Primary Angiitis of the Central Nervous System Mimicking Sporadic Creutzfeldt-Jakob Disease

2018 ◽  
Vol 32 (3) ◽  
pp. 258-261
Author(s):  
Dian He ◽  
Gang Cai ◽  
Yan Li ◽  
Qi Liu ◽  
Kang Xiao ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Primary Angiitis ◽  
Jakob Disease ◽  
The Central Nervous System

scholarly journals Creutzfeldt–Jakob Disease with a Five-Year Clinical Course, Multicentric Cerebellar Prion Plaques and Prior History of Biopsy-Proven Primary Angiitis of the Central Nervous System: A Case for Iatrogenic Exposure?

Viruses ◽  
2020 ◽  
Vol 12 (12) ◽  
pp. 1411
Author(s):  
Kristina Jeon ◽  
Jeffrey T. Joseph ◽  
Gerard H. Jansen ◽  
Anne Peterson ◽  
J. David Knox ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Parietal Lobe ◽  
Clinical Course ◽  
Prior History ◽  
System A ◽  
Primary Angiitis ◽  
History Of ◽  
Jakob Disease ◽  
The Central Nervous System

Creutzfeldt–Jakob disease (CJD) is a rapidly progressive neurodegenerative disease that can arise spontaneously, genetically, or be acquired through iatrogenic exposure. Most patients die within a year of symptom onset. It is rare, affecting 1–2 per million per year, and the majority of cases are sporadic. Primary angiitis of the central nervous system (PACNS) is also rare, affecting 2.4 per million per year. We present a case of an unusually long clinical course of CJD, almost five years, which began with symptoms of apraxia. The patient had biopsy-proven PACNS 16 years prior to clinical presentation, and the site of biopsy was the left parietal lobe. Autopsy revealed multicentric prion plaques in the cerebellum, in the setting of normal genetic testing. The presence of plaques in the cerebellum, and prior neurosurgery, raises the possibility of iatrogenic exposure. We present the details of this case, including pathology from the original biopsy and final autopsy, as well as a review of relevant cases in the literature.

scholarly journals Lymphocytic primary angiitis of the central nervous system with fan-shaped linear enhancement converging to the lateral ventricles: a case report

2014 ◽  
Vol 54 (9) ◽  
pp. 709-714
Author(s):  
Taro Okunomiya ◽  
Takashi Kageyama ◽  
Kanta Tanaka ◽  
Daisuke Kambe ◽  
Akiyo Shinde ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Case Report ◽  
Lateral Ventricles ◽  
Primary Angiitis ◽  
The Central Nervous System

Neuroradiologic Characteristics of Primary Angiitis of the Central Nervous System According to the Affected Vessel Size

2017 ◽  
Vol 29 (1) ◽  
pp. 37-44 ◽  
Author(s):  
Christian Thaler ◽  
Ann-Katrin Kaufmann-Bühler ◽  
Tserenchunt Gansukh ◽  
Amarjargal Gansukh ◽  
Simon Schuster ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Vessel Size ◽  
Primary Angiitis ◽  
The Central Nervous System

Mycophenolate mofetil as induction and long-term maintaining treatment in childhood: Primary angiitis of the central nervous system

2017 ◽  
Vol 84 (3) ◽  
pp. 353-356 ◽  
Author(s):  
Anna Rosati ◽  
Alessandra Cosi ◽  
Massimo Basile ◽  
Alice Brambilla ◽  
Renzo Guerrini ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Mycophenolate Mofetil ◽  
Primary Angiitis ◽  
The Central Nervous System

Involvement of CD45RO+ T Lymphocyte Infiltration in a Patient with Primary Angiitis of the Central Nervous System Restricted to Small Vessels

2001 ◽  
Vol 45 (3) ◽  
pp. 184-185 ◽  
Author(s):  
Tamaki Iwase ◽  
Kosei Ojika ◽  
Shigehisa Mitake ◽  
Eiichi Katada ◽  
Hiroyuki Katano ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
T Lymphocyte ◽  
Lymphocyte Infiltration ◽  
Small Vessels ◽  
Primary Angiitis ◽  
The Central Nervous System

Black Blood MRI in Suspected Large Artery Primary Angiitis of the Central Nervous System

2012 ◽  
Vol 23 (3) ◽  
pp. 379-383 ◽  
Author(s):  
Thomas Pfefferkorn ◽  
Jennifer Linn ◽  
Maximilian Habs ◽  
Christina Opherk ◽  
Clemens Cyran ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Black Blood ◽  
Large Artery ◽  
Black Blood Mri ◽  
Primary Angiitis ◽  
The Central Nervous System
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