scholarly journals Rare case of neglected large sacral Chordoma in a young female treated by wide En bloc resection and Sacrectomy

BMC Cancer ◽  
2018 ◽  
Vol 18 (1) ◽  
Author(s):  
Zi Hao Phang ◽  
Xue Yi Saw ◽  
Noreen Fadzlina Binti Mat Nor ◽  
Zolqarnain Bin Ahmad ◽  
Sa’adon Bin Ibrahim
2007 ◽  
Vol 14 (4) ◽  
pp. 362-364 ◽  
Author(s):  
Francesco Porpiglia ◽  
Cecilia M Cracco ◽  
Carlo Terrone ◽  
Marco Cossu ◽  
Julien Renard ◽  
...  

2019 ◽  
Vol 6 (6) ◽  
pp. 2213
Author(s):  
Cherring Tandup ◽  
Anish Chowdhury ◽  
Yashwant Raj Sakaray ◽  
Nasika Venkata Kanaka Naga Karthik

Cystic lymphangioma is benign tumor originating from the lymphatic vessels. Most commonly occurs in childhood and in the head or neck regions, retroperitoneal localization and presentations in adulthood are rare. Making a pre-operative diagnosis is challenging, and only possible subsequent to the histological examination. En bloc resection is the recommended treatment for cystic lymphangioma, and recurrence occurs due to an incomplete excision. We here present a case of 40 year female presenting with progressive palpable lump associated with pain in right quadrant of abdomen, which on computed tomography revealed a large retroperitoneal cystic lesion probably lymphanigoma or cystic mesothelioma.


2019 ◽  
Vol 2019 ◽  
pp. 1-4
Author(s):  
Chiao Yee Lim ◽  
Suryasmi Duski ◽  
Ping Ching Chye

Intramuscular myxomas are rare, benign mesenchymal tumors. Tumor location in the forearm is very rare among all the intramuscular myxomas. To the best of our knowledge, there were two cases of supinator intramuscular myxoma reported in the literature, and we intend to report the third case of supinator myxoma with encasement of the posterior interosseous nerve (PIN). A 67-year-old lady presented with history of left proximal forearm swelling for the past 5 years. Magnetic resonance imaging showed a lobulated multiseptated lesion seen within left supinator muscle, which was hyperintense on T2-weighted images (T2WI) and hypointense on T1-weighted images (T1WI), with peripheral enhancement post contrast. The tissue diagnosis of myxoma was confirmed via an open biopsy. She underwent en bloc resection of the tumor. The PIN was encased by the tumor; it was preserved and carefully released from the tumor. The nerve sheath served as an excision margin. In conclusion, we present a rare case of an intramuscular myxoma in the supinator muscle. In view of the location, extra attention should be paid during excision surgery to locate the PIN and to avoid damaging the surrounding structures.


2014 ◽  
Vol 20 (4) ◽  
pp. 421-429 ◽  
Author(s):  
Rajiv Saigal ◽  
Daniel C. Lu ◽  
Donna Y. Deng ◽  
Dean Chou

Chordomas of the sacrum require en bloc resection to reduce the risk of recurrence, but this may sacrifice nerves vital to bladder, bowel, and sexual function. High, mid-, and low sacral amputations have been previously classified based on nerve root sacrifice, not bony amputation. Sacrifice of the S-2 nerves or those above results in a high sacral amputation, but preserving the S-2 nerves converts it into a midsacral amputation. Preservation of the S-2 nerves has been shown to improve functional outcome, despite the bony osteotomy being unchanged. Thus, keeping the same bony amputation while preserving the S-2 nerve roots may allow for improved functional outcome while still achieving the same goal of oncological resection. Preservation of the S-2 nerves may be particularly difficult during amputation at the S-2 pedicle or above, and the authors describe their technique for preserving the S-2 nerves during partial sacrectomy at or just above the S-2 pedicle. Four cases of sacral chordoma resections are presented to illustrate the technique.


