Cor triatriatum sinister with left anomalous pulmonary venous return to innominate vein

2019 ◽  
Vol 29 (3) ◽  
pp. 428-430
Author(s):  
Christoph Jaschinski ◽  
Murat Uzdenov ◽  
Tsvetomir Loukanov
Keyword(s):  
Venous Return ◽  
Signs And Symptoms ◽  
Radical Resection ◽  
Complete Loss ◽  
Cor Triatriatum ◽  
Simultaneous Operation ◽  
Vertical Vein ◽  
Rare Congenital Abnormality ◽  
Cor Triatriatum Sinister ◽  
Anomalous Pulmonary Venous Return

AbstractCor triatriatum sinister is a rare congenital abnormality, with varying signs and symptoms related to the anatomic features and the components of the accompanying cardiac abnormalities. We present a 3-year-old girl who underwent successful simultaneous operation with complete loss of the membrane and ligation of vertical vein by anomalous venous return. The principles for surgical management of cor triatriatum can be summarised as radical resection of the membrane and correction of other intracardiac anomalies.

A Rare Case of Cardiogenic Shock: Cor Triatriatum With Anomalous Pulmonary Venous Return

2019 ◽  
Vol 10 (5) ◽  
pp. 651-653
Author(s):  
Bosco Moscoso ◽  
Stefano Congiu ◽  
Javier Mayol ◽  
Carin Walter ◽  
José M. Caffarena
Keyword(s):  
Cardiogenic Shock ◽  
Left Atrium ◽  
Clinical Condition ◽  
Rare Case ◽  
Venous Return ◽  
Cor Triatriatum ◽  
Cor Triatriatum Sinister ◽  
Anomalous Pulmonary Venous Return ◽  
Life Threatening ◽  
Rare Malformation

Obstructive total anomalous pulmonary venous return (TAPVR) is a potentially life-threatening clinical condition and a surgical emergency. Left-sided partial anomalous pulmonary venous return (PAPVR) in association with a subdivided left atrium, also known as cor triatriatum sinister (CTS), is a very rare malformation that can mimic obstructive TAPVR. We present a case of a newborn with clinical manifestation of cardiogenic shock caused by CTS and PAPVR.

Association of a Cor Triatriatum Sinister and a Right Partial Anomalous Pulmonary Venous Return. A Case Report

2005 ◽  
Vol 105 (2) ◽  
pp. 217-218 ◽  
Author(s):  
S.G. Tueche ◽  
H. Demanet ◽  
J.P. Goldstein ◽  
H. Dessy ◽  
P. Viart ◽  
...  
Keyword(s):  
Case Report ◽  
Venous Return ◽  
Cor Triatriatum ◽  
Cor Triatriatum Sinister ◽  
Anomalous Pulmonary Venous Return

Cor triatriatum with a left upper anomalous pulmonary venous return to the innominate vein

2013 ◽  
Vol 24 (3) ◽  
pp. 546-548 ◽  
Author(s):  
Claire Galoin-Bertail ◽  
Marielle Gouton
Keyword(s):  
Pulmonary Hypertension ◽  
Atrial Septal Defect ◽  
Septal Defect ◽  
Venous Return ◽  
Innominate Vein ◽  
Cor Triatriatum ◽  
Cardiac Anomaly ◽  
Congenital Cardiac Anomaly ◽  
Cor Triatriatum Sinister ◽  
Anomalous Pulmonary Venous Return

AbstractCor triatriatum sinister is an uncommon congenital cardiac anomaly accounting for 0.1% of all congenital cardiac malformations, with an anomalous venous return being a frequently associated condition. We present the case of a 14-year-old girl misdiagnosed as having an atrial septal defect with pulmonary hypertension who actually had a cor triatriatum with a left upper anomalous pulmonary venous return to the innominate vein.

Cor triatriatum and intracardiac anomalous pulmonary venous return: an inborn atrial flow inversion

2021 ◽  
Author(s):  
Giulia Poretti ◽  
Stiljan Hoxha ◽  
Antonio Segreto ◽  
Camilla Sandrini ◽  
Angela Murari ◽  
...  
Keyword(s):  
Venous Return ◽  
Cor Triatriatum ◽  
Anomalous Pulmonary Venous Return

scholarly journals A rare case of obstructive supracardiac TAPVR (Total Anomalous Pulmonary Venous Return) with aberrant right subclavian artery.

