Severe Intrarenal Fibrosis, Infundibular Stenosis, Renal Cysts, and Persistent Perilobar Nephrogenic Rests in a Patient With Beckwith-Wiedemann Syndrome 27 years After Diffuse Nephroblastomatosis and Wilms Tumor: Natural Progression or a Consequence of Treatment?

2002 ◽  
Vol 24 (5) ◽  
pp. 389-393 ◽  
Author(s):  
Roshni Kulkarni ◽  
J. Stuart Wolf ◽  
Niru Padiyar ◽  
Leonard Zuckerman ◽  
Renuka Gera ◽  
...  
2001 ◽  
Vol 125 (8) ◽  
pp. 1081-1083 ◽  
Author(s):  
Ronald S. Muc ◽  
Wayne Grayson ◽  
Johannes J. Grobbelaar

Abstract Five previous cases of extrarenal Wilms tumor (EWT) occurring in the uterus have been reported. The oldest patient was 22 years. We report a case of uterine EWT occurring in a 42-year-old woman. Histologically, there was typical triphasic differentiation, including epithelial, blastemal, and mesenchymal elements. The important differential diagnosis in this age group, the malignant mixed mullerian tumor, is excluded by the absence of glomeruloid structures and primitive tubules. The exact histogenesis of EWT is unknown but most likely relates to the presence of nephrogenic rests occurring in the female genital tract.


2020 ◽  
Vol 67 (11) ◽  
Author(s):  
Cécile Picard ◽  
Pierre Leblond ◽  
Jean‐Pierre Pracros ◽  
Grégoire Schneider ◽  
Frédéric Hameury ◽  
...  

2006 ◽  
Vol 47 (3) ◽  
pp. 260-267 ◽  
Author(s):  
Norman E. Breslow ◽  
J. Bruce Beckwith ◽  
Elizabeth J. Perlman ◽  
Anthony E. Reeve

2020 ◽  
Vol 7 (3) ◽  
pp. 119-124
Author(s):  
L. I. Shats ◽  
B. V. Kondratiev ◽  
M. B. Belogurova

Nephrogenic rests and nephroblastomatosis describe persistence of embryonic renal parenchyma (metanephric blastema) beyond 36 weeks of gestation, when nephrogenesis is normally complete. This persistent metanephric blastema may transform into the Wilms tumor, and are detected in 30–40 % of unilateral nephroblstoma and nearly 100 % in bilateral cases. The risk of Wilms tumour is increased in any type of nephrogenic rests/nephroblastomatosis but it is higher in infants and in patients with intralobar nephrogenic rests. We cite below several studies described different types of nephrogenic rests, their connection with nephroblastoma development and the details of diagnostic. We refer to clinical examples, in that regard. Two cases are presented: bilateral diffuse hyperplastic perilobar nephroblastomatosis in one child and an infant with combination of perilobar nephrogenic rests in one kidney and Wilms tumour in the other kidney.


2021 ◽  
Vol 8 (1) ◽  
pp. 7-10
Author(s):  
Nitin James Peters ◽  
Swapnil Pattanshetti ◽  
Muneer Abas Malik ◽  
Ram Samujh ◽  
Kirti Gupta

2004 ◽  
Vol 34 (2) ◽  
pp. 152-155 ◽  
Author(s):  
Pedram Argani ◽  
John P. Gearhart ◽  
Stanley S. Siegelman ◽  
Naveen Subhas

2001 ◽  
Vol 25 (10) ◽  
pp. 1290-1296 ◽  
Author(s):  
Trudie E. Muir ◽  
John C. Cheville ◽  
Donna J. Lager

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