Chest wall sarcoma of childhood with a good prognosis.

Four cases of a locally invasive sarcoma of the chest wall are described in children aged between 8 and 14 years. Although its morphology resembles a Ewing's sarcoma of bone there are light and electron microscopical features that are distinctive. The sarcoma is thought to represent an entity which has not previously been defined. Its clinical importance lies in the fact that the prognosis with appropriate treatment appears to be good. One child died after 2 1/2 years, but the others are alive 6, 8, and 16 years after presentation.

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Extra-osseous Ewing's sarcoma of chest wall

ANZ Journal of Surgery ◽

10.1111/j.1445-2197.2009.05063.x ◽

2009 ◽

Vol 79 (10) ◽

pp. 752-753 ◽

Cited By ~ 2

Keyword(s):

Chest Wall ◽

Ewing’S Sarcoma ◽

Ewing's Sarcoma

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Primary Occipital Ewing’s Sarcoma with Subsequent Spinal Seeding

Case Reports in Pediatrics ◽

10.1155/2017/1521407 ◽

2017 ◽

Vol 2017 ◽

pp. 1-4 ◽

Cited By ~ 1

Author(s):

Ali Alqahtani ◽

Roaa Amer ◽

Eman Bakhsh

Keyword(s):

Posterior Fossa ◽

Ewing’S Sarcoma ◽

Ewing's Sarcoma ◽

Bone Cancer ◽

Surgical Excision ◽

Good Prognosis ◽

Bone Lesions ◽

History Of ◽

Magnetic Resonance Imaging Mri ◽

Whole Spine

Ewing’s sarcoma is a primary bone cancer that mainly affects the long bones. This malignancy is particularly common in pediatric patients. Primary cranial involvement accounts for 1% of cases, with occipital involvement considered extremely rare. In this case study, primary occipital Ewing’s sarcoma with a posterior fossa mass and subsequent relapse resulting in spinal seeding is reported. A 3-year-old patient presented with a 1-year history of left-sided headaches, localized over the occipital bone with progressive torticollis. Computed tomography (CT) imaging showed a mass in the left posterior fossa compressing the brainstem. The patient then underwent surgical excision followed by adjuvant chemoradiation therapy. Two years later, the patient presented with severe lower back pain and urinary incontinence. Whole-spine magnetic resonance imaging (MRI) showed cerebrospinal fluid (CSF) seeding from the L5 to the S4 vertebrae. Primary cranial Ewing’s sarcoma is considered in the differential diagnosis of children with extra-axial posterior fossa mass associated with destructive permeative bone lesions. Although primary cranial Ewing’s sarcoma typically has good prognosis, our patient developed metastasis in the lower spine. Therefore, with CNS Ewing’s sarcoma, screening of the entire neural axis should be taken into consideration for early detection of CSF seeding metastasis in order to decrease the associated morbidity and mortality.

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Ewing's sarcoma of rib

Bangladesh Medical Journal Khulna ◽

10.3329/bmjk.v50i1-2.35842 ◽

2018 ◽

Vol 50 (1-2) ◽

pp. 41-43

Author(s):

Sk Moazzem Hossain ◽

Farjana Kabir ◽

SM Kamal ◽

Debasish Kumar Ghosh

Keyword(s):

Pleural Effusion ◽

Chest Wall ◽

Ewing’S Sarcoma ◽

Ewing's Sarcoma ◽

Bone Tumour ◽

Mass Lesion ◽

College Hospital ◽

X Ray ◽

Medical College ◽

First Rib

Ewing's sarcoma is an uncommon malignant bone tumour occuring in children, adolescents and young adults. We report a case of a 13 year old male admitted to Khulna Medical College Hospital with history of pain and swelling in chest wall for two weeks. Earlier chest X-ray showed a mass lesion in the left upper part of chest wall and erosion of first rib. Subsequent X-ray revealed left sided massive pleural effusion. CT scan revealed a mass lesion in the left upper part of chest wall originated from left first rib and left sided pleural effusion. FNAC from the mass lesion revealed features suggestive of Ewing's sarcoma. Patient was treated with chemotherapy and after first cycle there was significant improvement of all the signs and symptoms.Bang Med J (Khulna) 2017; 50 : 41-43

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