Prune-belly syndrome and pulmonary hypoplasia: A potential cause of death

2001 ◽  
Vol 43 (2) ◽  
pp. 172-175 ◽  
Author(s):  
Hanifi Soylu ◽  
N Onur Kutlu ◽  
Ergun Sonmezgoz ◽  
Yasar Bukte ◽  
Unsal Ozgen ◽  
...  
2009 ◽  
Vol 49 (5) ◽  
pp. 304
Author(s):  
Yenny Yenny ◽  
Kusuma P. A ◽  
Damanik M. P.

Prune-belly syndrome, also known as Eagle-Barretsyndrome, is a congenital anomaly comprisingthree clinical findings: deficient abdominalmusculature, urinary tract anomalies, andbilateral cryptorchidism. Other clinical findings involvingrespiratory, skeletal, digestion and cardiovascular systemmay also accompany the syndrome. The incidence isapproximately 1 : 30,000 to 40,000 live births and 95%of cases occur in boys. Pulmonary hypoplasia and kidneyfailure are important prognostic factors that contributeto 60% of mortality rate. Treatment includes surgicalcorrection of the abdominal wall and urinary tract,orchidopexy and other supportive managements.l-4 Wereport 4 cases on typical Prune-belly syndrome, togetherwith other clinical variants.


2010 ◽  
Vol 45 (11) ◽  
pp. 2217-2221 ◽  
Author(s):  
Abdol-Mohammad Kajbafzadeh ◽  
Mohammad Reza Rasouli ◽  
SeyedSaeid Dianat ◽  
Behtash G. Nezami ◽  
Amir Hassan Mahboubi ◽  
...  

1981 ◽  
Vol 5 (6) ◽  
pp. 548-549 ◽  
Author(s):  
James W. Reinig ◽  
Nancy S. Curry ◽  
Stephen I. Schabel ◽  
R. Duane Holland

2011 ◽  
Vol 35 (3) ◽  
pp. 241-243 ◽  
Author(s):  
Kristoff Verdonck ◽  
Gregory Van Eeckhout ◽  
Veerle De Boe ◽  
Paul Wylock

1979 ◽  
Vol 51 (6) ◽  
pp. 475-480 ◽  
Author(s):  
C. R. J. WOODHOUSE ◽  
M. J. KELLETT ◽  
D. I. WILLIAMS

2018 ◽  
Vol 51 ◽  
pp. 150-153 ◽  
Author(s):  
Taro Banno ◽  
Yoichi Kakuta ◽  
Kohei Unagami ◽  
Akiko Sakoda ◽  
Masayoshi Okumi ◽  
...  

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