scholarly journals Sudden Sensorineural Hearing Loss in the Only Hearing Ear: Large Vestibular Aqueduct Syndrome

2016 ◽  
Vol 2016 ◽  
pp. 1-3
Author(s):  
Kemal Koray Bal ◽  
Onur Ismi ◽  
Helen Bucioglu ◽  
Yusuf Vayısoğlu ◽  
Kemal Gorur
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Social Life ◽  
English Literature ◽  
Delayed Diagnosis ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

Sudden hearing loss in the only hearing ear cases are rarely published in the English literature; most of the cases are idiopathic. It is an otologic emergency needing urgent treatment. Delayed diagnosis can interfere with patient’s social life with interrupting the verbal communication. In this case report we presented a 33-year-old female patient having sudden sensorineural hearing loss in the only hearing ear diagnosed as bilateral large vestibular aqueduct syndrome.

Hyperbaric oxygen therapy for sudden sensorineural hearing loss in large vestibular aqueduct syndrome

2013 ◽  
Vol 128 (S1) ◽  
pp. S50-S54 ◽  
Author(s):  
H Shilton ◽  
M Hodgson ◽  
G Burgess
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Hyperbaric Oxygen ◽  
Hyperbaric Oxygen Therapy ◽  
Oxygen Therapy ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

AbstractIntroduction:We report the first use in Australia of hyperbaric oxygen therapy for sudden hearing loss following head trauma in a child with large vestibular aqueduct syndrome.Case report:A 12-year-old boy with large vestibular aqueduct syndrome presented with significant hearing loss following head trauma. He was treated with steroids and hyperbaric oxygen therapy, with good improvement of hearing thresholds on audiography. This case represents the first reported use of hyperbaric oxygen therapy for this indication in Australia, following a few previous reports of patients in Japan. We review the literature on management of acute sensorineural hearing loss in large vestibular aqueduct syndrome. The reported case demonstrates a potentially beneficial therapy for a rare condition that usually results in an inevitable decline in hearing.Conclusion:Hyperbaric oxygen therapy can be tolerated well by children, and may represent a potential treatment for sudden sensorineural hearing loss in patients with large vestibular aqueduct syndrome.

scholarly journals Large Vestibular Aqueduct Syndrome Associated with Sensorineural Hearing Loss. A Report of Two Cases.

1993 ◽  
Vol 86 (5) ◽  
pp. 641-645
Author(s):  
Masamitsu Senarita ◽  
Norihide Nishikawa ◽  
Akira Hara ◽  
Jun Kusakari ◽  
Yoshihisa Kurodaki
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct Syndrome ◽  
Large Vestibular Aqueduct

Bilateral sudden sensorineural hearing loss caused by Charcot-Marie-Tooth disease

2003 ◽  
Vol 117 (5) ◽  
pp. 399-401 ◽  
Author(s):  
Chariton E. Papadakis ◽  
Jiannis K. Hajiioannou ◽  
Dionysios E. Kyrmizakis ◽  
John G. Bizakis
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
English Literature ◽  
Sensory Neuropathy ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Prognostic Indicators ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
First Case

Charcot-Marie-Tooth (CMT) disease or hereditary motor and sensory neuropathy (HMSN) is a relatively common neurological syndrome, which has seldom been associated with hearing dysfunction, particularly sudden sensorineural hearing loss (SNHL). Families with autosomal dominant, autosomal recessive and X-linked forms of inheritance have been described.Sudden sensorineural hearing loss is a frustrating and frightening condition, especially if the hearing loss is bilateral. Regarding the site of the lesion, the evidence from the literature on HMSN suggests that either the VIIIth nerve or central auditory pathways are primarily involved in patients with hearing loss.We report the first case in the English literature of a patient with Charcot-Marie-Tooth type II disease presenting bilateral SNHL in the course of his disease. The patient was hospitalized for 15 days, and undergoing treatment without any audiological improvement. Detailed clinical, audiological and laboratory examination was performed.The aetiology and prognostic indicators of bilateral SNHL are discussed, as well as, the incidence of hearing loss in CMT patients.

Sudden Sensorineural Hearing Loss: A Hearing Emergency

2016 ◽  
Vol 9 (2) ◽  
pp. 177-182
Author(s):  
Susan Berg ◽  
Wafaa Kaf
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Middle Ear ◽  
Delayed Diagnosis ◽  
Diagnostic Reasoning ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Reasoning Process ◽  
Loss Of Hearing

Sudden sensorineural hearing loss (SSNHL) is a rare but emergent condition that afflicts approximately 4,000 Americans annually (Ciorba, Faita, Bianchini, Aimoni, & Scanelli, 2013; Scapa & Friedland, 2009; Stachler et al., 2012). It causes unilateral nerve loss of hearing that may not recover left untreated. Because SSNHL is uncommon, practitioners may be unaware of the urgency or the protocol for immediate testing and treatment. Aural fullness, a common presenting symptom of SSNHL, overlaps with more common outer and middle ear problems resulting in misdiagnosis and/or delayed diagnosis and treatment. This case study will lead practitioners through the necessary diagnostic reasoning process to identify, diagnose, treat, and refer SSNHL patients effectively.

Vestibular aqueduct in sudden sensorineural hearing loss

2007 ◽  
Vol 122 (9) ◽  
pp. 887-892 ◽  
Author(s):  
M Sugiura ◽  
S Naganawa ◽  
I M Ishida ◽  
M Teranishi ◽  
S Nakata ◽  
...  
Keyword(s):  
Magnetic Resonance Imaging ◽  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Contralateral Side ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Resonance Imaging ◽  
Vestibular Aqueduct ◽  
Pathological Conditions ◽  
Age Range

AbstractObjective:To evaluate the vestibular aqueduct in patients with sudden sensorineural hearing loss.Methods:We evaluated 19 patients (12 men and seven women; age range, 22−79 years) with unilateral sudden sensorineural hearing loss, using computed tomography and magnetic resonance imaging. All these patients had unilateral sudden sensorineural hearing loss. We also evaluated 47 control subjects (22 men and 25 women; age range, 22–79 years).Results:In sensorineural hearing loss affected ears, the width of the vestibular aqueduct at the midpoint and at the operculum was significantly greater than that in contralateral ears or in control ears. The width of the vestibular aqueduct at the midpoint and the operculum did not correlate with the audiometric threshold or the audiogram configuration. Contrast enhancement of the ipsilateral endolymphatic sac was observed in 17 of 19 patients with sudden sensorineural hearing loss (89 per cent). Eleven of these 17 patients also showed enhancement on the contralateral side, but no patient showed enhancement only on the contralateral side. In sensorineural hearing loss affected ears, the width of the vestibular aqueduct did not differ significantly between those patients with and without enhancement.Conclusions:The vestibular aqueducts of sudden sensorineural hearing loss affected ears are wider than those of controls. Precise imaging and evaluation of the inner ear is essential when investigating the pathological conditions responsible for sudden sensorineural hearing loss.

scholarly journals Sensorineural hearing loss in patients with large vestibular aqueduct

1995 ◽  
Vol 105 (3) ◽  
pp. 289-294 ◽  
Author(s):  
Tomoko Okumura ◽  
Haruo Takahashi ◽  
Iwao Honjo ◽  
Keiko Mitamura ◽  
Akira Takagi
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Aqueduct ◽  
Large Vestibular Aqueduct
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