol 15 (4) ◽  
pp. 422-424 ◽  
Author(s):  
Liane Eberhardt ◽  
Philippe Chetaille ◽  
Bernard Kreitmann
Keyword(s):  
Mitral Valve ◽  
Tricuspid Valve ◽  
Septal Defect ◽  
Surgical Repair ◽  
Atrioventricular Septal Defect ◽  
Left Ventricular ◽  
Atrioventricular Junction ◽  
Unusual Association ◽  
The Right ◽  
Double Orifice

We describe a patient in whom we found dual orifices in a straddling and overriding tricuspid valve, with two normally sized ventricles and a cleft in the mitral valve. The patient underwent successful surgical repair. We discuss the concept of “double-orifice right atrium”, as well as the need to differentiate the isolated cleft of the morphologically mitral valve from the zone of apposition between the left ventricular components of the bridging leaflets seen in the setting of atrioventricular septal defect with common atrioventricular junction. We emphasise the unusual association of these abnormalities of the right and left atrioventricular valves in patients with separate atrioventricular junctions.

scholarly journals Double-Outlet Right Ventricle in a Chianina Calf

Animals ◽  
2021 ◽  
Vol 11 (2) ◽  
pp. 318
Author(s):  
Domenico Caivano ◽  
Maria Chiara Marchesi ◽  
Piero Boni ◽  
Noemi Venanzi ◽  
Giovanni Angeli ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Septal Defect ◽  
Heart Defects ◽  
Double Outlet Right Ventricle ◽  
Cardiac Malformation ◽  
Septal Defects ◽  
Congenital Cardiac Malformation ◽  
The Right ◽  
Similar Complex ◽  
Echocardiographic Findings

Congenital heart defects have been occasionally reported in cattle and ventricular septal defect represents the most frequently encountered anomaly. The double-outlet right ventricle is a rare congenital ventriculoarterial malformation reported only in certain cattle breeds. We describe this rare and complex congenital cardiac malformation observed in a 10-day-old male Chianina calf. Clinical examination showed tachycardia, tachypnea, jugular pulses, cyanotic mucous membranes and a right apical systolic murmur. Transthoracic echocardiography revealed severe dilation of the right-sided cardiac chambers with a markedly hypoplastic left ventricle. Both aorta and pulmonary artery leaving the right ventricle in parallel alignment with the tricuspid valve were suggestive of a dual-outlet right ventricle. Interventricular and interatrial septal defects were also visualized. Post-mortem examination confirmed the echocardiographic findings. To the authors’ knowledge, a similar complex congenital cardiac malformation has not been reported in calves of the Chianina breed to date.

Anatomical Repair of an Unusual Combination of Tetralogy of Fallot and Atrioventricular Septal Defect With Unroofed Coronary Sinus

2015 ◽  
Vol 30 (11) ◽  
pp. 849-852
Author(s):  
Sachin Talwar ◽  
Rakesh Kumar ◽  
Amolkumar Bhoje ◽  
Shiv Kumar Choudhary ◽  
Balram Airan
Keyword(s):  
Tetralogy Of Fallot ◽  
Coronary Sinus ◽  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Unroofed Coronary Sinus ◽  
Unusual Combination
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