scholarly journals Complete correction of double-outlet right ventricle with situs inversus, 1-loop, and 1-malposition (I,L,L) with subaortic VSD and pulmonary stenosis

1976 ◽  
Vol 71 (1) ◽  
pp. 129-133 ◽  
Author(s):  
S. Stewart ◽  
J.D. Farnham ◽  
B. Schreiner ◽  
J. Manning
Keyword(s):  
Right Ventricle ◽  
Situs Inversus ◽  
Pulmonary Stenosis ◽  
Double Outlet Right Ventricle

Discordant Atrioventricular Connections in Situs Inversus, Dextrocardia with Double Outlet Right Ventricle, Pulmonary Stenosis, and Anomalous Coronary Artery: A Rare Case Report

2021 ◽  
pp. 215013512110415
Author(s):  
Hien S. Nguyen ◽  
Thanh T. Pham ◽  
Long D. Tran ◽  
Manh T. Tran ◽  
Dung H. Vuong ◽  
...  
Keyword(s):  
Coronary Artery ◽  
Right Ventricle ◽  
Situs Inversus ◽  
Superior Vena ◽  
Pulmonary Stenosis ◽  
Vena Cava ◽  
Double Outlet Right Ventricle ◽  
Anatomical Location ◽  
Single Coronary Artery ◽  
Rare Case Report

We report a case of a 2-year-old female presenting with cyanosis since birth and having rare cardiac anatomy of visceral situs inversus, dextrocardia, discordant atrioventricular connections with double outlet right ventricle, atrial communication, subaortic interventricular communication, anteriorly leftward aorta with right aortic arch, single coronary artery with a branch crossing right ventricle outflow tract, pulmonary stenosis, and bilateral superior vena cava. Corrective repair with atrial switch (Senning technique), intracardiac baffle, and right ventricle outflow reconstruction was successfully performed with challenges from altered anatomical location and orientation of the heart and abnormal coronary artery.

The spectrum of disease in double outlet right ventricle

2020 ◽  
pp. 73-84
Author(s):  
Andrew Ho ◽  
Tara Bharucha
Keyword(s):  
Left Ventricle ◽  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Pulmonary Stenosis ◽  
Double Outlet Right Ventricle ◽  
Term Infant ◽  
Management Options ◽  
Surgical Options ◽  
Learning Points ◽  
Blalock Taussig Shunt

Although often used as a diagnosis in its own right, double outlet right ventricle is more accurately merely a description of the ventriculo-arterial connection in a congenitally malformed heart, and use of the term must always be allied with further description of the anatomy. In this chapter we describe a term infant born at 3.4 kg following an antenatal diagnosis of double outlet right ventricle (DORV) with noncommitted ventricular septal defect (VSD), side-by-side great arteries and pulmonary stenosis. There was a duct-dependent pulmonary circulation in the neonatal period, and the infant underwent placement of a Blalock-Taussig shunt. Following multi-modality cardiac imaging, he underwent to complete surgical repair at 16 months of age, with VSD enlargement, tunnelled closure of the VSD to commit the left ventricle to the aorta, and augmentation of the pulmonary outflow tract. Through the chapter, we emphasise the importance of a detailed anatomical description and thorough investigation in this family of defects, in order to allow an understanding of the physiology, clinical behaviour and the management options available for individual patients. Learning points in the chapter include discussion regarding the definitions of DORV, detailed descriptions of the major anatomical groups and a synopsis of the more common surgical options.

Primary Intracardiac Repair of Double Outlet Right Ventricle and Ventricular Septal Defect without Pulmonary Stenosis

1995 ◽  
Vol 3 (3-4) ◽  
pp. 103-108
Author(s):  
KG Jaya Prasanna ◽  
Krishna Subramony Iyer ◽  
Rajesh Sharma ◽  
Balram Airan ◽  
Ivatury Mrityonjaya Rao ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Septal Defect ◽  
Arterial Switch Operation ◽  
Pulmonary Stenosis ◽  
Double Outlet Right Ventricle ◽  
Arterial Switch ◽  
Intracardiac Repair ◽  
Switch Operation

