Combination of double aortic arch and interruption of aortic arch in pulmonary atresia with ventricular septal defect

2015 ◽  
Vol 25 (5) ◽  
pp. 994-995
Author(s):  
Dai Asada ◽  
Toshiyuki Itoi ◽  
Kenji Hamaoka

AbstractNo reports on pulmonary atresia with ventricular septal defect with the combination of double aortic arch and interruption between left and right carotid arteries have been published so far.

2021 ◽  
pp. 1-3
Author(s):  
Mariana Lemos ◽  
Miguel Fogaça da Mata ◽  
Ana Coutinho Santos

Abstract An 18-month-old male with pulmonary atresia and ventricular septal defect presented with stridor after neonatal systemic-to-pulmonary artery shunt surgery, that persisted on follow-up. CT angiography revealed a vascular ring with balanced double aortic arch.


Author(s):  
Fernando Cesar Gimenes B. Santos ◽  
Ulisses Alexandre Croti ◽  
Carlos Henrique De Marchi ◽  
Sírio Hassem Sobrinho

2014 ◽  
Vol 2014 ◽  
pp. 1-4
Author(s):  
Devendra V. Kulkarni ◽  
Rahul G. Hegde ◽  
Ankit Balani ◽  
Anagha R. Joshi

Pulmonary atresia with ventricular septal defect (PA-VSD) with pulmonary arterial supply arising from the aorta representing large MAPCAs associated with a right sided aortic arch is an uncommon anomaly. Most of the patients succumb to severe respiratory compromise or congestive cardiac failure very early. We report the clinical details and imaging findings of a case of PA-VSD with a right sided aortic arch and a calcified pulmonary arteriovenous malformation (AVM) in a 21-year-old postpartum female with no previous episodes of cyanosis who was diagnosed as having a cardiac anomaly on echocardiography when she presented with breathlessness during the 8th month of the pregnancy.


2019 ◽  
Vol 3 (2) ◽  
Author(s):  
Yoshimi Matsumoto ◽  
Masahiro Kamada ◽  
Naomi Nakagawa ◽  
Yukiko Ishiguchi

Abstract Background Double aortic arch (DAA) and pulmonary artery sling (PAS) are vascular ring formations that present in neonates and infants with symptoms of respiratory stenosis. Case summary The patient was a girl with suspected ventricular septal defect (VSD), right aortic arch (AA), left patent ductus arteriosus, and bilateral superior vena cava (SVC) on foetal echography in the first day of life. The girl was delivered at 40 weeks and 4 days of gestation. Ventricular septal defect, DAA, coarctation of the left AA, and bilateral SVC were diagnosed. Contrast-enhanced computed tomography at Day 16 revealed PAS with concurrent anomalous tracheal branching in addition to DAA. The right A2 segmental artery, which supplies the right upper pulmonary artery, showed abnormal branching from the left pulmonary artery (LPA). At 3 months of age, VSD patching, left AA resection distal to the root of the left subclavian artery, arterial ligament dissection, and LPA replacement were performed. Discussion Pulmonary artery sling coexists with anomalous branching of the trachea and abnormal branching of the right pulmonary artery (RPA). Our patient had an extremely rare case of DAA concurrent with PAS and presented with anomalous tracheal and RPA branching. We were concerned that increased pulmonary blood flow caused by the VSD would exacerbate tracheal displacement. Radical surgery at 3 months of age resulted in good postoperative progress.


Author(s):  
M.V. Medvedev , M.V. Kubrina , O.L. Galkina et all

A retrospective analysis of 12 cases of prenatal diagnosed of pulmonary atresia with ventricular septum defect (PA-VSD) is presented. In the study of the fetal four chambers view cardiomegaly was detected in 2 (16.7 %) cases. The axis of the heart changed in 8 (66.7 %) cases. Ventricular septal defect (VSD) and overriding dilated ascending aorta were identified in all cases. Central pulmonary arteries were identified in 12 (100%) cases. In 7 (58.3 %) cases the dimensions of the pulmonary arteries were at least 2SD below the mean value for gestational age in the remaining 5 (41.7 %) cases were very narrow. Pulmonary blood supply was prenatally identified as ductus arteriosus (DA) in 8 (66.7 %) and major aortopulmonary collateral arteries (MARSAs) in 3 (25 %) and mixed (DA + MARSAs) in 1 (8.3 %). Fetal hydrops is detected in 2 (16.7 %) cases. The left aortic arch was in 9 (75 %) cases and right aortic arch — 3 (25 %). The average gestational age at prenatal diagnosis was 19.6 (13–23) weeks of gestation. Early diagnosis is represented by one case in 13 weeks of gestation. Еxtracardiac defects were registered in 3 (25 %) cases. Outcomes in fetuses with PA-VSD: termination of pregnancy — 10 (83.4 %), fetal death — 1 (8.3 %), only 1 (8.3 %) survivor


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