scholarly journals Aplasia cutis congenita with fetus papyraceus: an uncommon case report

2020 ◽  
Vol 6 (6) ◽  
pp. 809
Author(s):  
Vivekananda Ittigi ◽  
Aparna Anto
Keyword(s):  
Reproductive Technologies ◽  
In Utero ◽  
Multiple Gestation ◽  
Aplasia Cutis Congenita ◽  
Multiple Gestations ◽  
Symmetrical Distribution ◽  
Associated Conditions ◽  
Uncommon Case ◽  
Type V ◽  
Aplasia Cutis

<p class="abstract">Aplasia cutis congenita is a condition characterized by congenital absence of all skin layers in a localized or widespread area. Frieden's classification recognized a rare subtype, type V, that is associated with multiple gestations in which there is the in-utero demise of a twin with resultant fetus papyraceus or mummification. A twin pregnancy was complicated by in-utero death of one twin at 5 months. On full term birth of the other twin with fetus papyraceus large defects in the skin of knees were noted bilaterally. Conservative management with topical antibiotics and emollients helped in complete re-epithelialization in few months. As the use of reproductive technologies increase the incidence of multiple gestation and associated conditions are expected to increase. This type is clinically unique in that it is characterized by stellate lesions in a symmetrical distribution over the trunk and extremities, differing from other subtypes, which are typically localized to scalp (70%-85% of cases) or extremities. Management ranges from conservative to surgical grafts.</p>

scholarly journals Multiple aplasia cutis congenita type V and fetus papyraceous: a case report and review of the literature

2021 ◽  
Vol 15 (1) ◽  
Author(s):  
V. Thadchanamoorthy ◽  
Kavinda Dayasiri ◽  
M. Thirukumar ◽  
N. Thamilvannan ◽  
S. H. Chandraratne
Keyword(s):  
Rare Condition ◽  
The Body ◽  
Sri Lankan ◽  
Aplasia Cutis Congenita ◽  
Skin Defects ◽  
Underlying Causes ◽  
Cutis Aplasia ◽  
Contracture Formation ◽  
Type V ◽  
Aplasia Cutis

Abstract Background Aplasia cutis congenita is regarded as congenital focal absence of skin in the newborn, and occurrence of more than three similar skin defects is rare. The etiology is thought to be multifactorial, and precise etiopathogenesis is unknown. Case presentation A 13-day-old newborn Sri Lankan Tamil girl was referred to the dermatologic clinic with multiple skin defects at birth. There were six lesions on the body, and two of them had healed during intrauterine period, leaving scars. This was a second twin of her pregnancy. Her first twin fetus had demised before 19 weeks of pregnancy and was confirmed to be fetus papyraceous based on ultrasound-guided fetal assessment. The said child was thoroughly investigated and found to have no other congenital abnormalities. Chromosomal studies yielded normal findings. She was treated with tropical antibacterial ointment, and all lesions resolved spontaneously within 4 weeks, leaving scars. Physiotherapy was commenced to prevent contracture formation, and follow-up was arranged in collaboration with the plastic surgical team. Conclusions Aplasia cutis congenita is a rare condition of uncertain etiology, but consanguinity may play a role. This report described a newborn with type V cutis aplasia congenita in whom the diagnosis was confirmed based on clinical features and revision of antenatal history. The management depends on the pattern, extent, location, severity, underlying causes, and associated anomalies.

scholarly journals Aplasia Cutis Congenita and Skull Defects after Exposure to Methimazole in Utero

2005 ◽  
Vol 44 (11) ◽  
pp. 1202-1203 ◽  
Author(s):  
Shigenori NAKAMURA ◽  
Tomoko NISHIKAWA ◽  
Mako ISAJI ◽  
Masatoshi ISHIMORI ◽  
Nobuo SHIMIZU ◽  
...  
Keyword(s):  
In Utero ◽  
Aplasia Cutis Congenita ◽  
Skull Defects ◽  
Aplasia Cutis

scholarly journals MATERNAL COMPLICATIONS OF MULTIPLE GESTATIONS IN SECOND AND THIRD TRIMESTER OF PREGNANCY.

1969 ◽  
Vol 5 (1) ◽  
pp. 591-596
Author(s):  
SAIMA KHATTAK ◽  
MUHMMAD BILAL AWAN ◽  
MUHMMAD DANYAL AWAN
Keyword(s):  
Twin Pregnancy ◽  
Reproductive Technologies ◽  
High Order ◽  
Multiple Gestation ◽  
Third Trimester ◽  
Triplet Pregnancy ◽  
Maternal Complications ◽  
Multiple Gestations ◽  
Risk Pregnancy