2013 ◽  
Vol 15 (11) ◽  
Author(s):  
Mohammad Gharahdaghi ◽  
Hassan Rahimi Shorin ◽  
Ali Parsa ◽  
Maryam Assadian

2015 ◽  
Vol 8 (2) ◽  
pp. 84-88
Author(s):  
Chandra Kant ◽  
Virendra Kumar Prajapati ◽  
Vishwambhar Singh ◽  
Krishna Murari Tiwari

ABSTRACT Odontogenic fibromyxoma, a myxoma with abundant collagen fibers, is a rare benign tumor of jaw which mostly affects posterior part of mandible. It is ectomesenchymal in origin and probably arises from connective tissue of dental follicle or papilla. Commonly occurs in 2nd or 3rd decade with slight female predilection. Radiological investigations, such as conventional radiography, computed tomography (CT) scan or magnetic resonance imaging (MRI) can be used to differentiate it from other odontogenic tumors like ameloblastoma. Management is surgical by enucleation and curettage or by en bloc resection and segmental maxillectomy. Follow-up of patient is must for at least 2 years to diagnose any recurrence. In this article, we present fibromyxoma of maxilla which is a very rare site for occurrence of fibromyxoma and this relatively rare condition has been discussed in light of recent information from literature with a case report. How to cite this article Kant C, Prajapati VK, Singh V, Tiwari KM. Odontogenic Fibromyxoma of Maxilla: A Rare Case Report. Clin Rhinol An Int J 2015;8(2):84-88.


2020 ◽  
Vol 19 (4) ◽  
pp. E412-E412
Author(s):  
Martin Julian Gagliardi ◽  
Alfredo Guiroy ◽  
Alfredo Sícoli ◽  
Nicolás Gonzalez Masanés ◽  
Alejandro Morales Ciancio

Abstract Sacral chordomas are infrequent tumors that arise from remnants of the notochord. They are most often found in the sacrum and skull-base.1,2 These lesions rarely metastasize and usually have an indolent and oligosymptomatic clinical course. Chordomas show low sensitivity to standard radiation therapy and chemotherapy. Operative resection with wide resection margins offers the best long-term prognosis, including longer survival and local control.1,3 However, achieving a complete resection with oncological margins may be difficult because of the anatomic complexity of the sacrococcygeal region.4 The main complications of sacral resection include infections, wound closure defects, and anorectal and urogenital dysfunction. The rate of these complications is significantly increased when the tumor involves the S2 level or above. We report the case of a 64-yr-old male who presented with progressive sacrococcygeal pain and a feeling of incomplete evacuation. A heterogeneous, osteolytic lesion was found at the sacrococcygeal region. Full body imaging tests were negative for other lesions. A computed tomography (CT) guided biopsy was made. We usually use the midline approach in case we have to include the needle path in the resection. The pathology confirmed a sacrococcygeal, low-grade chordoma. We decided to perform an en bloc resection. A posterior, partial sacrectomy was planned distal to the S4 level.


2010 ◽  
Vol 66 (suppl_1) ◽  
pp. ons-41-ons-44 ◽  
Author(s):  
Ganesh Rao ◽  
George J. Chang ◽  
Ian Suk ◽  
Ziya Gokaslan ◽  
Laurence D. Rhines

Abstract Background: En bloc resection, with adequate surgical margins, of primary malignant bone tumors of the sacrum is associated with long term disease control and potential cure. Resection of sacral tumors is difficult due to the proximity of neurovascular and visceral structures, and complete, or even partial, sacrectomy often results in functional loss for the patient. Objective: We describe the technique for en bloc resection of a sacral chordoma through a mid-sacral amputation. Results: We demonstrate successful removal of a large sacral tumor with wide surgical margins while preserving neurologic function. Conclusion: This technique for midsacral amputation to remove a sacral tumor en bloc minimizes local recurrence and maximizes neurovascular function.


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