2021 ◽  
Vol 28 (7) ◽  
pp. 1058-1060
Author(s):  
Fazal ur Rehman ◽  
◽  
Sabiha Khan ◽  
Waqas Ali ◽  
Asif Ali Khuhro ◽  
...  
Keyword(s):  
Aortic Arch ◽  
Subclavian Artery ◽  
Right Atrium ◽  
Venous Return ◽  
Pulmonary Veins ◽  
Vena Cava ◽  
Aberrant Right Subclavian Artery ◽  
Vertical Vein ◽  
Anomalous Pulmonary Venous Return ◽  
Tract Infections

Congenital aortic arch malformations manifest a broad-spectrum of differences and abnormalities that come from disturbed embryogenesis of branchial arches. Current case was a 10 months old baby girl with length of 69 cm (less than –3 SD) and weight of 5.5 kg (less than –3 SD). The patient had history of recurrent lower respiratory tract infections since the time of birth and failure to gain adequate weight since the time of birth. The patient has been having multiple check-ups with registered medical practitioners in the nearby locality and multiple courses of antibiotics with only partial resolution of symptoms. The 2-D echocardiogram showed her to be a case of supracardiac type of “Total Anomalous Pulmonary Venous Return (TAPVR)”. All pulmonary veins making a confluence and draining into the right atrium. Significant turbulence observed at the level of superior vena cava to right atrium junction. A level of obstruction was recorded at the junction of the confluence of pulmonary veins and the vertical vein. There was aberrant right subclavian artery from the aortic arch as its third branch with no obstruction or aneurysm formation, having retrotracheal and esophageal course.

scholarly journals A Rare Case of Subtotal Cor Triatriatum With Anomalous Pulmonary Venous Return in an Adult

Research ◽  
2016 ◽  
Vol 3 ◽  
Author(s):  
Pramod Theetha Kariyanna ◽  
Nikhil Warrier ◽  
Sudhanva Hegde ◽  
Yuliya Kats
Keyword(s):  
Rare Case ◽  
Venous Return ◽  
Cor Triatriatum ◽  
Anomalous Pulmonary Venous Return

Abstract 17056: Report Of An Adult Living With Undiagnosed Total Anomalous Pulmonary Venous Return

Circulation ◽  
2021 ◽  
Vol 144 (Suppl_2) ◽  
Author(s):  
Kent Beam ◽  
Jorge Alegria ◽  
Matthew Schwartz
Keyword(s):  
Venous Return ◽  
Pulmonary Veins ◽  
Innominate Vein ◽  
Exercise Intolerance ◽  
Pulmonary Venous Obstruction ◽  
X Ray ◽  
Venous Structure ◽  
Vertical Vein ◽  
Anomalous Pulmonary Venous Return ◽  
Chest X Ray

Case Presentation: 25-year-old male presented with cellulitis and abscess of the lower extremity. He was an immigrant from Guatemala. He worked in landscaping and played soccer with limited exertion. His exam was notable for cyanosis and clubbing of all digits. A II/VI systolic ejection murmur at the left upper sternal border and a mildly accentuated P2 was auscultated. ECG was notable for right axis deviation and right ventricle hypertrophy. Chest x-ray showed a widened mediastinum with perihilar vascular prominence. CT chest with contrast demonstrated all pulmonary veins forming a large, coalescing venous structure draining into the left innominate vein. Transthoracic echocardiogram confirmed total pulmonary venous return by way of a large vertical vein draining into a dilated innominate vein and a 2.7 cm ostium secundum ASD. Discussion: Total anomalous pulmonary venous return (TAPVR) is a rare, often deadly condition. Most patients die in infancy. In the rare adult patient with unrepaired TAPVR, exercise intolerance, cyanosis, clubbing of the digits, and growth retardation is often noted. A right ventricular heave with auscultation of a fixed, split second heart sound with a loud pulmonic component is common. On chest x-ray, the classic “snowman” appearance is seen with vertical vein connections as in our patient. Right heart enlargement represents the base, and an enlarged connecting vertical vein and SVC make up the upper portion. Echocardiography can demonstrate the anomalous pulmonary venous conduit coursing behind the left atrium. CT angiography can also reveal TAPVR and the patient’s specific anatomy. Amongst the few surviving adult TAPVR patients, similar characteristics include large ASDs, short anomalous veins, and absence of pulmonary venous obstruction. A large interatrial connection provides adequate systemic flow. The latter two factors reduce pulmonary vascular resistance, hence improving pulmonary flow and systemic oxygen concentrations.

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