BACKGROUND: In recent times, the incidence of multiple pregnancies has significantly increased dueto medication for induced ovulation and other reproductive technologies. The present study is designedto see the maternal complication of multiple gestations in pregnancy.OBJECTIVE: To determine the maternal complications associated with multiple gestation in secondand third trimester of pregnancy.METHODOLOGY: This descriptive study was carried out in the department of obstetrics andGynaecology unit at Lady Reading Hospital Peshawar. Duration of the study was 06 months from 1stJanuary 2012 to 1st July 2012. All patients with twin gestations, triplets and high order multiples visitingobstetrics and Gynaecology unit at Lady Reading Hospital Peshawar and who were admitted in wardwere included in the study and after taking informed consent their characteristics were recorded byfilling proforma.RESULTS: Sixty patients with multiple gestations were included in the study. Fifty four (90%) of themhad twin pregnancy and 06 (10%) had triplet pregnancy. The antenatal complications detected in thesepatients were preterm labour 23(32.3%), anaemia 18(30%), pregnancy induced hypertension, preeclamptic toxaemia, eclampsia 13(21.7%), Malpresentation 13(21.7%), Antepartum Haemorrhage 5(8.3%), 5 patients (8.3%) had PROM, 4 (6.7%) had polyhydramnios, 3(5%) had miscarriages, 5 (8.3%)had postpartum haemorrhage, 44(73.3%) patients had spontaneous vaginal delivery and 15(25%)underwent caesarean section. In 28(46.7%) patients cephalic/cephalic was the most commonpresentation.CONCLUSION: Multiple gestation is a high risk pregnancy and is associated with both maternal andfetal complications. Patient needs to be educated about the importance and advantages of early antenatalbooking and regular antenatal follow-up to reduce the risks to the mother and the babies.KEY WORDS: Twin pregnancy, Triplets, High-order multiplets; Complications-Second Trimester,Third trimester.

scholarly journals Type V aplasia cutis congenita

2010 ◽  
Vol 30 (2) ◽  
pp. 171-172 ◽  
Author(s):  
Umar A. Qureshi ◽  
Nisar Ahmed
Keyword(s):  
Aplasia Cutis Congenita ◽  
Type V ◽  
Aplasia Cutis

Type V Aplasia Cutis Congenita: Case Report, Review of the Literature, and Proposed Treatment Algorithm

2012 ◽  
Vol 30 (6) ◽  
pp. e208-e213 ◽  
Author(s):  
Daniel Morrow ◽  
Robert Schelonka ◽  
Alfons Krol ◽  
Michael Davies ◽  
Anna Kuang
Keyword(s):  
Case Report ◽  
Treatment Algorithm ◽  
Review Of The Literature ◽  
Aplasia Cutis Congenita ◽  
Type V ◽  
Aplasia Cutis

Lesioni cutanee stellate e simmetriche in un gemello “rimasto solo”

2021 ◽  
Vol 40 (6) ◽  
pp. 383-385
Author(s):  
Claudia Sciarrotta ◽  
Gregorio Serra ◽  
Mandy Schierz ◽  
Giovanni Corsello
Keyword(s):  
Twin Pregnancy ◽  
Assisted Reproductive Technologies ◽  
Multiple Pregnancy ◽  
Reproductive Technologies ◽  
Intrauterine Death ◽  
Second Trimester ◽  
Aplasia Cutis Congenita ◽  
Multiple Gestations ◽  
Vanishing Twin Syndrome ◽  
Twin Pregnancies

The incidence of multiple pregnancy has increased, particularly because of the advances in assisted reproductive technologies. Multiple gestations are high risk pregnancies, especially the monochorionic ones. Two/thirds of initially twin pregnancies result in singles at birth, a condition defined as vanishing twin syndrome. The intrauterine death of one of the twins can cause direct fetal damage to the surviving one on several levels. The paper describes the case of a child born from twin pregnancy that was interrupted for one of the co-twins at early second trimester of gestation who presented with aplasia cutis congenita.

Aplasia cutis congenita type V: a case report and review of the literature

2017 ◽  
Vol 56 (6) ◽  
pp. e118-e121 ◽  
Author(s):  
Benjamin M. Perry ◽  
Cory B. Maughan ◽  
Matthew S. Crosby ◽  
Scott D. Hadenfeld
Keyword(s):  
Case Report ◽  
Review Of The Literature ◽  
Aplasia Cutis Congenita ◽  
Type V ◽  
Aplasia Cutis

scholarly journals Extensive Type V Aplasia Cutis Congenita Without Fetus Papyraceus or Placental Infarction: A Rare Case

2021 ◽  
Vol Volume 14 ◽  
pp. 1413-1418
Author(s):  
Raden Mohamad Rendy Ariezal Effendi ◽  
Lita Nuraeni ◽  
Inne Arline Diana ◽  
Srie Prihianti Gondokaryono ◽  
Hendra Gunawan ◽  
...  
Keyword(s):  
Rare Case ◽  
Aplasia Cutis Congenita ◽  
Type V ◽  
Aplasia Cutis

Lesioni cutanee stellate e simmetriche in un gemello “rimasto solo”

2021 ◽  
Vol 40 (7) ◽  
pp. 383-385
Author(s):  
Claudia Sciarotta ◽  
Gregorio Serra ◽  
mandy Schierz ◽  
Giovanni Corsello
Keyword(s):  
Twin Pregnancy ◽  
Assisted Reproductive Technologies ◽  
Multiple Pregnancy ◽  
Reproductive Technologies ◽  
Intrauterine Death ◽  
Second Trimester ◽  
Aplasia Cutis Congenita ◽  
Multiple Gestations ◽  
Vanishing Twin Syndrome ◽  
Twin Pregnancies

The incidence of multiple pregnancy has increased, particularly because of the advances in assisted reproductive technologies. Multiple gestations are high risk pregnancies, especially the monochorionic ones. Two/thirds of initially twin pregnancies result in singles at birth, a condition defined as vanishing twin syndrome. The intrauterine death of one of the twins can cause direct fetal damage to the surviving one on several levels. The paper describes the case of a child born from twin pregnancy that was interrupted for one of the co-twins at early second trimester of gestation who presented with aplasia cutis congenita.

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