scholarly journals Is Fahr’s disease a saviour for intracranial hypertensive bleeds? - A review

2021 ◽  
Vol 11 (2) ◽  
pp. 360-363
Author(s):  
Roopak Dubey ◽  
Kamal Kumar Sen ◽  
Mayank Goyal ◽  
D. Sindhu Reddy ◽  
Suma MK

Fahr’s disease (FD) is a rare disorder characterised by abnormal deposition of calcium in different parts of brain especially in basal ganglia, thalamus and dentate nucleus. Association of FD with ischemic stroke has been described in past but very less literature available showing association of FD with haemorrhagic stroke. We present here a case of 70 years old hypertensive male patient suffering from FD with left thalamic acute haemorrhage. Although basal ganglia is a common site for hypertensive bleed, but in this hypertensive patient, basal ganglia was spared. We assume that this could be due to presence of calcification within vessel walls of basal ganglia that strengthen the walls and hence act as a saviour for basal ganglia bleed in this case.

1970 ◽  
Vol 30 (1) ◽  
pp. 44-45
Author(s):  
Rahul Sinha ◽  
Kirandeep Sodhi ◽  
BM John ◽  
Daljit Singh

We report a case of Fahrs disease in a 15year old girl presented to us with focal seizure with secondary generalisation. Clinically there were no abnormal findings. The CT scan (brain) showed multiple symmetric and extensive calcifications in the basal ganglia, thalamus, and dentate nucleus, subcortical white matter of cerebral and cerebellar areas. Presently the child is under followup with good seizure control with carbamezpine. This rare case of idiopathic Fahr's disease in a child, which has never been reported in Indian literature has been brought out to highlight this unusual condition and its differentiation from the commoner Fahr's syndrome. Key words: Basal ganglia, calcification, Fahrs disease. DOI: 10.3126/jnps.v30i1.2459 Journal of Nepal Paediatric Society Vol.30(1) 2010 44-45


2019 ◽  
Author(s):  
Guotao Wang ◽  
Zhinan Ye ◽  
Jian Cheng ◽  
Guohua Ma

Abstract Background: Fahr’s disease is a rare neurological disorder which is characterized by diffuse intracranial calcification documented in bilateral basal ganglia and dentate nuclei of the cerebellum. In recent years, some acute presentations of Fahr’s disease have been reported. Here we describe a Fahr’s disease patient presenting with thalamic hemorrhage, which has not been reported so far. Case presentation: A 51-year-old man doesn’t have any prior premonitory symptoms and significant family history of neurologic disorder, he presented to our emergency department because of acute left limb numbness. Both brain CT and MRI study exhibited symmetric calcifications in bilateral basal ganglia and bilateral cerebellar dentate nuclei, which was consistent with Fahr’s disease. In addition, the blood investigation provided no criteria to secondary intracranial calcification. After proper clinical medical treatment and sustained physical rehabilitation, the patient’s symptoms relieved and he was discharged from hospital. Conclusion: We describe a case of sporadic Fahr’s disease presenting with thalamic hemorrhage. It is unknown whether the calcification in Fahr’s disease negatively affects intracranial vessels predisposing acute presentation. Therefore, the association between idiopathic basal ganglia calcification and acute cerebrovascular disease is worth special attention and needs further studies. Keywords: Fahr’s disease, thalamic hemorrhage.


2012 ◽  
Vol 10 (2) ◽  
pp. 155-156
Author(s):  
K Ahmad ◽  
K Dhungel ◽  
P Sah ◽  
S Ansari ◽  
Dr. Shashikar

Fahr's disease is a rare neurodegenerative disorder that is characterized by the bilateral symmetrical deposition of calcium in the basal ganglia, thalamus, dentate nuclei and centrum semiovale in the absence of hypoparathyroidism. It is often familial. Hereby, we are reporting a rare case of Fahr's disease who presented with repeated episodes of seizures and was diagnosed as Fahr's disease after performing computed tomographic (CT) scan.DOI: http://dx.doi.org/10.3126/hren.v10i2.6589 Health Renaissance 2012; Vol 10 (No.2); 155-156  


2021 ◽  
Vol 16 (10) ◽  
pp. 3055-3059
Author(s):  
Adele DURANTE ◽  
Nunzia AUDINO ◽  
Mariarita CRISTIANO ◽  
Michela TANGA ◽  
Maria Teresa MARTINO ◽  
...  

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