Cochlear ossification after labyrinthine schwannoma surgery

We present the case of a young female patient diagnosed with Cogan’s syndrome after the rapid onset of profond hearing and vestibular loss with concomitant eye symptoms. After appropriate medical treatment, her hearing did not respond and she underwent bilateral simultaneous cochlear implantation with findings of extensive cochlear ossification in both ears. The case and outcome are described in the body of the paper.

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Auditory Performance of Children With Cochlear Ossification and Partial Implant Insertion

The Laryngoscope ◽

10.1288/00005537-199209000-00009 ◽

1992 ◽

Vol 102 (9) ◽

pp. 1001???1005 ◽

Cited By ~ 23

Author(s):

John L. Kemink ◽

Susan Zimmerman-Phillips ◽

Paul R. Kileny ◽

Jill B. Firszt ◽

Michael A. Novak

Keyword(s):

Auditory Performance ◽

Cochlear Ossification

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The role of preoperative imaging for auditory implants in children

Otolaryngologia Polska ◽

10.5604/01.3001.0014.2438 ◽

2020 ◽

Vol 74 (6) ◽

pp. 1-5

Author(s):

Małgorzata Burzyńska-Makuch ◽

Józef Mierzwiński ◽

Karolina Haber

Keyword(s):

Inner Ear ◽

Cochlear Implantation ◽

Preoperative Imaging ◽

Surgical Approaches ◽

Clinical Decisions ◽

Imaging Studies ◽

Inner Ear Malformations ◽

Ear Malformations ◽

Cochlear Ossification ◽

Temporal Bones

Introduction: Preoperative imaging, besides audiological evaluation, plays a major role in evaluation of candidacy for auditory implants, and in particular cochlear implants. It is essential to assess whether the basic criteria necessary for implantation are met. Diagnostic imaging is crucial not only in determining candidacy, but also determining the feasibility of cochlear implantation as it allow to anticipate surgical difficulties which could preclude or complicate the implantation of the device. The aim of the study is to present the protocol for the evaluation of preoperative imaging studies with particular focus on the factors potentially affecting clinical decisions in children qualified for cochlear implantation. Material and method: Preoperative imaging studies of 111 children performed prior to cochlear implantation were analyzed: high-resolution computed tomography (HRCT) of temporal bones and MRI. The assessment was made according to the presented protocol. Results: Pathologies and anomalies identified during the assessment of preoperative imaging studies significantly altered clinical decisions in 30% of patients. In the study group, in 17% of patients inner ear malformations were identified. 2.7% of children were disqualified from a cochlear implantation due to severe congenital inner ear malformations. 9% of the patients have had bacterial meningitis. In 50% of them difficulties related to complete or progressive cochlear ossification occurred. In 4.5% of patients less common surgical approaches other than mastoidectomy with a posterior tympanotomy were applied. Discussion: Preoperative imaging allow for the identification of significant pathologies and anomalies affecting qualification decisions and further treatment. HRCT and MRI are complementary to each other for preoperative imaging. The two modalities in combination allow accurate and optimal evaluation of the anatomical structures prior to implantation. Inner ear malformations and cochlear ossification following meningitis are relatively frequently encountered in children qualified for a cochlear implant.

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Auditory Brainstem Implant in Adult Patient With Cochlear Ossification From Otosclerosis

Otology & Neurotology ◽

10.1097/mao.0000000000002946 ◽

2020 ◽

Vol Publish Ahead of Print ◽

Author(s):

Laura H. Christopher ◽

Kathryn Noonan ◽

Zachary Barnard ◽

Gautum Mehta ◽

Jordan Rock ◽

...

Keyword(s):

Adult Patient ◽

Auditory Brainstem ◽

Auditory Brainstem Implant ◽

Cochlear Ossification

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Medical, surgical and audiological complications of the first 100 adult cochlear implant patients in Birmingham

The Journal of Laryngology & Otology ◽

10.1017/s002221510014602x ◽

1999 ◽

Vol 113 (24) ◽

pp. 14-17 ◽

Cited By ~ 42

Author(s):

D. W. Proops ◽

R. L. Stoddart ◽

I. Donaldson

Keyword(s):

Cochlear Implant ◽

Wound Infection ◽

Complication Rate ◽

Older Patients ◽

Major Complication ◽

Medical Complication ◽

Minor Complication ◽

Major Complication Rate ◽

Cochlear Ossification ◽

Electrode Insertion

AbstractOf the first 100 patients implanted on the Midland Cochlear Implant Programme the commonest aetiologies of deafness were idiopathic 31 per cent, meningitis 28 per cent and cochlear otosclerosis 16 per cent.The major complication rate was three per cent. The most severe was one individual who post-operatively developed a cerebral infarct and subsequently died. The minor complication rate was 39 per cent, all of which successfully resolved, and included 11 cases of wound infection, nine cases of vertigo, three transient facial palsies and two post-operative bleeds.Older patients and men were most likely to have a post-operative medical complication. Women were more likely to have an abnormal electrode insertion. Meningitis and otosclerosis were the most complicated aetiologies in terms of cochlear ossification and electrode insertion. A non-patient cochlea was associated with fewer active electrodes. In six cases which had been reported pre-operatively as showing patent cochleas, some form of obstructional ossification was encountered. Patients functioning with greater than 15 active electrodes performed better on auditory tests than patients with fewer than 15 active electrodes.

