scholarly journals Monostotic Fibrous Dysplasia Involving the Mandible: A Case Report

2020 ◽  
Vol 8 ◽  
pp. 2050313X2093695
Author(s):  
Khalil Ibrahim Assiri
Keyword(s):  
Case Report ◽  
Fibrous Dysplasia ◽  
Fibrous Tissue ◽  
Malignant Potential ◽  
Definitive Diagnosis ◽  
Rapid Progression ◽  
Polyostotic Fibrous Dysplasia ◽  
Clinical Behavior ◽  
Normal Bone ◽  
Examination Methods

Fibrous dysplasia (FD) is a skeletal developmental anomaly, which is non-hereditary and idiopathic in origin. It is characterized by the replacement of normal bone with the excess proliferation of fibrous tissue in irregular bony trabeculae. Patients might complain of swelling, pain, or numbness on the affected side. The incidence of monostotic FD (MFD) is four times more than that of polyostotic fibrous dysplasia. In MFD, the maxilla is more commonly affected than the mandible. The clinical behavior and rapid progression of FD renders the treatment challenging. The malignant potential is 0.5% for untreated cases. Here, we present a case of FD involving the mandible. The clinical diagnostic approach, different imaging modalities, and histological examination methods for definitive diagnosis have been elaborated.

scholarly journals Fibrous dysplasia of maxilla – A rare case report

2021 ◽  
pp. 485-488
Author(s):  
Vijaya R Kamble ◽  
Shalini N Waghmare ◽  
Aditi V Rangari ◽  
Mangala Meti ◽  
Pritam Pohankar ◽  
...  
Keyword(s):  
Case Report ◽  
Fibrous Dysplasia ◽  
Female Patient ◽  
Malignant Transformation ◽  
Histological Examination ◽  
Rare Case ◽  
Definitive Diagnosis ◽  
Developmental Anomaly ◽  
Rare Case Report ◽  
Examination Methods

Fibrous dysplasia (FD) is a skeletal developmental anomaly, which is non-hereditary in origin and idiopathic in nature. It is a benign fibro-osseous disease that affects one or more bones. It usually affects unilaterally and is seen in the posterior region. Approximately 0.5% of untreated cases show the malignant transformation. We report the case of a 35-year-old female patient with FD involving the maxilla. The clinical diagnostic approach, different imaging modalities, and histological examination methods for definitive diagnosis have been elaborated.

Polyostotic fibrous dysplasia: A case report

2020 ◽  
Vol 12 (2) ◽  
pp. 43-45
Keyword(s):  
Case Report ◽  
Fibrous Dysplasia ◽  
Unknown Etiology ◽  
Pathological Features ◽  
Polyostotic Fibrous Dysplasia ◽  
Fibrous Stroma ◽  
Normal Bone ◽  
Skeletal Frame ◽  
Gnas1 Gene

Fibrous dysplasia (FD) is a fibro-osseous anomaly, where in normal bone is substituted with fibrous stroma. It is of unknown etiology but recently reported to be associated with mutation in GNAS1 gene (20q13.2) and consists of three subtypes monostotic, polyostotic and craniofacial. Craniofacial FD (CFD) mainly affects the bones of the craniofacial skeletal frame. This article reports a case of a 10 year old boy diagnosed with polyostotic fibrous dysplasia with clinical, radiographical and tissue pathological features.

scholarly journals Frontal sinus mucocele in association with polyostotic fibrous dysplasia: A case report

2019 ◽  
Vol 28 (3) ◽  
pp. 208-210
Author(s):  
Leslie Timothy Koh ◽  
Katherine Pollaers ◽  
Chris Rataphol Dhepnorrarat
Keyword(s):  
Bone Marrow ◽  
Case Report ◽  
Fibrous Dysplasia ◽  
Frontal Sinus ◽  
Endoscopic Drainage ◽  
Normal Bone Marrow ◽  
Osseous Tissue ◽  
Polyostotic Fibrous Dysplasia ◽  
Transnasal Approach ◽  
Normal Bone

