Craniofacial polyostotic fibrous dysplasia: A case report

Fibrous dysplasia is a bone disorder whereby normal medullary bone is replaced by fibrous tissue. Many sites may be affected, including the craniofacial skeleton. A 33-year-old female presented at the Bristol Dental Hospital in 2007 complaining of a prominent and expanding lower jaw as well as poor aesthetics. She was diagnosed with craniofacial polyostotic fibrous dysplasia. In order to manage her concerns and the ongoing growth of the polyostotic lesions, a combined maxillofacial and restorative approach was utilized. After ten years of ongoing management and care, including surgery and dental rehabilitation, her primary concerns have been addressed. CPD/Clinical Relevance: The clinician should be able to understand the clinical and radiographic appearance of craniofacial fibrous dysplasia, how the condition can impact a patient and the complex management that may be involved.

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Polyostotic Fibrous Dysplasia in a Dog

Veterinary and Comparative Orthopaedics and Traumatology ◽

10.1055/s-0038-1632620 ◽

1998 ◽

Vol 11 (02) ◽

pp. 112-117 ◽

Cited By ~ 1

Author(s):

M. Pepe ◽

L. Mechelli ◽

A. Spaterna ◽

A. Di Meo

Keyword(s):

Fibrous Dysplasia ◽

Fibrous Tissue ◽

Growth Period ◽

Recovery Phase ◽

Complete Healing ◽

Radiographic Examination ◽

Cystic Lesions ◽

Polyostotic Fibrous Dysplasia ◽

Short Period ◽

The Right

SummaryA young Dobermann Pincher dog with severe right hind leg lameness was admitted to our clinic. A complete radiographic examination showed the presence of cystic lesions in the right tibia and femur and polyostotic fibrous dysplasia was diagnosed.The distal tibial lesion, associated with an incomplete cortical fracture, was treated by surgical curettage and drainage of the cyst cavity. The other cystic lesions were treated conservatively.Radiological, morphological and histological examinations were then performed to evaluate the recovery phase. At six months, the surgically treated tibial lesion showed good ossification of the fibrous tissue. At twelve months, the examination showed complete healing of the tibial lesion but the femur lesions still had a cystic appearance.It appeared that surgical curettage of the cystic cavity alone enables recovery to be achieved in a relatively short period of time.Fibrous dysplasia in dogs is a seldom reported, condition which usually it has a benign outcome and mainly involves young subjects during their growth period. It is characterized by substitution of the bone with fibrous tissue thus favouring the occurrence of spontaneous fractures.The diagnosis of this disorder is based on radiographic reports and histological examination. The lesion can be treated with conservative therapy or by surgery, but the latter significantly reduced the period of recovery.

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Clinical, microscopic and imaging findings associated to Mccune-Albright syndrome: report of two cases

Brazilian Dental Journal ◽

10.1590/s0103-64402008000200014 ◽

2008 ◽

Vol 19 (2) ◽

pp. 165-170 ◽

Cited By ~ 5

Author(s):

Samuel Porfírio Xavier ◽

Michel Campos Ribeiro ◽

Luciana Gonçalves Sicchieri ◽

Luiz Guilherme Brentegani ◽

Suzie Aparecida Lacerda

Keyword(s):

