scholarly journals Type I congenital extrahepatic portosystemic shunt treated by orthotopic liver transplantation: A case report

2019 ◽  
Vol 7 (7) ◽  
pp. 903-907 ◽  
Author(s):  
Wen Xiang ◽  
Hao Wang ◽  
Zhong-Zhou Si ◽  
Guang-Shun Chen ◽  
Guan-Wu Wang ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Case Report ◽  
Orthotopic Liver Transplantation ◽  
Portosystemic Shunt ◽  
Type I ◽  
Congenital Extrahepatic Portosystemic Shunt

scholarly journals Orthotopic Liver Transplantation for Hereditary Hemorrhagic Telangiectasia and MEN Type I Syndrome - Case Report and Review of Literature

Chirurgia ◽  
2018 ◽  
Vol 113 (6) ◽  
pp. 837
Author(s):  
Mihnea-Ioan Ionescu ◽  
Ian David Edwin Nesbitt ◽  
Colin Hugh Wilson ◽  
Samantha Erica Saikia ◽  
David Talbot
Keyword(s):  
Liver Transplantation ◽  
Case Report ◽  
Orthotopic Liver Transplantation ◽  
Hereditary Hemorrhagic Telangiectasia ◽  
Type I ◽  
Review Of Literature

scholarly journals ABERNETHY MALFORMATION AS A RARE INDICATION FOR LIVER TRANSPLANTATION: CASE REPORT

2019 ◽  
Vol 141 (5-6) ◽  
pp. 134-137
Keyword(s):  
Liver Transplantation ◽  
Case Report ◽  
Portal Vein ◽  
Liver Tumors ◽  
Splenic Vein ◽  
Vena Cava ◽  
Portal Blood ◽  
Type I ◽  
Abernethy Malformation ◽  
Congenital Cardiac Anomalies

Abernethy malformation or congenital agenesis of the portal vein (CAPV) is a rare malformation of the abdominal splanchnic venous system. This malformation is commonly found in children and is often associated with other malformations such as congenital cardiac anomalies and skeletal system disorders, as well as liver tumors. There are two types of Abernethy malformation. In type I, portal blood bypasses the liver completely, with the superior mesenteric vein and the splenic vein draining into the inferior vena cava separately (type Ia), or together (type Ib). There are no intrahepatic portal vein branches in the liver. Type II is a partial portocaval shunt in which portal blood partially supplies the liver. There is no unified therapeutic approach for all patients with Abernethy malformation, however, liver transplantation is recommended in patients with liver disease (encephalopathy, poor liver function) and those with liver tumors. In this case report we present a case of Abernethy type Ib malformation in a 17-year-old patient with chronic malaise and uper abdominal pain. During diagnostic work-up, an unresectable liver tumor was found and the patient was successfully treated with orthotopic liver transplantation.

Case report: Portal-systemic encephalopathy due to a congenital extrahepatic portosystemic shunt

1996 ◽  
Vol 11 (7) ◽  
pp. 626-629 ◽  
Author(s):  
MASATO KIRIYAMA ◽  
SHIGEKI TAKASHIMA ◽  
HIROYUKI SAHARA ◽  
YOSHIYUKI KUROSAKA ◽  
MASAHIRO MATSUSHITA ◽  
...  
Keyword(s):  
Case Report ◽  
Portosystemic Shunt ◽  
Portal Systemic Encephalopathy ◽  
Congenital Extrahepatic Portosystemic Shunt

Orthotopic Liver Transplantation in an Adult With Biliary Atresia, Situs Inversus, and Inferior Cava Vein Absence: A Case Report

2015 ◽  
Vol 47 (8) ◽  
pp. 2407-2409 ◽  
Author(s):  
N. Fernández Soria ◽  
M.A. García Novoa ◽  
J.I. Rivas Polo ◽  
C. Fernández Sellés ◽  
M. de los Ángeles Vázquez ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Case Report ◽  
Biliary Atresia ◽  
Orthotopic Liver Transplantation ◽  
Situs Inversus ◽  
Cava Vein ◽  
Inferior Cava Vein

Orthotopic liver transplantation for haemophilia A may not always lead to a phenotypic cure of haemophilia A: A case report

Haemophilia ◽  
2018 ◽  
Vol 24 (6) ◽  
pp. e420-e422
Author(s):  
Yuji Suzuki ◽  
Keisuke Kakisaka ◽  
Tomoko Matsumoto ◽  
Keiji Nogami ◽  
Hirokatsu Katagiri ◽  
...  
Keyword(s):  
Liver Transplantation ◽  
Case Report ◽  
Orthotopic Liver Transplantation ◽  
Haemophilia A
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