Discordant Atrioventricular Connections in Situs Inversus, Dextrocardia with Double Outlet Right Ventricle, Pulmonary Stenosis, and Anomalous Coronary Artery: A Rare Case Report

2021 ◽  
pp. 215013512110415
Author(s):  
Hien S. Nguyen ◽  
Thanh T. Pham ◽  
Long D. Tran ◽  
Manh T. Tran ◽  
Dung H. Vuong ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Right Ventricle ◽  
Situs Inversus ◽  
Superior Vena ◽  
Pulmonary Stenosis ◽  
Vena Cava ◽  
Double Outlet Right Ventricle ◽  
Anatomical Location ◽  
Single Coronary Artery ◽  
Rare Case Report

We report a case of a 2-year-old female presenting with cyanosis since birth and having rare cardiac anatomy of visceral situs inversus, dextrocardia, discordant atrioventricular connections with double outlet right ventricle, atrial communication, subaortic interventricular communication, anteriorly leftward aorta with right aortic arch, single coronary artery with a branch crossing right ventricle outflow tract, pulmonary stenosis, and bilateral superior vena cava. Corrective repair with atrial switch (Senning technique), intracardiac baffle, and right ventricle outflow reconstruction was successfully performed with challenges from altered anatomical location and orientation of the heart and abnormal coronary artery.

Double-Outlet Right Ventricle with Supravalvular Mitral Ring and Parachute Mitral Valve

1997 ◽  
Vol 5 (4) ◽  
pp. 247-249
Author(s):  
Fatih İslamoğlu ◽  
Yüksel Atay ◽  
İlker Alat ◽  
Osman Saribülbül ◽  
E Alp Alayunt
Keyword(s):  
Mitral Valve ◽  
Right Ventricle ◽  
Septal Defect ◽  
Superior Vena ◽  
Vena Cava ◽  
Double Outlet Right Ventricle ◽  
Parachute Mitral Valve ◽  
Valve Opening ◽  
Polytetrafluoroethylene Patch

A 3-year-old female presented with double-outlet right ventricle associated with supravalvular mitral ring, parachute mitral valve, left persistent superior vena cava, and atrial septal defect. The supra-annular mitral valve ring was resected. Only one papillary muscle of the mitral valve could be detected and this was minimally divided to achieve adequate valve opening. An intraventricular tunnel repair technique using a polytetrafluoroethylene patch was carried out to repair the double-outlet right ventricle, which had a subaortic ventricular septal defect. The follow-up results at 2 years are excellent.

Simultaneous Occurrence of a Single Coronary Artery and Persistent Left Superior Vena Cava

2011 ◽  
Vol 341 (3) ◽  
pp. 234-237 ◽  
Author(s):  
Emily Hass ◽  
Ammar Shreef ◽  
Joseph M. Bumgarner ◽  
Michael J. Gillespie ◽  
George A. Stouffer ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Superior Vena Cava ◽  
Superior Vena ◽  
Vena Cava ◽  
Simultaneous Occurrence ◽  
Single Coronary Artery ◽  
Left Superior Vena Cava ◽  
Persistent Left Superior Vena

Double outlet right ventricle with single coronary artery

2013 ◽  
Vol 22 (1) ◽  
pp. 112 ◽  
Author(s):  
Nikhil Prakash Patil ◽  
Karuna Katti ◽  
Deepak Kumar Satsangi
Keyword(s):  
Coronary Artery ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Single Coronary Artery

Persistent Left Superior Vena Cava Draining into the Left Atrium

1993 ◽  
Vol 1 (4) ◽  
pp. 184-186
Author(s):  
Kiyoshi Haneda ◽  
Naoshi Sato ◽  
Mikio Ohmi ◽  
Motohisa Tofiikuji ◽  
Takahiko Nakame ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Left Atrium ◽  
Superior Vena Cava ◽  
Superior Vena ◽  
Vena Cava ◽  
Double Outlet Right Ventricle ◽  
Cor Triatriatum ◽  
Left Superior Vena Cava ◽  
Venous Flow ◽  
Persistent Left Superior Vena

An 8-year-old male presented with persistent left superior vena cava draining into the left atrium, hemizygous continuation, double outlet right ventricle, cor triatriatum, and visceroatrial discordance. After correction of the double outlet right ventricle and cor triatriatum at the age of 5, he developed mild cyanosis due to a persistent left superior vena cava draining into the left atrium. At the age of 8, an intraatrial tunnel was successfully constructed with bovine pericardium to reroute the abnormal systemic venous flow.

scholarly journals P1485 multiple hindrances in and outside the heart : right ventricular outflow tract obstruction in a child with severe post-subclavian coarctation of aorta and ventricular septal defect

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
S Naganur
Keyword(s):  
Pulmonary Artery ◽  
Right Ventricle ◽  
Superior Vena ◽  
Pulmonary Stenosis ◽  
Main Pulmonary Artery ◽  
Vena Cava ◽  
Right Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Coarctation Of Aorta ◽  
Descending Aorta

Abstract Funding Acknowledgements Not applicable OnBehalf Not applicable 11 years boy with shortness of breath/easy fatigability. On examination obese, comfortable at rest, pulse : 80bpm, regular, normal JVP. Blood pressure : 170/100 in upper limb, 120/80 in lower limb. Mild cardiomegaly, normal S2, no S3/S4/click, harsh 4/6 ESM in left 3rd intercostal space, faint continuous murmur at the back. CXR : mild cardiomegaly, adequate pulmonary blood flow. ECG : sinus rhythm, normal QRS axis/intervals, biventricular hypertrophy. Echo : severe pulmonary stenosis (predominantly subvalvular, gradient 100mmHg) coarctation (gradient 50mmHg) preserved biventricular function. Cardiac CT : confirmed echo" findings, additional ? DCRV, anomalous RCA from left sinus. Cardiac MRI couldn"t yield more information. Hence, catheterization was performed. Pressure data : severe infundibular and mild valvular RVOT obstruction, normal PA pressure, severe coarctation. Oximetry : small L–>R shunt. RV angiogram : obstruction at sub-valvular/valvular levels, doming/reverse doming of pulmonary valve. LV angiogram : small subaortic VSD, L–>R. Aortic root angiogram : bicuspid aortic valve, no AR, anomalous RCA from left sinus, severe coarctation, no PDA. Plan : Single antihypertensive, surgical resection of infundibular RVOTO, pulmonary valvotomy, VSD closure, coarctation repair. Cath data Pressure in mm of Hg Right atrium (mean) 8 Right ventricle (apex) systolic 100 end diastolic 12 Right ventricle (outflow) systolic 60 end diastolic 12 Main pulmonary artery 25/10 (15) Left ventricle systolic 158 end diastolic 14 Ascending aorta 165/75 (140) Descending aorta 116/80 (100) Right Femoral artery 117/76 (98) Oximetry Superior vena cava 68% Inferior vena cava 74% Pulmonary artery 82% Aorta 99% Pulmonary vein 100% Qp/ Qs 1.6:1 Abstract P1485 Figure. CT/MRI/Cath

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