scholarly journals Evaluation of Kinesiophobia and Its Correlations with Pain and Fatigue in Joint Hypermobility Syndrome/Ehlers-Danlos Syndrome Hypermobility Type

2013 ◽  
Vol 2013 ◽  
pp. 1-7 ◽  
Author(s):  
Claudia Celletti ◽  
Marco Castori ◽  
Giuseppe La Torre ◽  
Filippo Camerota
Keyword(s):  
Quality Of Life ◽  
Joint Hypermobility ◽  
Bivariate Analysis ◽  
Hypermobility Syndrome ◽  
Joint Hypermobility Syndrome ◽  
Cross Sectional ◽  
Ehlers Danlos Syndrome ◽  
The Impact ◽  
Danlos Syndrome

Ehlers-Danlos syndrome hypermobility type a. k. a. joint hypermobility syndrome (JHS/EDS-HT) is a hereditary musculoskeletal disorder associating generalized joint hypermobility with chronic pain. Anecdotal reports suggest a prominent role forkinesiophobiain disease manifestations, but no study has systematically addressed this point.Objective. To investigate the impact ofkinesiophobiaand its relationship with pain, fatigue, and quality of life in JHS/EDS-HT.Design. Cross-sectional study.Subjects/Patients. 42 patients (40 female and 2 male) with JHS/EDS-HT diagnosis following standardized diagnostic criteria were selected.Methods. Disease features were analyzed by means of specific questionnaires and scales evaluating kinesiophobia, pain, fatigue, and quality of life. The relationships among variables were investigated using the Spearman bivariate analysis.Results.Kinesiophobiaresulted predominantly in the patients’ sample. The values ofkinesiophobiadid not correlate with intensity of pain, quality of life, and (or) the single component of fatigue. A strong correlation was discovered betweenkinesiophobiaand general severity of fatigue.Conclusions. In JHS/EDS-HT, the onset of pain-avoiding strategies is related to the presence of pain but not to its intensity. The clear-cut correlation betweenkinesiophobiaand severity of fatigue suggests a direct link between musculoskeletal pain and fatigue. In JHS/EDS-HT, the underlying mechanism is likely to be facilitated by primary disease characteristics, including hypotonia.

scholarly journals Association between Postural Orthostatic Tachycardia Syndrome and Joint Hypermobility

2021 ◽  
Vol 2021 ◽  
pp. 1-4
Author(s):  
Alexis Javier Atuesta-Rodriguez ◽  
Yimy F. Medina-Velasquez ◽  
Orfa Motta ◽  
Maria Isabel Narvaez-Medina ◽  
Federico Rondon-Herrera
Keyword(s):  
Systemic Disease ◽  
Clinical Manifestations ◽  
Joint Hypermobility ◽  
Postural Orthostatic Tachycardia Syndrome ◽  
Hypermobility Syndrome ◽  
Joint Hypermobility Syndrome ◽  
Ehlers Danlos Syndrome ◽  
Type 3 ◽  
The Impact

Joint hypermobility syndrome refers to increased joint flexibility beyond the normal range of motion. This syndrome has a benign form known as Ehlers-Danlos syndrome type 3. This is a disorder in which hypermobility is accompanied by clinical manifestations in the absence of any systemic disease. A clinical finding associated with this condition is postural orthostatic tachycardia syndrome. The following is a rare case of joint hypermobility syndrome and postural orthostatic tachycardia syndrome. The relevance of this case report lies in the impact that this disease had on the patient’s quality of life and the limitation in the performance of activities of daily living.

Low tendon stiffness and abnormal ultrastructure distinguish classic Ehlers‐Danlos syndrome from benign joint hypermobility syndrome in patients

2014 ◽  
Vol 28 (11) ◽  
pp. 4668-4676 ◽  
Author(s):  
Rie Harboe Nielsen ◽  
Christian Couppé ◽  
Jacob Kildevang Jensen ◽  
Morten Raun Olsen ◽  
Katja Maria Heinemeier ◽  
...  
Keyword(s):  
Joint Hypermobility ◽  
Hypermobility Syndrome ◽  
Joint Hypermobility Syndrome ◽  
Ehlers Danlos Syndrome ◽  
Tendon Stiffness ◽  
Benign Joint Hypermobility Syndrome ◽  
Danlos Syndrome

scholarly journals Dermal Ultrastructure in Low Beighton Score Members of 17 Families with Hypermobile-Type Ehlers-Danlos Syndrome

2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
Trinh Hermanns-Lê ◽  
Marie-Annick Reginster ◽  
Claudine Piérard-Franchimont ◽  
Philippe Delvenne ◽  
Gérald E. Piérard ◽  
...  
Keyword(s):  
Clinical Parameter ◽  
Joint Hypermobility ◽  
Elastic Fibers ◽  
Hypermobility Syndrome ◽  
Beighton Score ◽  
Joint Hypermobility Syndrome ◽  
Ehlers Danlos Syndrome ◽  
Transmission Electron ◽  
Asymptomatic Subjects ◽  
Danlos Syndrome

The distinction between the Ehlers-Danlos syndrome hypermobile type (EDSH) and the benign joint hypermobility syndrome (BJHS) is unclear. The aim of the present study was to compare skin ultrastructural abnormalities of EDSH and BJHS among different families. Skin of 23 EDSH, 27 BJHS, and 41 asymptomatic subjects from 17 families was examined using transmission electron microscopy. Similar ultrastructural abnormalities were found irrespective of the Beighton score. Flower-like collagen fibrils represented the key change and elastic fibers were altered as well. Beighton score is a clinical parameter rating joint mobility that appeared unrelated to quantitative and qualitative collagen ultrastructural alterations in the skin. Some EDSH family members fit with BJHS diagnosis. BJHS possibly represents a mild variant of EDSH.

Impaired quality of life and functional status in patients with benign joint hypermobility syndrome

MYOPAIN ◽  
2015 ◽  
Vol 23 (1-2) ◽  
pp. 28-33 ◽  
Author(s):  
Ebru Sahin ◽  
Selmin Gulbahar ◽  
Meltem Baydar ◽  
Gozde Ozcan Soylev ◽  
Cigdem Bircan ◽  
...  
Keyword(s):  
Quality Of Life ◽  
Functional Status ◽  
Joint Hypermobility ◽  
Hypermobility Syndrome ◽  
Joint Hypermobility Syndrome ◽  
Benign Joint Hypermobility Syndrome ◽  
Impaired Quality
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