Fibrous Dysplasia ◽

The Body ◽

Lower Limbs ◽

Endocrine Disorders ◽

Polyostotic Fibrous Dysplasia ◽

Radiographic Appearance ◽

Mccune Albright Syndrome ◽

Aged Woman ◽

Albright Syndrome ◽

Mccune Albright

McCune-Albright syndrome is characterized by the triad café-au-lait cutaneous spots, polyostotic fibrous dysplasia and endocrinopathies. This article presents two cases of McCune-Albright syndrome in a middle-aged woman and a young girl. Both patients presented café-au-lait spots on the face and other parts of the body and expansion of the mandible with radiopaque-radiolucent areas with ground-glass radiographic appearance, and were diagnosed as having fibrous dysplasia and endocrine disorders. The patient of Case 1 had fibrous dysplasia on the upper and lower limbs, thorax, face and cranium, early puberty, hyperglycemia, hyperthyroidism and high serum alkaline phosphatase levels. The patient of Case 2 presented lesions on the upper limbs and evident endocrine disorders. In both cases presented in this article, the initial exam was made because of the mandibular lesion. However, a diagnosis of fibrous dysplasia must lead to investigation of the involvement of other bones, characterizing polyostotic fibrous dysplasia, which is manifested in a number of diseases. An accurate differential diagnosis is mandatory to determine the best treatment approach for each case.

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Tibial fibrous dysplasia in children treated by Ilizarov technique – a review of treatment options

Genij Ortopedii ◽

10.18019/1028-4427-2021-27-3-357-360 ◽

2021 ◽

Vol 27 (3) ◽

pp. 357-360

Author(s):

M.M. Bari ◽

◽

I. Shahidul ◽

A. Tanvir ◽

A.M. Shayan R. Bari ◽

...

Keyword(s):

Fibrous Dysplasia ◽

Operative Treatment ◽

Pathological Condition ◽

Treatment Options ◽

Fibrous Tissue ◽

Ilizarov Technique ◽

Medullary Bone

Fibrous dysplasia is a pathological condition, where normal medullary bone is replaced by fibrous tissue and small woven specules of bone. Fibrous dysplasia can occur in epiphysis, metaphysis or diaphysis. Occasionally, biopsy is necessary to establish the diagnosis. We present a review of operative treatment using the Ilizarov technique.

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Tibial fibrous dysplasia in children treated by Ilizarov Technique- A review of treatment options

MOJ Orthopedics & Rheumatology ◽

10.15406/mojor.2021.13.00542 ◽

2021 ◽

Vol 13 (2) ◽

pp. 26-29

Author(s):

Bari MM ◽

Islam Shahidul ◽

Ashraf Tanvir ◽

Bari AM Shayan R

Keyword(s):

Fibrous Dysplasia ◽

Operative Treatment ◽

Pathological Condition ◽

Treatment Options ◽

Fibrous Tissue ◽

Ilizarov Technique ◽

Medullary Bone

ibrous dysplasia is a pathological condition, where normal medullary bone is replaced by fibrous tissue and small, woven specules of bone. Fibrous dysplasia can occur in epiphysis, metaphysis or diaphysis. Occationally, biopsy is necessary to establish the diagnosis. We present a review of operative treatment using the Ilizarov technique.

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Monostotic Fibrous Dysplasia Involving the Mandible: A Case Report

SAGE Open Medical Case Reports ◽

10.1177/2050313x20936954 ◽

2020 ◽

Vol 8 ◽

pp. 2050313X2093695

Author(s):

Khalil Ibrahim Assiri

Keyword(s):

Case Report ◽

Fibrous Dysplasia ◽

Fibrous Tissue ◽

Malignant Potential ◽

Definitive Diagnosis ◽

Rapid Progression ◽

Polyostotic Fibrous Dysplasia ◽

Clinical Behavior ◽

Normal Bone ◽

Examination Methods

Fibrous dysplasia (FD) is a skeletal developmental anomaly, which is non-hereditary and idiopathic in origin. It is characterized by the replacement of normal bone with the excess proliferation of fibrous tissue in irregular bony trabeculae. Patients might complain of swelling, pain, or numbness on the affected side. The incidence of monostotic FD (MFD) is four times more than that of polyostotic fibrous dysplasia. In MFD, the maxilla is more commonly affected than the mandible. The clinical behavior and rapid progression of FD renders the treatment challenging. The malignant potential is 0.5% for untreated cases. Here, we present a case of FD involving the mandible. The clinical diagnostic approach, different imaging modalities, and histological examination methods for definitive diagnosis have been elaborated.

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