Fibrous dysplasia is an uncommon developmental anomaly of bone wherein normal bone marrow is substituted and subsequently expanded by fibro-osseous tissue. Its association with mucocele formation in the paranasal sinuses is extremely rare. We present a case report of a patient with polyostotic fibrous dysplasia with frontal sinus mucocele formation, who underwent endoscopic drainage and marsupialisation via a transnasal approach.

scholarly journals Ossifying Fibroma of the Maxilla: A Case Report and Literature Update

2021 ◽  
pp. 1-4
Author(s):  
Abdouldaim Ukwas ◽  
Abdouldaim Ukwas ◽  
Mohammed Magdy ◽  
Mahmoud Elshik
Keyword(s):  
Case Report ◽  
Female Patient ◽  
Bone Grafting ◽  
Fibrous Tissue ◽  
Definitive Diagnosis ◽  
Ossifying Fibroma ◽  
Normal Bone ◽  
Calcified Tissues ◽  
Slow Growing ◽  
Normal Bone Tissue

Ossifying fibroma is a rare benign fibro-osseous neoplasm of the jaw characterized by the replacement of normal bone tissue by a combination of fibrous tissue and newly formed calcified tissues of bone and/or cementum-like material. Lesions often manifest at the 2nd to 4th decades of life with a predominant female predilection. The tumor is usually slow-growing and asymptomatic but can cause notable expansion of the jawbones. Definitive diagnosis of OF can be challenging and usually requires careful clinical, radiographic and histologic assessments. Treatment commonly depends on the size, location and aggressiveness of tumor and can accordingly vary from enucleation and curettage to resection and bone grafting. The prognosis is generally good when the lesion is completely removed, but recurrence is possible in some circumstances. The aim of this article is to present a case report of a recurrent ossifying fibroma in a 28-year-old female patient and to provide an update of the literature.

Pathological Fractures from Craniocervical Polyostotic Fibrous Dysplasia Treated with Percutaneous Vertebroplasty: Case Report

Skull Base ◽  
2007 ◽  
Vol 17 (S 1) ◽  
Author(s):  
Mirza Baig ◽  
David Dang ◽  
Gregory Christoforidis ◽  
Antonio Chiocca ◽  
Gabriel Josue
Keyword(s):  
Case Report ◽  
Fibrous Dysplasia ◽  
Percutaneous Vertebroplasty ◽  
Polyostotic Fibrous Dysplasia ◽  
Pathological Fractures

scholarly journals Long-term efficacy of oral alendronate therapy in an elderly patient with polyostotic fibrous dysplasia: A case report

2011 ◽  
Vol 2 (6) ◽  
pp. 1239-1242 ◽  
Author(s):  
GUI-DONG LI ◽  
AKIRA OGOSE ◽  
TETSUO HOTTA ◽  
HIROYUKI KAWASHIMA ◽  
TAKASHI ARIIZUMI ◽  
...  
Keyword(s):  
Elderly Patient ◽  
Case Report ◽  
Fibrous Dysplasia ◽  
Polyostotic Fibrous Dysplasia ◽  
Term Efficacy

scholarly journals Pleural effusion caused by polyostotic fibrous dysplasia involving the ribs, the sternum and the thoracic spine associated with multiple cystic degenerations – a case report

2019 ◽  
Vol 72 (1-2) ◽  
pp. 39-42
Author(s):  
Ivan Ergelasev ◽  
Ivan Kuhajda ◽  
Dejan Djuric ◽  
Danijela Kuhajda ◽  
Sinisa Maksimovic
Keyword(s):  
Case Report ◽  
Pleural Effusion ◽  
Fibrous Dysplasia ◽  
The Body ◽  
Bone Involvement ◽  
Cystic Degeneration ◽  
Histopathological Analysis ◽  
Daily Routine ◽  
Polyostotic Fibrous Dysplasia ◽  
Chest Wall Injury

