Double outlet right atrium and complete atrioventricular septal defect with abnormal findings of the biopsied lung

1994 ◽  
Vol 4 (4) ◽  
pp. 402-404 ◽  
Author(s):  
Kiyoshi Suzuki ◽  
Toshio Kikuchi ◽  
Shigekazu Mimori
Keyword(s):  
Septal Defect ◽  
Pulmonary Veins ◽  
Pulmonary Arteries ◽  
Atrioventricular Septal Defect ◽  
Pulmonary Trunk ◽  
Atrial Septum ◽  
Corrective Surgery ◽  
Rare Type ◽  
Medial Hypertrophy ◽  
Complete Atrioventricular

SummaryWe describe a rare type of atrioventricular septal defect with common atrioventricular orifice and malaligned atrial septum, the latter feature resulting in severe obstruction of the left atrial egress. Excision of the atrial septum and banding of the pulmonary trunk was performed at the age of thirteen months. Lung biopsy demonstrated marked medial hypertrophy with severe intimal fibrosis in the small pulmonary arteries and mild thickening of the pulmonary veins, considered contraindications for corrective surgery.

Extracardiac Repair of Complex Unroofed Coronary Sinus

1998 ◽  
Vol 6 (1) ◽  
pp. 52-53
Author(s):  
Jacques AM van Son ◽  
Jörg Hambsch ◽  
Friedrich W Mohr
Keyword(s):  
Coronary Sinus ◽  
Septal Defect ◽  
Pulmonary Veins ◽  
Atrioventricular Septal Defect ◽  
Caval Vein ◽  
Unroofed Coronary Sinus ◽  
Superior Caval Vein ◽  
The Right ◽  
Unroofed Coronary Sinus Syndrome ◽  
Complete Atrioventricular

A technique for conversion of an intra-atrial baffle repair to an extracardiac repair is described for complex unroofed coronary sinus syndrome (including a complete atrioventricular septal defect) with connection of the left superior caval vein to the roof of the left-sided atrium. The left superior caval vein was divided distally and anastomosed to the right superior caval vein in an end-to-side fashion. In addition, the baffle in the left-sided atrium connecting the pulmonary veins with the left atrioventricular valve orifice was removed and the atria were septated. This extracardiac repair technique avoids the various disadvantages of the intra-atrial baffle technique such as creation of a small left atrium with low compliance.

Improved results of corrective repair for complete atrioventricular septal defect

2009 ◽  
Vol 56 (S 01) ◽  
Author(s):  
M Ono ◽  
H Görler ◽  
D Böthig ◽  
M Westhoff-Bleck ◽  
A Haverich ◽  
...  
Keyword(s):  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Complete Atrioventricular Septal Defect ◽  
Complete Atrioventricular

Characteristics of the pulmonary circulation in infants with complete atrioventricular septal defect

2020 ◽  
pp. 1-6
Author(s):  
Hirohito Doi ◽  
Jun Muneuchi ◽  
Mamie Watanabe ◽  
Yuichiro Sugitani ◽  
Ryohei Matsuoka ◽  
...  
Keyword(s):  
Down Syndrome ◽  
Gestational Age ◽  
Pulmonary Circulation ◽  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Left Heart ◽  
Complete Atrioventricular Septal Defect ◽  
Pulmonary Arterial ◽  
Heart Lesions ◽  
Complete Atrioventricular

Abstract Objective: Infants with complete atrioventricular septal defect occasionally accompany pulmonary hypertension; however, the pulmonary circulation can be altered by pulmonary vascular conditions as well as the left heart lesions. This study aimed to explore whether the left heart lesions were related to the pulmonary circulation among them. Methods: We performed echocardiography and cardiac catheterisation in 42 infants with complete atrioventricular septal defect and studied relationships between the pulmonary haemodynamic parameters and the left heart morphology. Results: Age and weight at preoperative evaluation were 65 days (47-114) (the median following interquartile range) and 5.5 kg (4.0-7.1), respectively. There were 27 individuals with Down syndrome. Gestational age was 38 weeks (37-39). Catheterisation showed mean pulmonary arterial pressure: 36 (29-46) mmHg, the ratio of pulmonary to systemic blood flow: 3.45 (2.79-4.98), pulmonary vascular resistance: 2.20 Wood units·m2 (1.53-3.65), and pulmonary arterial compliance: 2.78 (1.86-4.10) ml/Hg/m2. Echocardiography showed the Rastelli classification type A in 28 and type C in 14, moderate or severe left atrioventricular valve regurgitation in 19 patients (45%), atrioventricular valve index of 0.67 (0.56-0.79), left ventricular end-diastolic volume z score of 4.46 (1.96-7.78), and aortic valve diameter z score of −0.70 (−1.91 to 0.20). Multivariable regression analysis revealed that preoperative pulmonary vascular resistance was significantly correlated to gestational age (p = 0.002), and that preoperative pulmonary arterial compliance was significantly correlated to gestational age (p = 0.009) and Down syndrome (p = 0.036). Conclusions: The pulmonary circulation does not depend upon the presence of left heart lesions but gestational age and Down syndrome in infants with complete atrioventricular septal defect.

scholarly journals Treatment of Isolated Complete Atrioventricular Septal Defect: The Hue Central Hospital Experience

2020 ◽  
Vol Volume 13 ◽  
pp. 39-46
Author(s):  
Nguyen Thanh Xuan ◽  
Nguyen Xuan Hung ◽  
Tran Hoai An ◽  
Nguyen Dang Phuoc ◽  
Nguyen Huu Son ◽  
...  
Keyword(s):  
Septal Defect ◽  
Atrioventricular Septal Defect ◽  
Central Hospital ◽  
Complete Atrioventricular Septal Defect ◽  
Hospital Experience ◽  
Complete Atrioventricular
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