From January 1991' to May 1994, 29 patients with double outlet right ventricle with ventricular septal defect, without pulmonary stenosis underwent primary intracardiac repair at the All India Institute of Medical Sciences, New Delhi. Patients were classified into 4 groups based on location of the ventricular septal defect. The ventricular septal defect was subaortic in 11, subpulmonary in 13, doubly committed subarterial in 1, and noncommitted in 4 patients. Surgical treatment consisted of intraventricular routing of the left ventricle to the aorta (17), and the left ventricle to the pulmonary artery followed by an arterial switch operation (12). There were 4 (13.9%) early deaths. Follow-up ranged from 3 months to 3 years (mean, 1.5 years). There was no late mortality. Three patients had residual ventricular septal defect, one of whom has undergone reoperation. One patient has a gradient of 25 mmHg across the left ventricular outflow tract. Double outlet right ventricle with subpulmonic ventricular septal defect was found to be a significant risk factor for early mortality (p = 0.03). The subgroup of double outlet right ventricle with subpulmonic ventricular septal defect who had a combination of single coronary artery and post arterial switch operation was particularly prone to pulmonary hypertensive crisis and hospital death (p = 0.002).

scholarly journals Oral Prostaglandin E1 Derivative (OP-1206) in an Infant with Double Outlet Right Ventricle and Pulmonary Stenosis. Effect on Ductus-Dependent Pulmonary Circulation.

1991 ◽  
Vol 32 (5) ◽  
pp. 735-740 ◽  
Author(s):  
Tsutomu SAJI ◽  
Hiroyuki MATSUURA ◽  
Kyoko HOSHINO ◽  
Shin YAMAMOTO ◽  
Takashi ISHIKITA ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Pulmonary Circulation ◽  
Prostaglandin E1 ◽  
Pulmonary Stenosis ◽  
Double Outlet Right Ventricle

scholarly journals Individualized Surgical Reconstruction of the Right Ventricle Outflow Tract in Double Outlet Right Ventricle With Mirror Image-Dextrocardia

2021 ◽  
Vol 9 ◽  
Author(s):  
Wangping Chen ◽  
Chukwuemeka Daniel Iroegbu ◽  
Xia Xie ◽  
Wenwu Zhou ◽  
Ming Wu ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Right Ventricular ◽  
Pulmonary Stenosis ◽  
Right Ventricular Outflow Tract ◽  
Ventricular Outflow Tract ◽  
Double Outlet Right Ventricle ◽  
Mirror Image ◽  
Outflow Tract ◽  
Surgical Reconstruction ◽  
The Right

Introduction: The purpose of this study was to report our experience in the surgical reconstruction of the right ventricular outflow tract in double outlet right ventricle with a major coronary artery crossing the right ventricular outflow tract in the presence of mirror image-dextrocardia.Methods: From January 2005 to December 2019, 19 double outlet right ventricle patients (median age 4 years) with mirror image-dextrocardia and a major coronary artery crossing the right ventricular outflow tract received surgical repair. An autologous pericardial patch was used to enlarge the right ventricular outflow tract in four patients without pulmonary stenosis and three patients with mild pulmonary stenosis. A valved bovine jugular venous conduit was added to a hypoplastic native pathway in nine patients, among which six patients with moderate pulmonary stenosis received small-sized bovine jugular venous conduit implantation (diameter ≤ 16 mm). In comparison, a large-sized bovine jugular venous conduit (diameter >16 mm) was adopted in a total of three patients with severe pulmonary stenosis. Finally, three patients with preoperative pulmonary hypertension (mean pulmonary artery pressure ≥40 mmHg) did not undergo further intervention of right ventricular outflow tract due to the adequate outflow tract blood flow.Results: There was no hospital mortality. One patient with sub-pulmonary ventricular septal defect and concomitant severe pulmonary hypertension died from respiratory failure 11 months after the operation. Kaplan-Meier survival was 94% at 5, 10 years. Within a mean echocardiographic follow-up of 6.9 ± 3.6 years, a total of two patients received reintervention due to valvular stenosis of the bovine jugular venous conduit (pressure gradient > 50 mmHg at 4 and 9 years) after surgical operation. Actuarial freedom from reoperation was 90 and 72% at 5 and 10 years, respectively. During the last echocardiographic follow-up phase, all the survivors were in NYHA class I.Conclusions: Double outlet right ventricle with mirror image-dextrocardia is a rare and complicated congenital cardiac malformation. Surgical reconstruction of the right ventricular outflow tract should be individualized based on the degree of pulmonary stenosis and the specific anatomical features of each patient. Reconstructing the pulmonary artery using the various sizes of valved bovine jugular venous conduit is a safe and effective surgical method.

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