Anomalous origin of right pulmonary artery: diagnosis, treatment, and follow-up in an adult patient

2020 ◽  
Vol 30 (8) ◽  
pp. 1199-1201
Author(s):  
Susan Pumacayo-Cárdenas ◽  
Moises Jimenez-Santos ◽  
Edgar Quea-Pinto
Keyword(s):  
Pulmonary Artery ◽  
Heart Defects ◽  
Anomalous Origin ◽  
Medium Term ◽  
Branch Pulmonary Artery ◽  
Right Pulmonary Artery ◽  
Favourable Evolution ◽  
Rare Malformation ◽  
The Right

AbstractAnomalous origin of a branch pulmonary artery from the aorta is a rare malformation, accounting for 0.12% of all congenital heart defects. We present the case of a 43-year-old man with an anomalous origin of the right pulmonary artery (AORPA) from the ascending aorta. Reimplantation of the right pulmonary artery was carried out successfully, with favourable evolution in the medium-term follow-up. It is the first described case that receives corrective treatment in adulthood with a favourable evolution.

Anomalous Origin of the Right Pulmonary Artery From the Aorta and Congenital Tracheal Stenosis: Staged Repair in a Neonate

2021 ◽  
pp. 215013512110493
Author(s):  
Nguyen L.T. Truong ◽  
Tran Q. Vinh ◽  
Nguyen T. Mai
Keyword(s):  
Pulmonary Artery ◽  
Tracheal Stenosis ◽  
Neonatal Period ◽  
Ascending Aorta ◽  
Anomalous Origin ◽  
Congenital Tracheal Stenosis ◽  
Unique Case ◽  
Right Pulmonary Artery ◽  
Rare Malformation ◽  
The Right

Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA), sometimes referred to as hemitruncus, is a rare malformation. We report a unique case of AORPA associated with Ebstein's anomaly and with congenital tracheal stenosis due to complete tracheal rings. The AORPA and tracheal stenosis were both successfully corrected in the neonatal period.

scholarly journals The role of modern imaging techniques in the diagnosis of malposition of the branch pulmonary arteries and possible association with microdeletion 22q11.2

2012 ◽  
Vol 23 (2) ◽  
pp. 181-188 ◽  
Author(s):  
Goran Cuturilo ◽  
Danijela Drakulic ◽  
Aleksandar Krstic ◽  
Marija Gradinac ◽  
Tamara Ilisic ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Imaging Techniques ◽  
Heart Defects ◽  
Pulmonary Arteries ◽  
Left Pulmonary Artery ◽  
Modern Imaging ◽  
Right Pulmonary Artery ◽  
Rare Malformation ◽  
22Q11.2 Microdeletion ◽  
The Right

AbstractMalposition of the branch pulmonary arteries is a rare malformation with two forms. In the typical form, pulmonary arteries cross each other as they proceed to their respective lungs. The “lesser form” is characterised by the left pulmonary artery ostium lying directly superior to the ostium of the right pulmonary artery, without crossing of the branch pulmonary arteries. Malposition of the branch pulmonary arteries is often associated with other congenital heart defects and extracardiac anomalies, as well as with 22q11.2 microdeletion. We report three infants with crossed pulmonary arteries and one adolescent with “lesser form” of the malformation. The results suggest that diagnosis of malposition of the branch pulmonary arteries could be challenging if based solely on echocardiography, whereas modern imaging technologies such as contrast computed tomography and magnetic resonance angiography provide reliable establishment of diagnosis. In addition, we performed the first molecular characterisation of the 22q11.2 region among patients with malposition of the branch pulmonary arteries and revealed a 3-megabase deletion in two out of four patients.

scholarly journals A Rare Case of Adult Aortopulmonary Window Combined with Anomalous Origin of the Right Pulmonary Artery from the Aorta Leading to Eisenmenger Syndrome

2021 ◽  
Vol 49 (1) ◽  
pp. 030006052098465
Author(s):  
Mingyue Cui ◽  
Binfeng Xia ◽  
Heru Wang ◽  
Haihui Liu ◽  
Xia Yin
Keyword(s):  
Pulmonary Artery ◽  
Rare Case ◽  
Congenital Heart ◽  
Respiratory Tract Infections ◽  
Anomalous Origin ◽  
Aortopulmonary Window ◽  
Eisenmenger Syndrome ◽  
Right Pulmonary Artery ◽  
The Right ◽  
Tract Infections

Aortopulmonary window is a rare congenital heart disease that can increase pulmonary vascular resistance, exacerbate left-to-right shunt and lead to heart failure and respiratory tract infections. Most patients die during childhood. We report a 53-year-old male patient with a large aortopulmonary window combined with anomalous origin of the right pulmonary artery from the aorta, with Eisenmenger syndrome and without surgery.