Introduction. Fibrous dysplasia is a noninherited benign skeletal disorder associated with abnormal bone development. Single bone involvement, the monostotic form, accounts for 70 ? 80% of cases, while the polyostotic form, with multiple bone involvement, accounts for 20 ? 30% of cases. Cystic degeneration and occasional aneurysmal bone cyst formation may be found in fibrous dysplasia lesions, particularly in the costal lesions. Case Report. A 51-year-old man presented with acute shortness of breath after sustaining simple chest wall injury. Chest computed tomography showed multiple massive osteolytic rib lesions, as well as a massive left-sided pleural effusion with compression atelectasis of the lung parenchyma. Osteolytic lesions of the anterior 2nd and 7th thoracic vertebral body were found, along with a well defined osteolytic lesion in the body of the sternum. Video-assisted thoracoscopy of the left pleural space was performed and frozen sections, collected using endoscopic biopsy forceps of the cystic wall and solid parts of the tumors, were sent for ex tempore histopathological analysis. Results showed fibrous dysplasia with suspected malignancy. Talc pleurodesis was performed based on the obtained results. At present, the patient is asymptomatic with his daily routine uninterrupted by his medical condition. Conclusion. Treatment of pleural effusion caused by a cyst rupture of unresectable degenerated polyostotic fibrous dysplasia of the ribs represents a surgical challenge. Surgical drainage of the cysts followed by chemical pleurodesis seems to be a reasonable solution in cases where pulmonary functions are impacted by combined effects of pleural effusion and cystic compression.

scholarly journals Fibrous Dysplasia of the Temporal Bone Complicated by Cholesteatoma and Thrombophlebitis of the Transverse and Sigmoid Sinuses: A Case Report

2008 ◽  
Vol 87 (2) ◽  
pp. 81-85 ◽  
Author(s):  
Rodrigo Martinez ◽  
Jay B. Farrior
Keyword(s):  
Case Report ◽  
Fibrous Dysplasia ◽  
Temporal Bone ◽  
Broad Spectrum ◽  
Polyostotic Fibrous Dysplasia ◽  
Facial Bones ◽  
Benign Condition

Fibrous dysplasia is a benign condition that can affect the skull and facial bones and cause a broad spectrum of otolaryngologic conditions. We present the case of a boy with polyostotic fibrous dysplasia with involvement of the temporal bone that was first diagnosed when he was 9 years old. His condition eventually became complicated by cholesteatoma and thrombophlebitis of the left transverse and sigmoid sinuses, and he died of his disease at the age of 19 years. We discuss these and other complications of fibrous dysplasia of the temporal bone and their management.

Craniofacial polyostotic fibrous dysplasia: A case report

Dental Update ◽  
2019 ◽  
Vol 46 (8) ◽  
pp. 768-774
Author(s):  
Claire Forbes-Haley ◽  
Anna Najran ◽  
Sukbir Nandra ◽  
Surina Bhola
Keyword(s):  
Fibrous Dysplasia ◽  
Fibrous Tissue ◽  
Craniofacial Skeleton ◽  
Polyostotic Fibrous Dysplasia ◽  
Medullary Bone ◽  
Radiographic Appearance ◽  
Lower Jaw ◽  
Bone Disorder ◽  
Dental Hospital ◽  
Dental Rehabilitation

Fibrous dysplasia is a bone disorder whereby normal medullary bone is replaced by fibrous tissue. Many sites may be affected, including the craniofacial skeleton. A 33-year-old female presented at the Bristol Dental Hospital in 2007 complaining of a prominent and expanding lower jaw as well as poor aesthetics. She was diagnosed with craniofacial polyostotic fibrous dysplasia. In order to manage her concerns and the ongoing growth of the polyostotic lesions, a combined maxillofacial and restorative approach was utilized. After ten years of ongoing management and care, including surgery and dental rehabilitation, her primary concerns have been addressed. CPD/Clinical Relevance: The clinician should be able to understand the clinical and radiographic appearance of craniofacial fibrous dysplasia, how the condition can impact a patient and the complex management that may be involved.

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