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Cochlear Implantation in the Setting of Cochlear Ossification as Sequela of Malarial Meningitis

Otology & Neurotology ◽

10.1097/mao.0000000000000551 ◽

2016 ◽

Vol 37 (1) ◽

pp. e3-e4

Author(s):

Maja Svrakic ◽

Benjamin Rafii ◽

J. Thomas Roland

Keyword(s):

Cochlear Implantation ◽

Cochlear Ossification

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Auditory rehabilitation of patients with neurofibromatosis Type 2 by using cochlear implants

Journal of Neurosurgery ◽

10.3171/2011.5.jns101929 ◽

2011 ◽

Vol 115 (4) ◽

pp. 827-834 ◽

Cited By ~ 33

Author(s):

Pamela C. Roehm ◽

Jon Mallen-St. Clair ◽

Daniel Jethanamest ◽

John G. Golfinos ◽

William Shapiro ◽

...

Keyword(s):

Cochlear Implants ◽

Cochlear Implantation ◽

Neurofibromatosis Type ◽

Neurofibromatosis Type 2 ◽

Speech Understanding ◽

Speech Discrimination ◽

Auditory Rehabilitation ◽

Open Set ◽

Cochlear Ossification

Object The aim of this study was to determine whether patients with neurofibromatosis Type 2 (NF2) who have intact ipsilateral cochlear nerves can have open-set speech discrimination following cochlear implantation. Methods Records of 7 patients with documented NF2 were reviewed to determine speech discrimination outcomes following cochlear implantation. Outcomes were measured using consonant-nucleus-consonant words and phonemes; Hearing in Noise Test sentences in quiet; and City University of New York sentences in quiet and in noise. Results Preoperatively, none of the patients had open-set speech discrimination. Five of the 7 patients had previously undergone excision of ipsilateral vestibular schwannoma (VS). One of the patients who received a cochlear implant had received radiation therapy for ipsilateral VS, and another was undergoing observation for a small ipsilateral VS. Following cochlear implantation, 4 of 7 patients with NF2 had open-set speech discrimination following cochlear implantation during extended follow-up (15–120 months). Two of the 3 patients without open-set speech understanding had a prolonged period between ipsilateral VS resection and cochlear implantation (120 and 132 months), and had cochlear ossification at the time of implantation. The other patient without open-set speech understanding had good contralateral hearing at the time of cochlear implantation. Despite these findings, 6 of the 7 patients were daily users of their cochlear implants, and the seventh is an occasional user, indicating that all of the patients subjectively gained some benefit from their implants. Conclusions Cochlear implantation can provide long-term auditory rehabilitation, with open-set speech discrimination for patients with NF2 who have intact ipsilateral cochlear nerves. Factors that can affect implant performance include the following: 1) a prolonged time between VS resection and implantation; and 2) cochlear ossification.

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Cochlear Implantation in Cochlear Ossification

Otology & Neurotology ◽

10.1097/mao.0000000000001613 ◽

2018 ◽

Vol 39 (1) ◽

pp. 17-28 ◽

Cited By ~ 5

Author(s):

Ashish Vashishth ◽

Andrea Fulcheri ◽

Sampath Chandra Prasad ◽

Margherita Bassi ◽

Gianluca Rossi ◽

...

Keyword(s):

Cochlear Implantation ◽

Cochlear Ossification

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Cochlear Implants in Pediatric Bacterial Meningitis

Otolaryngology ◽

10.1016/j.otohns.2008.05.203 ◽

2008 ◽

Vol 139 (2_suppl) ◽

pp. P63-P63

Author(s):

Brandon Isaacson ◽

Kenneth H Lee ◽

Joe W Kutz ◽

Peter S Roland

Keyword(s):

Hearing Loss ◽

Bacterial Meningitis ◽

Cochlear Implant ◽

Tertiary Care ◽

Performance Outcomes ◽

Case Review ◽

Retrospective Case ◽

Labyrinthitis Ossificans ◽

Cochlear Ossification ◽

And Performance

Objective 1) To determine pediatric cochlear implant performance outcomes for hearing loss secondary to bacterial meningitis. 2) To determine if a performance difference exists in pediatric cochlear implant patients with and without labyrinthitis ossificans. Methods A retrospective case review was performed at a tertiary care multi-disciplinary cochlear implant program. 45 children were implanted from 1991 to 2006 whose hearing loss resulted from bacterial meningitis. Mode of communication, school placement and performance were reviewed. Results 21 patients(52%) were in a mainstream educational enviroment and 19 (48%) were in a special needs enviroment. 24 subjects (58%) used an auditory-verbal mode of communication, while 17 (42%) used total communication. The mean speech reception threshold was 28dB with a range from 5 to 65dB. 14 subjects (56%) had labyrinthis ossifcans, while 11 subjects (44%) did not. Conclusions The present study demonstrated that over half of our subjects developed labyrinthitis ossificans. Despite the presence of cochlear ossification, patients with bacterial meningitis-induced hearing loss can often perform in a main-stem classroom with auditory-verbal communication.

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