Anomalous origin of the right pulmonary artery from the ascending aorta: Diagnosis by magnetic resonance imaging

1995 ◽  
Vol 18 (2) ◽  
pp. 118-121 ◽  
Author(s):  
Tae Kyoung Kim ◽  
Yeon Hyoen Choe ◽  
Hak Soo Kim ◽  
Jae Kon Ko ◽  
Young Tak Lee ◽  
...  
Keyword(s):  
Magnetic Resonance Imaging ◽  
Magnetic Resonance ◽  
Pulmonary Artery ◽  
Ascending Aorta ◽  
Anomalous Origin ◽  
Resonance Imaging ◽  
Right Pulmonary Artery ◽  
The Right

Total anomalous origin of the coronary circulation from the right pulmonary artery

2008 ◽  
Vol 17 (4) ◽  
pp. 246-249 ◽  
Author(s):  
Fabio Tavora ◽  
Allen Burke ◽  
Robert Kutys ◽  
Ling Li ◽  
Renu Virmani
Keyword(s):  
Pulmonary Artery ◽  
Coronary Circulation ◽  
Anomalous Origin ◽  
Right Pulmonary Artery ◽  
The Right

Prenatal diagnosis of anomalous origin of the right pulmonary artery from the ascending aorta

2002 ◽  
Vol 12 (2) ◽  
pp. 186-188 ◽  
Author(s):  
Mi-Jin Jung ◽  
Shi-Joon Yoo
Keyword(s):  
Prenatal Diagnosis ◽  
Pulmonary Artery ◽  
Ascending Aorta ◽  
Anomalous Origin ◽  
Fetal Ultrasound ◽  
Cardiac Screening ◽  
Rare Anomaly ◽  
Right Pulmonary Artery ◽  
The Right

We report a case of anomalous origin of the right pulmonary artery from the ascending aorta that was diagnosed by fetal ultrasound at 21 weeks of gestation. The clue to the diagnosis was present in the three-vessel view, this being one of the views that we use for fetal cardiac screening. The anomaly was corrected surgically at 11 days of age. We discuss the importance of prenatal diagnosis in the management of this rare anomaly.

Intramural Aortic Course Should Always Be Considered for Anomalous Origin of the Left Coronary Artery From the Right Pulmonary Artery

2019 ◽  
Vol 10 (4) ◽  
pp. 508-512
Author(s):  
Vishal Agrawal ◽  
Nikunj Vaidhya ◽  
Mrinal Patel ◽  
Amit Mishra ◽  
Dinesh Patel
Keyword(s):  
Coronary Artery ◽  
Pulmonary Artery ◽  
Left Coronary Artery ◽  
Anomalous Origin ◽  
Preoperative Imaging ◽  
Rare Entity ◽  
Right Pulmonary Artery ◽  
The Right

Anomalous origin of the left coronary artery (LCA) from the right pulmonary artery (ALCARPA) is an extremely rare subset of an already rare entity, anomalous origin of the LCA from the pulmonary artery. Whenever it is diagnosed preoperatively, one should be extremely vigilant about the potential intramural course of the descending part of the LCA in the aorta. Preoperative imaging frequently fails to delineate this intramural course. We report our experience with one such case where we had accidentally injured the LCA during dissection from the right pulmonary artery. Although it was successfully managed, it reinforces our aforementioned point concerning the importance of vigilance in seeking to identify intramurality as a component of this anomaly of coronary artery origin.

Hypoplastic left heart syndrome with anomalous origin of right pulmonary artery

2020 ◽  
pp. 021849232095506
Author(s):  
Ashish Mishra ◽  
Bhavik Champaneri ◽  
Yashpal Rana ◽  
Gaurav Singh ◽  
Senthilraj Thangasami ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Hypoplastic Left Heart Syndrome ◽  
Venous Drainage ◽  
Anomalous Origin ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Right Pulmonary Artery ◽  
Complex Forms ◽  
The Right ◽  
Left Heart Syndrome

Classic hypoplastic left heart syndrome is a rare but fatal congenital heart disease associated with variable underdevelopment of the left side of the heart. Complex forms of hypoplastic left heart syndrome have been reported to coexist with anomalous pulmonary venous drainage, transposition of the great arteries, or pulmonary valve dysplasia. We report a case of hypoplastic left heart syndrome with anomalous origin of the right pulmonary artery from the ascending aorta a rare association not reported in the literature. Preoperative comprehensive echocardiography is essential for diagnosis and accurate recognition of such rare anatomic variations.

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