Introduction. Sinus pericranii is a rare vascular anomaly. It is
characterized by abnormal communication between the extracranial and
intracranial venous system, usually involving the superior sagittal sinus and
occasionally the transverse sinus. Off the midline lesions are extremely
rare. Multiplicity, associated venous lakes, venous angioma and lateral
location are unusual and unique presentation of sinus pericranii. Case
report. A case of multiple congenital off-midline sinus pericranii in the
left frontotemporal and parietal region is presented. Magnetic resonance
imaging showed an extracranial vascular anomaly connected with the
intracranial venous system through abnormal diploic or emissary veins. The
lesions were removed completely by surgery. Conclusion. Sinus pericranii is a
rare vascular malformation with unique clinical and radiological features.
Sinus pericranii may cause fatal complications, and it must be treated by
surgical or endovascular procedures.